Q26.4
BillableAnomalous pulmonary venous connection, unspecified
Anomalous pulmonary venous connection, unspecified
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q26.0Congenital stenosis of vena cava
Q26.1Persistent left superior vena cava
Q26.2Total anomalous pulmonary venous connection
Q26.3Partial anomalous pulmonary venous connection
Q26.5Anomalous portal venous connection
Q26.6Portal vein-hepatic artery fistula
Q26.8Other congenital malformations of great veins
Q26.9Congenital malformation of great vein, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(144)
SNOMED CT
- Anomalous pulmonary venous drainage to abdominal portion of inferior vena cava22750001
- Anomalous pulmonary venous drainage to coronary sinus29934004
- Anomalous pulmonary venous drainage to hepatic veins32194006
- Transposition of pulmonary veins36422005
- Anomalous pulmonary venous drainage to right atrium37639005
- Pulmonary venolobar syndrome39905002
- Scimitar syndrome39905002
- Congenital hypoplasia of pulmonary artery54682008
- Pulmonary artery hypoplasia54682008
- APVC - Anomalous pulmonary venous connection59631007
- APVD - Anomalous pulmonary venous drainage59631007
- Anomalous pulmonary venous connection59631007
- Anomalous pulmonary venous drainage59631007
- Anomalous pulmonary venous drainage to superior vena cava66858001
- Congenital pulmonary vein confluence128566008
- PA - Pulmonary vein atresia204467000
- Pulmonary vein atresia204467000
- Abnormal inferior vena caval connection253316001
- Anomalous termination of right pulmonary vein253321003
- Obstructed pulmonary venous connection253322005
- Anomalous pulmonary venous connection to portal system445296005
- Infracardiac location of anomalous pulmonary venous connections to portal system445296005
- Anomalous pulmonary venous connection to inferior vena cava445371009
- Infracardiac location of anomalous pulmonary venous connections to inferior caval vein445371009
- Anomalous pulmonary venous connection to bilateral isomeric atriums445543002
- Intracardiac location of anomalous pulmonary venous connections to bilateral isomeric atriums445543002
- Obstructed pulmonary venous connection at coronary sinus orifice446890001
- Pulmonary venous confluence remote from left atrium447663001
- Pulmonary venous confluence in direct proximity to left atrium447691009
- Pulmonary venous confluence in horizontal orientation447813008
- Pulmonary venous confluence in vertical orientation447814002
- Congenital abnormality of hepatic vein447823004
- Cor triatriatum with some pulmonary veins to proximal chamber448320008
- Divided left atrium with some pulmonary veins to proximal chamber448320008
- Anomalous pulmonary to systemic collateral vein448486000
- Anomalous pulmonary venous connection of mixed type448487009
- Infracardiac location of anomalous pulmonary venous connection448499002
- Intracardiac location of anomalous pulmonary venous connection448500006
- Scimitar syndrome with additional anomalous pulmonary venous connection448595006
- Supracardiac location of anomalous pulmonary venous connection448728003
- Intracardiac location of anomalous pulmonary venous connection to coronary sinus449425007
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium449429001
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium449429001
- Supracardiac location of anomalous pulmonary venous connection to left superior caval vein449434002
- Supracardiac location of anomalous pulmonary venous connection to left superior vena cava449434002
- Infracardiac location of anomalous pulmonary venous connection with two descending veins449435001
- Cor triatriatum with some pulmonary veins to proximal chamber draining to left atrium449436000
- Divided left atrium with some pulmonary veins to proximal chamber draining to left atrium449436000
- Supracardiac location of anomalous pulmonary venous connection to left sided vertical vein449443006
- Infracardiac location of anomalous pulmonary venous connection to hepatic vein449444000
- Supracardiac location of anomalous pulmonary venous connection to hemiazygos vein449451009
- Intracardiac location of anomalous pulmonary venous connection to right atrium449452002
- Supracardiac location of anomalous pulmonary venous connection to right sided vertical vein449493005
- Supracardiac location of anomalous pulmonary venous connection to right superior caval vein449494004
- Supracardiac location of anomalous pulmonary venous connection to right superior vena cava449494004
- Infracardiac location of anomalous pulmonary venous connection to patent ductus venosus449495003
- Infracardiac location of anomalous pulmonary venous connection to patent venous duct449495003
- Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atria449514000
- Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atriums449514000
- Anomalous pulmonary venous connection of mixed type with two pulmonary venous confluences449521000
- Supracardiac location of anomalous pulmonary venous connection to azygos vein449533005
- Cor triatriatum with some pulmonary veins to proximal chamber draining to left atrium and others connecting directly to left atrium449593007
- Divided left atrium with some pulmonary veins to proximal chamber draining to left atrium and others connecting directly to left atrium449593007
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium and others connecting anomalously449595000
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium and others connecting anomalously449595000
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium and others connecting directly to left atrium449596004
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium and others connecting directly to left atrium449596004
- Congenital hypoplasia of right side of chest1144410003
UMLS
- APVC - Anomalous pulmonary venous connectionC0265916
- APVD - Anomalous pulmonary venous drainageC0265916
- Anomalous pulmonary venous connectionC0265916
- Anomalous pulmonary venous connection, unspecifiedC0265916
- Anomalous pulmonary venous dischargeC0265916
- Anomalous pulmonary venous drainageC0265916
- Anomalous pulmonary venous drainage (disorder)C0265916
Clinical Terms
- Infracardiac location of anomalous pulmonary venous connection with two descending veins
- Obstructed pulmonary venous connection
- Divided left atrium with some pulmonary veins to proximal chamber draining to left atrium and others connecting directly to left atrium
- Supracardiac location of anomalous pulmonary venous connection to left sided vertical vein
- APVD - Anomalous pulmonary venous drainage
- Divided left atrium with some pulmonary veins to proximal chamber
- Anomalous pulmonary venous connection to portal system
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium and others connecting directly to left atrium
- Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atria
- Anomalous pulmonary venous connection of mixed type
- Intracardiac location of anomalous pulmonary venous connection to right atrium
- Intracardiac location of anomalous pulmonary venous connections to bilateral isomeric atriums
- Supracardiac location of anomalous pulmonary venous connection to azygos vein
- Supracardiac location of anomalous pulmonary venous connection
- Transposition of pulmonary veins
- Infracardiac location of anomalous pulmonary venous connections to inferior caval vein
- Pulmonary venous confluence remote from left atrium
- Anomalous pulmonary venous connection to bilateral isomeric atriums
- Infracardiac location of anomalous pulmonary venous connection to patent ductus venosus
- Anomalous pulmonary venous drainage to coronary sinus
- Intracardiac location of anomalous pulmonary venous connection to coronary sinus
- Divided left atrium with some pulmonary veins to proximal chamber draining to left atrium
- Congenital hypoplasia of right side of chest
- Infracardiac location of anomalous pulmonary venous connection to patent venous duct
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium and others connecting anomalously
- Supracardiac location of anomalous pulmonary venous connection to hemiazygos vein
- Cor triatriatum with some pulmonary veins to proximal chamber draining to left atrium
- Intracardiac location of anomalous pulmonary venous connection
- Anomalous pulmonary venous connection of mixed type with two pulmonary venous confluences
- Anomalous pulmonary venous drainage to hepatic veins
- Pulmonary artery hypoplasia
- Pulmonary venous confluence in direct proximity to left atrium
- Scimitar syndrome
- Cor triatriatum with some pulmonary veins to proximal chamber
- Cor triatriatum with some pulmonary veins to proximal chamber draining to right atrium
- Abnormal inferior vena caval connection
- Pulmonary venous confluence in horizontal orientation
- Congenital abnormality of hepatic vein
- Cor triatriatum with some pulmonary veins to proximal chamber draining to left atrium and others connecting directly to left atrium
- Infracardiac location of anomalous pulmonary venous connection to hepatic vein
- Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atriums
- Supracardiac location of anomalous pulmonary venous connection to left superior caval vein
- Infracardiac location of anomalous pulmonary venous connections to portal system
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium and others connecting anomalously
- Anomalous pulmonary venous drainage to right atrium
- Pulmonary venolobar syndrome
- Obstructed pulmonary venous connection at coronary sinus orifice
- Supracardiac location of anomalous pulmonary venous connection to right sided vertical vein
- Anomalous pulmonary venous discharge
- Supracardiac location of anomalous pulmonary venous connection to left superior vena cava
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium and others connecting directly to left atrium
- Infracardiac location of anomalous pulmonary venous connection
- Congenital hypoplasia of pulmonary artery
- Anomalous pulmonary venous drainage to superior vena cava
- Anomalous termination of right pulmonary vein
- Anomalous pulmonary venous connection to inferior vena cava
- Scimitar syndrome with additional anomalous pulmonary venous connection
- Anomalous pulmonary venous drainage (disorder)
- APVC - Anomalous pulmonary venous connection
- Anomalous pulmonary venous drainage
- Supracardiac location of anomalous pulmonary venous connection to right superior caval vein
- Congenital pulmonary vein confluence
- Anomalous pulmonary to systemic collateral vein
- Pulmonary vein atresia
- Anomalous pulmonary venous drainage to abdominal portion of inferior vena cava
- PA - Pulmonary vein atresia
- Supracardiac location of anomalous pulmonary venous connection to right superior vena cava
- Pulmonary venous confluence in vertical orientation
- Divided left atrium with some pulmonary veins to proximal chamber draining to right atrium
Frequently Asked Questions
What is the ICD-10 code for anomalous pulmonary venous connection, unspecified?
The ICD-10-CM code for anomalous pulmonary venous connection, unspecified is Q26.4. The full clinical description is "Anomalous pulmonary venous connection, unspecified". Q26.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q26.4 mean?
ICD-10-CM code Q26.4 represents “Anomalous pulmonary venous connection, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q26.4 a billable code?
Yes, Q26.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q26.4 in?
Q26.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q26.4 map to?
Q26.4 maps to 49 SNOMED CT concepts: 59631007, 253316001, 448486000, 448487009, 449521000, and 44 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q26.4?
Q26.4 is linked to 1 UMLS Concept Unique Identifier: C0265916. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q26.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like anomalous pulmonary venous connection, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q26.4?
Q26.4 maps to the ICD-11 code: LA86.2Z (Anomalous pulmonary venous connection, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.