AutoICD API

A81.00

Billable

Creutzfeldt-Jakob disease, unspecified

Creutzfeldt-Jakob disease, unspecified

Status

Billable / Specific

Block

A80-A89

Parent Code

A81.0

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Jakob-Creutzfeldt disease, unspecified

Includes

Conditions included under this code

  • diseases generally recognized as communicable or transmissible
  • diseases of the central nervous system caused by prions

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Use Additional Code

Additional codes that should follow this code

Related Codes(2)
A81.01

Variant Creutzfeldt-Jakob disease

BillableA81.09

Other Creutzfeldt-Jakob disease

Billable
Also Known As / Clinical Terms(111)

SNOMED CT

UMLS

Clinical Terms

  • CREUTZFELDT JAKOB DIS
  • Dementia due to Creutzfeldt Jakob disease
  • Creutzfeld-Jakob disease
  • Jakob-Creutzfeldt Syndrome
  • CJD (Creutzfeldt Jakob Disease)
  • Spongiform Encephalopathies, Subacute
  • CJ disease
  • Subacute spongiform encephalopathy
  • CJD
  • Jacob-Creutzfeld disease
  • Disease, Jakob-Creutzfeldt
  • jakob-creutzfeldt disease
  • Spongiform Encephalopathy, Subacute
  • Encephalopathies, Subacute Spongiform
  • Creutzfeld-Jacob disease
  • Jakob Creutzfeldt Syndrome
  • Disease, Creutzfeldt Jacob
  • Jakob-Creutzfeldt disease (disorder)
  • Creutzfeldt Jacob Disease
  • Creutzfeldt Jakob disease
  • Creutzfeldt-Jacob Disease
  • Creutzfeldt-Jakob Syndrome
  • Iatrogenic Jakob-Creutzfeldt disease
  • JAKOB CREUTZFELDT DIS
  • creutzfeldt jakob syndrome
  • Iatrogenic Creutzfeldt-Jakob disease
  • Subacute Spongiform Encephalopathies
  • Encephalopathy, Subacute Spongiform
  • Jacob Disease, Creutzfeldt
  • Syndrome, Jakob-Creutzfeldt
  • Cerebral degeneration due to Creutzfeldt-Jakob disease
  • Disease, Creutzfeldt-Jakob
  • SPONGIFORM ENCEPH SUBACUTE
  • CJD (Creutzfeldt-Jakob Disease)
  • Dementia due to Creutzfeldt-Jakob disease
  • Transmissible virus dementia
  • CJD CREUTZFELDT JAKOB DIS
  • Jakob Creutzfeldt Disease
  • Dementia due to prion disease
  • CJD - Creutzfeldt-Jakob disease
  • Jakob-Creutzfeldt disease, unspecified
  • Creutzfeldt Jakob disease following graft of dura
  • Syndrome, Creutzfeldt-Jakob
  • Graft infection
  • JCD - Jakob-Creutzfeldt disease
Frequently Asked Questions
What is the ICD-10 code for creutzfeldt-jakob disease, unspecified?

The ICD-10-CM code for creutzfeldt-jakob disease, unspecified is A81.00. The full clinical description is "Creutzfeldt-Jakob disease, unspecified". A81.00 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code A81.00 mean?

ICD-10-CM code A81.00 represents “Creutzfeldt-Jakob disease, unspecified”. It is classified under Chapter 1: Certain Infectious and Parasitic Diseases and is a billable/specific code that can be used on a claim.

Is A81.00 a billable code?

Yes, A81.00 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is A81.00 in?

A81.00 is in Chapter 1: Certain Infectious and Parasitic Diseases (codes A00-B99).

What codes cannot be used with A81.00?

A81.00 has Excludes1 notes indicating codes that cannot be used together with it, including: certain localized infections - see body system-related chapters; postpolio syndrome (G14); sequelae of poliomyelitis (B91); and 1 more.

Are additional codes required with A81.00?

Yes, when using A81.00, also report: resistance to antimicrobial drugs (Z16.-); code, if applicable, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).

What SNOMED CT codes does A81.00 map to?

A81.00 maps to 7 SNOMED CT concepts: 792004, 192818008, 1163119007, 429458009, 762350007, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for A81.00?

A81.00 is linked to 1 UMLS Concept Unique Identifier: C0022336. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does A81.00 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like creutzfeldt-jakob disease, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of A81.00?

There is no direct ICD-11 mapping available for A81.00 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.