A81.0
Non-billableCreutzfeldt-Jakob disease
Creutzfeldt-Jakob disease
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Includes
Conditions included under this code
- diseases generally recognized as communicable or transmissible
- diseases of the central nervous system caused by prions
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- certain localized infections - see body system-related chapters
- •postpolio syndromeG14
- •sequelae of poliomyelitisB91
- •sequelae of viral encephalitisB94.1
Excludes 2
Conditions not included here, but the patient may have both
Use Additional Code
Additional codes that should follow this code
- •code to identify resistance to antimicrobial drugsZ16
- code, if applicable, to identify:
- •dementia with anxiety, A4, B4, C4)F02.84, F02, F02, F02
- •dementia with behavioral disturbance, A1-, B1-, C1-)F02.81, F02, F02, F02
- •dementia with mood disturbance, A3, B3, C3)F02.83, F02, F02, F02
- •dementia with psychotic disturbance, A2, B2, C2)F02.82, F02, F02, F02
- •dementia without behavioral disturbance, A0, B0, C0)F02.80, F02, F02, F02
- •mild neurocognitive disorder due to known physiological conditionF06.7
Child Codes (3)
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(52)
UMLS
- CJ diseaseC0022336
- CJDC0022336
- CJD (Creutzfeldt Jakob Disease)C0022336
- CJD (Creutzfeldt Jakob disease)C0022336
- CJD (Creutzfeldt-Jakob Disease)C0022336
- CJD - Creutzfeldt-Jakob diseaseC0022336
- CJD CREUTZFELDT JAKOB DISC0022336
- CREUTZFELDT JAKOB DISC0022336
- CREUTZFELDT-JAKOB DISEASEC0022336
- Creutzfeld-Jacob diseaseC0022336
- Creutzfeld-Jakob diseaseC0022336
- Creutzfeldt Jacob DiseaseC0022336
- Creutzfeldt Jakob DiseaseC0022336
- Creutzfeldt Jakob SyndromeC0022336
- Creutzfeldt Jakob diseaseC0022336
- Creutzfeldt-Jacob DiseaseC0022336
- Creutzfeldt-Jakob DiseaseC0022336
- Creutzfeldt-Jakob SyndromeC0022336
- Creutzfeldt-Jakob diseaseC0022336
- Creutzfeldt-Jakob disease, unspecifiedC0022336
- Disease, Creutzfeldt JacobC0022336
- Disease, Creutzfeldt-JakobC0022336
- Disease, Jakob-CreutzfeldtC0022336
- Encephalopathies, Subacute SpongiformC0022336
- Encephalopathy, Subacute SpongiformC0022336
- JAKOB CREUTZFELDT DISC0022336
- JCD - Jakob-Creutzfeldt diseaseC0022336
- Jacob Disease, CreutzfeldtC0022336
- Jacob-Creutzfeld diseaseC0022336
- Jakob Creutzfeldt DiseaseC0022336
- Jakob Creutzfeldt SyndromeC0022336
- Jakob-Creutzfeldt DiseaseC0022336
- Jakob-Creutzfeldt SyndromeC0022336
- Jakob-Creutzfeldt diseaseC0022336
- Jakob-Creutzfeldt disease (disorder)C0022336
- Jakob-Creutzfeldt disease, unspecifiedC0022336
- SPONGIFORM ENCEPH SUBACUTEC0022336
- Spongiform Encephalopathies, SubacuteC0022336
- Spongiform Encephalopathy, SubacuteC0022336
- Subacute Spongiform EncephalopathiesC0022336
- Subacute Spongiform EncephalopathyC0022336
- Subacute spongiform encephalopathyC0022336
- Syndrome, Creutzfeldt-JakobC0022336
- Syndrome, Jakob-CreutzfeldtC0022336
- Transmissible virus dementiaC0022336
- cjdC0022336
- creutzfeldt jakob diseaseC0022336
- creutzfeldt jakob syndromeC0022336
- creutzfeldt-jakob diseaseC0022336
- creutzfeldt-jakob syndromeC0022336
- jakob-creutzfeldt diseaseC0022336
- jakob-creutzfeldt syndromeC0022336
Frequently Asked Questions
What is the ICD-10 code for creutzfeldt-jakob disease?
The ICD-10-CM code for creutzfeldt-jakob disease is A81.0. The full clinical description is "Creutzfeldt-Jakob disease". A81.0 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code A81.0 mean?
ICD-10-CM code A81.0 represents “Creutzfeldt-Jakob disease”. It is classified under Chapter 1: Certain Infectious and Parasitic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is A81.0 a billable code?
No, A81.0 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under A81.0.
What chapter is A81.0 in?
A81.0 is in Chapter 1: Certain Infectious and Parasitic Diseases (codes A00-B99).
What codes cannot be used with A81.0?
A81.0 has Excludes1 notes indicating codes that cannot be used together with it, including: certain localized infections - see body system-related chapters; postpolio syndrome (G14); sequelae of poliomyelitis (B91); and 1 more.
What are the subcategories under A81.0?
A81.0 has 3 child codes, including: A81.00 (Creutzfeldt-Jakob disease, unspecified), A81.01 (Variant Creutzfeldt-Jakob disease), A81.09 (Other Creutzfeldt-Jakob disease).
Are additional codes required with A81.0?
Yes, when using A81.0, also report: resistance to antimicrobial drugs (Z16.-); code, if applicable, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).
What are the UMLS CUIs for A81.0?
A81.0 is linked to 1 UMLS Concept Unique Identifier: C0022336. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does A81.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like creutzfeldt-jakob disease affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of A81.0?
A81.0 maps to the ICD-11 code: 8E02.0 (Genetic Creutzfeldt-Jakob disease).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.