A81.1
BillableSubacute sclerosing panencephalitis
Subacute sclerosing panencephalitis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Dawson's inclusion body encephalitis
- Van Bogaert's sclerosing leukoencephalopathy
Includes
Conditions included under this code
- diseases generally recognized as communicable or transmissible
- diseases of the central nervous system caused by prions
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- certain localized infections - see body system-related chapters
- •postpolio syndromeG14
- •sequelae of poliomyelitisB91
- •sequelae of viral encephalitisB94.1
Excludes 2
Conditions not included here, but the patient may have both
Use Additional Code
Additional codes that should follow this code
- •code to identify resistance to antimicrobial drugsZ16
- code, if applicable, to identify:
- •dementia with anxiety, A4, B4, C4)F02.84, F02, F02, F02
- •dementia with behavioral disturbance, A1-, B1-, C1-)F02.81, F02, F02, F02
- •dementia with mood disturbance, A3, B3, C3)F02.83, F02, F02, F02
- •dementia with psychotic disturbance, A2, B2, C2)F02.82, F02, F02, F02
- •dementia without behavioral disturbance, A0, B0, C0)F02.80, F02, F02, F02
- •mild neurocognitive disorder due to known physiological conditionF06.7
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(135)
SNOMED CT
- Post measles encephalitis111872008
- Dawson's inclusion body encephalitis192685000
- SSPE - Subacute sclerosing panencephalitis192685000
- Subacute sclerosing panencephalitis192685000
- Post-infectious encephalitis192727001
- Van Bogaert sclerosing leucoencephalitis359686005
- Van Bogaert sclerosing leukoencephalitis359686005
- Van Bogaert's sclerosing leucoencephalitis359686005
- Van Bogaert's sclerosing leukoencephalitis359686005
- Measles of the central nervous system406592004
- Dementia associated with viral encephalitis698726009
- White matter disorder caused by infection722601005
- Sequela of infection caused by Morbillivirus723110008
- Chronic infection of central nervous system846660004
- Chronic infectious disease of central nervous system846660004
- Encephalitis caused by Paramyxoviridae1163074009
- Paramyxoviridae encephalitis1163074009
- Encephalitis caused by Morbillivirus1163076006
- Morbillivirus encephalitis1163076006
- Dementia due to subacute sclerosing panencephalitis1259519008
UMLS
- Dawson's encephalitisC0038522
- Dawson's inclusion body encephalitisC0038522
- Encephalitis, Inclusion Body, MeaslesC0038522
- INCLUSION BODY ENCEPH MEASLESC0038522
- Immunosuppressive measles encephalitisC0038522
- Inclusion Body Encephalitis, MeaslesC0038522
- LEUKOENCEPH SUBACUTE SCLEROSINGC0038522
- LEUKOENCEPH VAN BOGAERTSC0038522
- Leukoencephalitides, Subacute SclerosingC0038522
- Leukoencephalitis, Subacute SclerosingC0038522
- Leukoencephalitis, Van BogaertC0038522
- Leukoencephalitis, Van Bogaert'sC0038522
- Leukoencephalitis, Van BogaertsC0038522
- MEASLES INCLUSION BODY ENCEPHC0038522
- MIBE - Measles inclusion body encephalitisC0038522
- Measles Inclusion Body EncephalitisC0038522
- Measles inclusion body encephalitisC0038522
- Measles inclusion body encephalitis (disorder)C0038522
- PANENCEPH SUBACUTE SCLEROSINGC0038522
- PANENCEPHALITIS, SUBACUTE SCLEROSINGC0038522
- Panencephalitides, Subacute SclerosingC0038522
- Panencephalitis, Subacute SclerosingC0038522
- SCLEROSING LEUKOENCEPH SUBACUTEC0038522
- SCLEROSING PANENCEPH SUBACUTEC0038522
- SSPEC0038522
- SSPE - Subacute sclerosing panencephalitisC0038522
- SUBACUTE SCLEROSING PANENCEPHC0038522
- SUBACUTE SCLEROSING PANENCEPHALITISC0038522
- Sclerosing Leukoencephalitides, SubacuteC0038522
- Sclerosing Leukoencephalitis, SubacuteC0038522
- Sclerosing Panencephalitides, SubacuteC0038522
- Sclerosing Panencephalitis, SubacuteC0038522
- Subacute Sclerosing LeukoencephalitidesC0038522
- Subacute Sclerosing LeukoencephalitisC0038522
- Subacute Sclerosing PanencephalitidesC0038522
- Subacute Sclerosing PanencephalitisC0038522
- Subacute sclerosing panencephalitisC0038522
- Subacute sclerosing panencephalitis (disorder)C0038522
- VAN BOGAERTS LEUKOENCEPHC0038522
- Van Bogaert LeukoencephalitisC0038522
- Van Bogaert encephalitisC0038522
- Van Bogaert sclerosing leucoencephalitisC0038522
- Van Bogaert sclerosing leukoencephalitisC0038522
- Van Bogaert's LeukoencephalitisC0038522
- Van Bogaert's sclerosing leucoencephalitisC0038522
- Van Bogaert's sclerosing leukoencephalitisC0038522
- Van Bogaert's sclerosing leukoencephalitis (disorder)C0038522
- Van Bogaerts LeukoencephalitisC0038522
- sspeC0038522
- subacute inclusion body encephalitisC0038522
- subacute sclerosing leukoencephalopathyC0038522
- subacute sclerosing panencephalitisC0038522
- subacute sclerosing panencephalitis (SSPE)C0038522
- van Bogaert's sclerosing leukoencephalitisC0038522
- Van Bogaert's sclerosing leukoencephalopathyC2900451
Clinical Terms
- subacute sclerosing panencephalitis (SSPE)
- Leukoencephalitis, Subacute Sclerosing
- Subacute Sclerosing Leukoencephalitis
- Panencephalitis, Subacute Sclerosing
- SUBACUTE SCLEROSING PANENCEPH
- Measles inclusion body encephalitis
- subacute sclerosing leukoencephalopathy
- VAN BOGAERTS LEUKOENCEPH
- Leukoencephalitis, Van Bogaert
- Van Bogaert sclerosing leukoencephalitis
- PANENCEPH SUBACUTE SCLEROSING
- INCLUSION BODY ENCEPH MEASLES
- Van Bogaert encephalitis
- Subacute sclerosing panencephalitis (disorder)
- Sequela of infection caused by Morbillivirus
- Dawson's inclusion body encephalitis
- Van Bogaert's sclerosing leucoencephalitis
- Encephalitis, Inclusion Body, Measles
- Inclusion Body Encephalitis, Measles
- SCLEROSING LEUKOENCEPH SUBACUTE
- SSPE - Subacute sclerosing panencephalitis
- Van Bogaert's sclerosing leukoencephalitis
- White matter disorder caused by infection
- MIBE - Measles inclusion body encephalitis
- Measles inclusion body encephalitis (disorder)
- LEUKOENCEPH VAN BOGAERTS
- Van Bogaert's sclerosing leukoencephalopathy
- Sclerosing Leukoencephalitides, Subacute
- Chronic infection of central nervous system
- Encephalitis caused by Morbillivirus
- MEASLES INCLUSION BODY ENCEPH
- SCLEROSING PANENCEPH SUBACUTE
- Leukoencephalitis, Van Bogaerts
- Sclerosing Panencephalitis, Subacute
- Van Bogaert Leukoencephalitis
- Dementia due to subacute sclerosing panencephalitis
- Panencephalitides, Subacute Sclerosing
- LEUKOENCEPH SUBACUTE SCLEROSING
- Dementia associated with viral encephalitis
- Van Bogaert's Leukoencephalitis
- Van Bogaert's sclerosing leukoencephalitis (disorder)
- Dawson's encephalitis
- Chronic infectious disease of central nervous system
- Paramyxoviridae encephalitis
- Leukoencephalitides, Subacute Sclerosing
- subacute inclusion body encephalitis
- Measles of the central nervous system
- Post measles encephalitis
- Van Bogaert sclerosing leucoencephalitis
- sspe
- Immunosuppressive measles encephalitis
- Sclerosing Leukoencephalitis, Subacute
- Van Bogaerts Leukoencephalitis
- Post-infectious encephalitis
- Morbillivirus encephalitis
- Sclerosing Panencephalitides, Subacute
- Subacute Sclerosing Panencephalitides
- Encephalitis caused by Paramyxoviridae
- Leukoencephalitis, Van Bogaert's
- Subacute Sclerosing Leukoencephalitides
Frequently Asked Questions
What is the ICD-10 code for subacute sclerosing panencephalitis?
The ICD-10-CM code for subacute sclerosing panencephalitis is A81.1. The full clinical description is "Subacute sclerosing panencephalitis". A81.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code A81.1 mean?
ICD-10-CM code A81.1 represents “Subacute sclerosing panencephalitis”. It is classified under Chapter 1: Certain Infectious and Parasitic Diseases and is a billable/specific code that can be used on a claim.
Is A81.1 a billable code?
Yes, A81.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is A81.1 in?
A81.1 is in Chapter 1: Certain Infectious and Parasitic Diseases (codes A00-B99).
What codes cannot be used with A81.1?
A81.1 has Excludes1 notes indicating codes that cannot be used together with it, including: certain localized infections - see body system-related chapters; postpolio syndrome (G14); sequelae of poliomyelitis (B91); and 1 more.
Are additional codes required with A81.1?
Yes, when using A81.1, also report: resistance to antimicrobial drugs (Z16.-); code, if applicable, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).
What SNOMED CT codes does A81.1 map to?
A81.1 maps to 12 SNOMED CT concepts: 846660004, 192685000, 698726009, 1259519008, 1163076006, and 7 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for A81.1?
A81.1 is linked to 2 UMLS Concept Unique Identifiers: C0038522, C2900451. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does A81.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like subacute sclerosing panencephalitis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of A81.1?
A81.1 maps to the ICD-11 code: 8A45.01 (Subacute sclerosing panencephalitis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.