AutoICD API

Q26.8

Billable

Other congenital malformations of great veins

Other congenital malformations of great veins

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(259)

SNOMED CT

Clinical Terms

  • Sinus venosus defect with overriding inferior vena cava
  • Inferior vena cava connecting to morphological left atrium
  • Interrupted right inferior vena cava
  • Right superior vena cava connecting to left atrium and right atrium
  • Persistent left posterior cardinal vein (disorder)
  • Congenital dilated posterior vena cava
  • Congenital azygos continuation of inferior vena cava (disorder)
  • Abnormal inferior vena caval connection
  • Congenital malposition of superior vena cava
  • Left inferior vena cava connecting to left atrium and right atrium
  • Transposition of inferior vena cava
  • Left inferior caval vein connecting to left atrium and right atrium
  • Right superior caval vein connecting to coronary sinus
  • Obstructive Eustachian valve
  • Right inferior caval vein connecting to left sided atrium
  • Left sided azygos continuation of inferior caval vein to left superior caval vein
  • Congenital absence of vena cava
  • Mirror image great vessels
  • Right superior caval vein connecting to left atrium and right atrium
  • Interrupted anterior vena cava
  • Azygos continuation of inferior vena cava to right superior vena cava
  • Venous valvular anomaly
  • Absence of vena cava (inferior) (superior)
  • Abnormality of right superior vena cava
  • Scimitar anomaly
  • Congenital pulmonary venous atrium
  • Atresia of left superior caval vein
  • Obstructed anomalous pulmonary venous pathway
  • Left sided azygos continuation of inferior vena cava to left superior vena cava
  • SCIMITAR SYNDROME
  • Persistent left-sided superior vena cava
  • Inferior vena cava connecting to right atrium and left atrium
  • Sinus venosus defect
  • Congenital hypoplasia of cardiac vein
  • Interrupted posterior vena cava
  • Pulmonary venous hypoplasia
  • Superior sinus venosus defect
  • Congenital dilatation of inferior vena cava
  • Congenital absence of inferior vena cava
  • Pulmonary artery hypoplasia
  • Azygos continuation of inferior vena cava
  • Right superior caval vein connecting to coronary sinus and then to left sided atrium
  • Interrupted left inferior caval vein
  • Atretic right superior vena cava
  • Prominent valve of inferior vena cava
  • Pulmonary vein stenosis
  • Pulmonary venolobar syndrome
  • Sinus venosus defect with overriding superior vena cava
  • Anomaly, Scimitar
  • Congenital malpositioned posterior vena cava
  • Congenital dilatation of superior vena cava
  • Azygos continuation of inferior caval vein
  • Bilateral superior vena cava
  • Hypoplasia of cardiac vein
  • Interrupted inferior vena cava
  • Congenital hypoplasia of pulmonary artery
  • Scimitar syndrome with additional anomalous pulmonary venous connection
  • Right superior vena cava connecting to coronary sinus
  • Atresia of systemic vein
  • Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
  • Congenital pulmonary vein stenosis
  • Primary congenital aneurysm of inferior vena cava
  • Abnormality of right inferior caval vein
  • Congenital malposition of inferior vena cava
  • Azygos continuation of inferior caval vein to right superior caval vein
  • Inferior sinus venosus defect
  • Primary congenital inferior vena cava aneurysm
  • Interrupted left inferior vena cava
  • Absent right superior vena cava
  • Inferior vena cava anterior and same side as descending aorta
  • Persistent left posterior cardinal vein
  • Right inferior vena cava connecting to left sided atrium
  • Absence of inferior vena cava
  • Absent bridging vein
  • Inferior vena cava interruption without azygos continuation
  • Inferior vena cava interruption with bilateral azygos continuation
  • SVC - Sinus venosus defect with overriding superior vena cava
  • Congenital atresia of inferior vena cava without azygos continuation
  • Pulmonary hypertension due to developmental abnormality
  • Inferior caval vein anterior and same side as descending aorta
  • Primary congenital superior vena cava aneurysm
  • Prolapse of Eustachian valve
  • Right superior vena cava connecting to coronary sinus and then to left sided atrium
  • Inferior cava to left of spine with right descending aorta
  • Congenital dilated anterior vena cava
  • Inferior vena cava interruption with azygos continuation
  • Congenital anomaly of valve of vein
  • Right inferior caval vein connecting to left atrium and right atrium
  • Congenital stenosis of pulmonary veins
  • Congenital systemic venous atrium
  • Right inferior vena cava connecting to left atrium and right atrium
  • Left-sided inferior vena cava
  • Congenital malpositioned anterior vena cava
  • Interrupted right inferior caval vein
  • Primary congenital aneurysm of superior vena cava
  • Inferior vena cava interruption
  • Inferior vena cava interruption with right sided azygos continuation
  • Right superior caval vein persisting to coronary sinus and then to right sided atrium
  • Inferior vena cava interruption with left sided hemiazygos continuation
  • Scimitar syndrome (disorder)
  • Atresia of left superior vena cava
  • Congenital absence of superior vena cava
  • Congenital azygos continuation of inferior vena cava
  • Inferior caval vein connecting to right atrium and left atrium
  • Right superior vena cava persisting to coronary sinus and then to right sided atrium
  • Abnormality of right inferior vena cava
  • Inferior vena cava connecting to coronary sinus
  • Absence of superior vena cava
  • Prominent Eustachian valve
  • Congenital abnormality of hepatic vein
  • Congenital atresia of inferior vena cava
  • Anomalous insertion of right superior vena cava to left atrium
  • Persistent common pulmonary vein
  • Congenital atresia of superior vena cava
  • Inferior vena cava to left of spine
  • Venous remnant
  • Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
  • IVC - Sinus venosus defect with overriding inferior vena cava
  • Persistent Eustachian valve
  • Sinus venosus atrial septal defect
  • Congenital abnormality of great veins and coronary sinus
  • Separate hepatic venous and inferior caval venous connections to heart
  • Congenital hypoplasia of right side of chest
  • Separate hepatic vein and inferior vena cava connections to heart
Frequently Asked Questions
What is the ICD-10 code for other congenital malformations of great veins?

The ICD-10-CM code for other congenital malformations of great veins is Q26.8. The full clinical description is "Other congenital malformations of great veins". Q26.8 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q26.8 mean?

ICD-10-CM code Q26.8 represents “Other congenital malformations of great veins”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q26.8 a billable code?

Yes, Q26.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q26.8 in?

Q26.8 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What SNOMED CT codes does Q26.8 map to?

Q26.8 maps to 75 SNOMED CT concepts: 253316001, 448644004, 253306009, 204463001, 204464007, and 70 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q26.8?

Q26.8 is linked to 5 UMLS Concept Unique Identifiers: C2910141, C0036400, C1859772, C0478003, C0265955. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q26.8 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital malformations of great veins affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q26.8?

Q26.8 maps to the ICD-11 code: LA86.Z (Congenital anomaly of mediastinal vein, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.