Q26.8
BillableOther congenital malformations of great veins
Other congenital malformations of great veins
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Absence of vena cava (inferior) (superior)
- Azygos continuation of inferior vena cava
- Persistent left posterior cardinal vein
- Scimitar syndrome
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q26.0Congenital stenosis of vena cava
Q26.1Persistent left superior vena cava
Q26.2Total anomalous pulmonary venous connection
Q26.3Partial anomalous pulmonary venous connection
Q26.4Anomalous pulmonary venous connection, unspecified
Q26.5Anomalous portal venous connection
Q26.6Portal vein-hepatic artery fistula
Q26.9Congenital malformation of great vein, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(259)
SNOMED CT
- Congenital absence of vena cava2534005
- Congenital pulmonary vein stenosis11614003
- Congenital stenosis of pulmonary veins11614003
- Congenital absence of superior vena cava26865008
- Persistent left posterior cardinal vein38385001
- Pulmonary venolobar syndrome39905002
- Scimitar syndrome39905002
- Congenital hypoplasia of pulmonary artery54682008
- Pulmonary artery hypoplasia54682008
- Congenital hypoplasia of cardiac vein72252007
- Congenital absence of inferior vena cava74908007
- Congenital atresia of inferior vena cava93031005
- Inferior vena cava interruption93031005
- Interrupted inferior vena cava93031005
- Interrupted posterior vena cava93031005
- Congenital atresia of superior vena cava93033008
- Interrupted anterior vena cava93033008
- Congenital dilatation of inferior vena cava93056004
- Congenital dilated posterior vena cava93056004
- Congenital dilatation of superior vena cava93062009
- Congenital dilated anterior vena cava93062009
- Congenital malposition of inferior vena cava93328001
- Congenital malpositioned posterior vena cava93328001
- Congenital malposition of superior vena cava93354009
- Congenital malpositioned anterior vena cava93354009
- Sinus venosus atrial septal defect95268002
- Sinus venosus defect95268002
- Congenital pulmonary venous atrium128567004
- Congenital systemic venous atrium128568009
- Hypoplasia of cardiac vein204391005
- Absence of inferior vena cava204463001
- Absence of superior vena cava204464007
- Pulmonary vein stenosis234062003
- Congenital anomaly of valve of vein234125002
- Venous valvular anomaly234125002
- Congenital abnormality of great veins and coronary sinus234132006
- Abnormality of right superior vena cava253306009
- Atretic right superior vena cava253307000
- Absent right superior vena cava253308005
- Anomalous insertion of right superior vena cava to left atrium253310007
- Bilateral superior vena cava253311006
- Persistent left-sided superior vena cava253311006
- Absent bridging vein253312004
- Inferior vena cava interruption with left sided hemiazygos continuation253313009
- Inferior vena cava interruption with right sided azygos continuation253314003
- Inferior vena cava interruption with bilateral azygos continuation253315002
- Abnormal inferior vena caval connection253316001
- Inferior vena cava connecting to morphological left atrium253317005
- Inferior vena cava connecting to coronary sinus253318000
- Inferior vena cava to left of spine253319008
- Inferior cava to left of spine with right descending aorta253320002
- Mirror image great vessels253320002
- Prominent Eustachian valve253340009
- Prominent valve of inferior vena cava253340009
- Obstructive Eustachian valve253341008
- Prolapse of Eustachian valve253342001
- SVC - Sinus venosus defect with overriding superior vena cava253369000
- Sinus venosus defect with overriding superior vena cava253369000
- Superior sinus venosus defect253369000
- IVC - Sinus venosus defect with overriding inferior vena cava253370004
- Inferior sinus venosus defect253370004
- Sinus venosus defect with overriding inferior vena cava253370004
- Venous remnant280143008
- Pulmonary venous hypoplasia446432002
- Persistent common pulmonary vein447269006
- Congenital abnormality of hepatic vein447823004
- Atresia of left superior caval vein447902006
- Atresia of left superior vena cava447902006
- Right superior caval vein connecting to left atrium and right atrium448000003
- Right superior vena cava connecting to left atrium and right atrium448000003
- Atresia of systemic vein448005008
- Right ventricular outflow tract obstruction due to prolapse of Eustachian valve448082008
- Right superior caval vein connecting to coronary sinus448113007
- Right superior vena cava connecting to coronary sinus448113007
- Right inferior caval vein connecting to left atrium and right atrium448326002
- Right inferior vena cava connecting to left atrium and right atrium448326002
- Interrupted left inferior caval vein448501005
- Interrupted left inferior vena cava448501005
- Scimitar syndrome with additional anomalous pulmonary venous connection448595006
- Inferior caval vein anterior and same side as descending aorta448614002
- Inferior vena cava anterior and same side as descending aorta448614002
- Azygos continuation of inferior caval vein to right superior caval vein448620001
- Azygos continuation of inferior vena cava to right superior vena cava448620001
- Right inferior caval vein connecting to left sided atrium448631009
- Right inferior vena cava connecting to left sided atrium448631009
- Left inferior caval vein connecting to left atrium and right atrium448632002
- Left inferior vena cava connecting to left atrium and right atrium448632002
- Abnormality of right inferior caval vein448644004
- Abnormality of right inferior vena cava448644004
- Interrupted right inferior caval vein448782004
- Interrupted right inferior vena cava448782004
- Inferior caval vein connecting to right atrium and left atrium448965008
- Inferior vena cava connecting to right atrium and left atrium448965008
- Left sided azygos continuation of inferior caval vein to left superior caval vein449426008
- Left sided azygos continuation of inferior vena cava to left superior vena cava449426008
- Right superior caval vein connecting to coronary sinus and then to left sided atrium449458003
- Right superior vena cava connecting to coronary sinus and then to left sided atrium449458003
- Separate hepatic vein and inferior vena cava connections to heart449516003
- Separate hepatic venous and inferior caval venous connections to heart449516003
- Right superior caval vein persisting to coronary sinus and then to right sided atrium449523002
- Right superior vena cava persisting to coronary sinus and then to right sided atrium449523002
- Pulmonary venous hypertension due to congenital stenosis of pulmonary vein697928004
- Left-sided inferior vena cava781065009
- Transposition of inferior vena cava781065009
- Persistent Eustachian valve783011004
- Obstructed anomalous pulmonary venous pathway870323006
- Pulmonary hypertension due to developmental abnormality1010627004
- Congenital hypoplasia of right side of chest1144410003
- Congenital atresia of inferior vena cava without azygos continuation1230062001
- Inferior vena cava interruption without azygos continuation1230062001
- Azygos continuation of inferior caval vein1234908005
- Congenital azygos continuation of inferior vena cava1234908005
- Inferior vena cava interruption with azygos continuation1234908005
- Primary congenital aneurysm of superior vena cava1366399005
- Primary congenital superior vena cava aneurysm1366399005
- Primary congenital aneurysm of inferior vena cava1366400003
- Primary congenital inferior vena cava aneurysm1366400003
UMLS
- Absence of vena cava (inferior) (superior)C2910141
- Anomaly, ScimitarC0036400
- Pulmonary venolobar syndromeC0036400
- SCIMITAR ANOMALYC0036400
- SCIMITAR SYNDROMEC0036400
- Scimitar AnomalyC0036400
- Scimitar SyndromeC0036400
- Scimitar anomalyC0036400
- Scimitar syndromeC0036400
- Scimitar syndrome (disorder)C0036400
- Azygos continuation of inferior caval veinC1859772
- Azygos continuation of inferior vena cavaC1859772
- Congenital azygos continuation of inferior vena cavaC1859772
- Congenital azygos continuation of inferior vena cava (disorder)C1859772
- Inferior vena cava interruption with azygos continuationC1859772
- Other congenital malformations of great veinsC0478003
- Persistent left posterior cardinal veinC0265955
- Persistent left posterior cardinal vein (disorder)C0265955
Clinical Terms
- Sinus venosus defect with overriding inferior vena cava
- Inferior vena cava connecting to morphological left atrium
- Interrupted right inferior vena cava
- Right superior vena cava connecting to left atrium and right atrium
- Persistent left posterior cardinal vein (disorder)
- Congenital dilated posterior vena cava
- Congenital azygos continuation of inferior vena cava (disorder)
- Abnormal inferior vena caval connection
- Congenital malposition of superior vena cava
- Left inferior vena cava connecting to left atrium and right atrium
- Transposition of inferior vena cava
- Left inferior caval vein connecting to left atrium and right atrium
- Right superior caval vein connecting to coronary sinus
- Obstructive Eustachian valve
- Right inferior caval vein connecting to left sided atrium
- Left sided azygos continuation of inferior caval vein to left superior caval vein
- Congenital absence of vena cava
- Mirror image great vessels
- Right superior caval vein connecting to left atrium and right atrium
- Interrupted anterior vena cava
- Azygos continuation of inferior vena cava to right superior vena cava
- Venous valvular anomaly
- Absence of vena cava (inferior) (superior)
- Abnormality of right superior vena cava
- Scimitar anomaly
- Congenital pulmonary venous atrium
- Atresia of left superior caval vein
- Obstructed anomalous pulmonary venous pathway
- Left sided azygos continuation of inferior vena cava to left superior vena cava
- SCIMITAR SYNDROME
- Persistent left-sided superior vena cava
- Inferior vena cava connecting to right atrium and left atrium
- Sinus venosus defect
- Congenital hypoplasia of cardiac vein
- Interrupted posterior vena cava
- Pulmonary venous hypoplasia
- Superior sinus venosus defect
- Congenital dilatation of inferior vena cava
- Congenital absence of inferior vena cava
- Pulmonary artery hypoplasia
- Azygos continuation of inferior vena cava
- Right superior caval vein connecting to coronary sinus and then to left sided atrium
- Interrupted left inferior caval vein
- Atretic right superior vena cava
- Prominent valve of inferior vena cava
- Pulmonary vein stenosis
- Pulmonary venolobar syndrome
- Sinus venosus defect with overriding superior vena cava
- Anomaly, Scimitar
- Congenital malpositioned posterior vena cava
- Congenital dilatation of superior vena cava
- Azygos continuation of inferior caval vein
- Bilateral superior vena cava
- Hypoplasia of cardiac vein
- Interrupted inferior vena cava
- Congenital hypoplasia of pulmonary artery
- Scimitar syndrome with additional anomalous pulmonary venous connection
- Right superior vena cava connecting to coronary sinus
- Atresia of systemic vein
- Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
- Congenital pulmonary vein stenosis
- Primary congenital aneurysm of inferior vena cava
- Abnormality of right inferior caval vein
- Congenital malposition of inferior vena cava
- Azygos continuation of inferior caval vein to right superior caval vein
- Inferior sinus venosus defect
- Primary congenital inferior vena cava aneurysm
- Interrupted left inferior vena cava
- Absent right superior vena cava
- Inferior vena cava anterior and same side as descending aorta
- Persistent left posterior cardinal vein
- Right inferior vena cava connecting to left sided atrium
- Absence of inferior vena cava
- Absent bridging vein
- Inferior vena cava interruption without azygos continuation
- Inferior vena cava interruption with bilateral azygos continuation
- SVC - Sinus venosus defect with overriding superior vena cava
- Congenital atresia of inferior vena cava without azygos continuation
- Pulmonary hypertension due to developmental abnormality
- Inferior caval vein anterior and same side as descending aorta
- Primary congenital superior vena cava aneurysm
- Prolapse of Eustachian valve
- Right superior vena cava connecting to coronary sinus and then to left sided atrium
- Inferior cava to left of spine with right descending aorta
- Congenital dilated anterior vena cava
- Inferior vena cava interruption with azygos continuation
- Congenital anomaly of valve of vein
- Right inferior caval vein connecting to left atrium and right atrium
- Congenital stenosis of pulmonary veins
- Congenital systemic venous atrium
- Right inferior vena cava connecting to left atrium and right atrium
- Left-sided inferior vena cava
- Congenital malpositioned anterior vena cava
- Interrupted right inferior caval vein
- Primary congenital aneurysm of superior vena cava
- Inferior vena cava interruption
- Inferior vena cava interruption with right sided azygos continuation
- Right superior caval vein persisting to coronary sinus and then to right sided atrium
- Inferior vena cava interruption with left sided hemiazygos continuation
- Scimitar syndrome (disorder)
- Atresia of left superior vena cava
- Congenital absence of superior vena cava
- Congenital azygos continuation of inferior vena cava
- Inferior caval vein connecting to right atrium and left atrium
- Right superior vena cava persisting to coronary sinus and then to right sided atrium
- Abnormality of right inferior vena cava
- Inferior vena cava connecting to coronary sinus
- Absence of superior vena cava
- Prominent Eustachian valve
- Congenital abnormality of hepatic vein
- Congenital atresia of inferior vena cava
- Anomalous insertion of right superior vena cava to left atrium
- Persistent common pulmonary vein
- Congenital atresia of superior vena cava
- Inferior vena cava to left of spine
- Venous remnant
- Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
- IVC - Sinus venosus defect with overriding inferior vena cava
- Persistent Eustachian valve
- Sinus venosus atrial septal defect
- Congenital abnormality of great veins and coronary sinus
- Separate hepatic venous and inferior caval venous connections to heart
- Congenital hypoplasia of right side of chest
- Separate hepatic vein and inferior vena cava connections to heart
Frequently Asked Questions
What is the ICD-10 code for other congenital malformations of great veins?
The ICD-10-CM code for other congenital malformations of great veins is Q26.8. The full clinical description is "Other congenital malformations of great veins". Q26.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q26.8 mean?
ICD-10-CM code Q26.8 represents “Other congenital malformations of great veins”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q26.8 a billable code?
Yes, Q26.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q26.8 in?
Q26.8 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q26.8 map to?
Q26.8 maps to 75 SNOMED CT concepts: 253316001, 448644004, 253306009, 204463001, 204464007, and 70 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q26.8?
Q26.8 is linked to 5 UMLS Concept Unique Identifiers: C2910141, C0036400, C1859772, C0478003, C0265955. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q26.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital malformations of great veins affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q26.8?
Q26.8 maps to the ICD-11 code: LA86.Z (Congenital anomaly of mediastinal vein, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.