D76.2
BillableHemophagocytic syndrome, infection-associated
Hemophagocytic syndrome, infection-associated
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •(Abt-) Letterer-Siwe diseaseC96.0
- •eosinophilic granulomaC96.6
- •Hand-Schüller-Christian diseaseC96.5
- •histiocytic medullary reticulosisC96.9
- •histiocytic sarcomaA)C96
- •histiocytosis X, multifocalC96.5
- •histiocytosis X, unifocalC96.6
- •Langerhans-cell histiocytosis, multifocalC96.5
- •Langerhans-cell histiocytosis NOSC96.6
- •Langerhans-cell histiocytosis, unifocalC96.6
- •leukemic reticuloendotheliosisC91.4
- •lipomelanotic reticulosisI89.8
- •malignant histiocytosisA)C96
- •malignant reticulosisC86.0
- •nonlipid reticuloendotheliosisC96.0
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Use Additional Code
Additional codes that should follow this code
- code to identify infectious agent or disease.
Related Codes(2)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(70)
SNOMED CT
- Haemophagocytic lymphohistiocytosis due to infection190959006
- Haemophagocytic syndrome due to infection190959006
- Hemophagocytic lymphohistiocytosis due to infection190959006
- Hemophagocytic syndrome due to infection190959006
- Infection-associated haemophagocytic syndrome190959006
- Infection-associated hemophagocytic syndrome190959006
- Infection-induced haemophagocytic histiocytosis190959006
- Infection-induced hemophagocytic histiocytosis190959006
- Haemophagocytic lymphohistiocytosis234437005
- Haemophagocytic syndrome234437005
- Hemophagocytic lymphohistiocytosis234437005
- Hemophagocytic syndrome234437005
- Hyperinflammatory lymphohistiocytosis234437005
- Haemophagocytic lymphohistiocytosis with rheumatologic disease430478003
- Hemophagocytic lymphohistiocytosis with rheumatologic disease430478003
- Macrophage activation syndrome430478003
- Reactive haemophagocytic syndrome430478003
- Reactive hemophagocytic syndrome430478003
- Haemophagocytic syndrome with human immunodeficiency virus infection713444005
- Hemophagocytic syndrome with human immunodeficiency virus infection713444005
- Secondary haemophagocytic lymphohistiocytosis1153417000
- Secondary hemophagocytic lymphohistiocytosis1153417000
- Infection-associated MAS (macrophage activation syndrome)1290500002
- Infection-associated macrophage activation syndrome1290500002
- Macrophage activation syndrome due to infectious disease1290500002
UMLS
- Haemophagocytic lymphohistiocytosis due to infectionC0019068
- Haemophagocytic syndrome due to infectionC0019068
- Hemophagocytic Syndrome, Infection AssociatedC0019068
- Hemophagocytic Syndrome, Infection-AssociatedC0019068
- Hemophagocytic Syndrome, ReactiveC0019068
- Hemophagocytic lymphohistiocytosis due to infectionC0019068
- Hemophagocytic lymphohistiocytosis due to infection (disorder)C0019068
- Hemophagocytic syndrome due to infectionC0019068
- Hemophagocytic syndrome, infection-associatedC0019068
- Infection-Associated Hemophagocytic SyndromeC0019068
- Infection-associated haemophagocytic syndromeC0019068
- Infection-associated hemophagocytic syndromeC0019068
- Infection-induced haemophagocytic histiocytosisC0019068
- Infection-induced hemophagocytic histiocytosisC0019068
- Reactive Hemophagocytic SyndromeC0019068
- Reactive haemophagocytic syndromeC0019068
- Reactive hemophagocytic syndromeC0019068
Clinical Terms
- Infection-induced haemophagocytic histiocytosis
- Infection-associated haemophagocytic syndrome
- Haemophagocytic syndrome
- Hemophagocytic lymphohistiocytosis due to infection
- Secondary hemophagocytic lymphohistiocytosis
- Infection-associated macrophage activation syndrome
- Infection-associated MAS (macrophage activation syndrome)
- Macrophage activation syndrome
- Hemophagocytic lymphohistiocytosis
- Infection-Associated Hemophagocytic Syndrome
- Hyperinflammatory lymphohistiocytosis
- Infection-induced hemophagocytic histiocytosis
- Haemophagocytic lymphohistiocytosis with rheumatologic disease
- Hemophagocytic Syndrome, Reactive
- Secondary haemophagocytic lymphohistiocytosis
- Reactive Hemophagocytic Syndrome
- Macrophage activation syndrome due to infectious disease
- Haemophagocytic lymphohistiocytosis
- Hemophagocytic syndrome
- Haemophagocytic syndrome with human immunodeficiency virus infection
- Hemophagocytic syndrome with human immunodeficiency virus infection
- Hemophagocytic lymphohistiocytosis due to infection (disorder)
- Hemophagocytic syndrome due to infection
- Hemophagocytic lymphohistiocytosis with rheumatologic disease
- Hemophagocytic Syndrome, Infection Associated
- Haemophagocytic syndrome due to infection
- Haemophagocytic lymphohistiocytosis due to infection
- Reactive haemophagocytic syndrome
Frequently Asked Questions
What is the ICD-10 code for hemophagocytic syndrome, infection-associated?
The ICD-10-CM code for hemophagocytic syndrome, infection-associated is D76.2. The full clinical description is "Hemophagocytic syndrome, infection-associated". D76.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D76.2 mean?
ICD-10-CM code D76.2 represents “Hemophagocytic syndrome, infection-associated”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D76.2 a billable code?
Yes, D76.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D76.2 in?
D76.2 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D76.2?
D76.2 has Excludes1 notes indicating codes that cannot be used together with it, including: (Abt-) Letterer-Siwe disease (C96.0); eosinophilic granuloma (C96.6); Hand-Schüller-Christian disease (C96.5); and 12 more.
Are additional codes required with D76.2?
Yes, when using D76.2, also report: infectious agent or disease..
What SNOMED CT codes does D76.2 map to?
D76.2 maps to 6 SNOMED CT concepts: 234437005, 190959006, 430478003, 713444005, 1290500002, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D76.2?
D76.2 is linked to 1 UMLS Concept Unique Identifier: C0019068. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D76.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hemophagocytic syndrome, infection-associated affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D76.2?
D76.2 maps to the ICD-11 code: 3B62.5 (Haemophagocytic syndrome associated with infection).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.