Q26.5
BillableAnomalous portal venous connection
Anomalous portal venous connection
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q26.0Congenital stenosis of vena cava
Q26.1Persistent left superior vena cava
Q26.2Total anomalous pulmonary venous connection
Q26.3Partial anomalous pulmonary venous connection
Q26.4Anomalous pulmonary venous connection, unspecified
Q26.6Portal vein-hepatic artery fistula
Q26.8Other congenital malformations of great veins
Q26.9Congenital malformation of great vein, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(35)
SNOMED CT
- Portal systemic vascular shunt disorder128058007
- Portal-systemic shunt anomaly128058007
- Portasystemic vascular shunt disorder128058007
- Partial portal-systemic vascular shunt128059004
- Congenital portal-systemic shunt128062001
- Congenital portosystemic shunt128062001
- Congenital portosystemic venous fistula128062001
- Congenital extrahepatic portal-systemic shunt128063006
- Congenital extrahepatic portasystemic shunt128063006
- Congenital absence of portal vein128064000
- Congenital partial portal-systemic shunt128065004
- Congenital partial portasystemic shunt128065004
- Congenital splenorenal shunt128066003
- Congenital intrahepatic portal-systemic shunt128067007
- Anomalous portal vein termination204460003
UMLS
Clinical Terms
- Anomalous portal vein termination
- Anomalous pulmonary venous drainage to hepatic veins (disorder)
- Congenital intrahepatic portal-systemic shunt
- Congenital extrahepatic portal-systemic shunt
- Portasystemic vascular shunt disorder
- Congenital absence of portal vein
- Congenital partial portal-systemic shunt
- Congenital partial portasystemic shunt
- Congenital portosystemic shunt
- Congenital extrahepatic portasystemic shunt
- Congenital portosystemic venous fistula
- Partial portal-systemic vascular shunt
- Portal systemic vascular shunt disorder
- Congenital splenorenal shunt
- Portal-systemic shunt anomaly
- Congenital portal-systemic shunt
- Anomalous pulmonary venous drainage to hepatic veins
Frequently Asked Questions
What is the ICD-10 code for anomalous portal venous connection?
The ICD-10-CM code for anomalous portal venous connection is Q26.5. The full clinical description is "Anomalous portal venous connection". Q26.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q26.5 mean?
ICD-10-CM code Q26.5 represents “Anomalous portal venous connection”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q26.5 a billable code?
Yes, Q26.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q26.5 in?
Q26.5 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q26.5 map to?
Q26.5 maps to 9 SNOMED CT concepts: 204460003, 128064000, 128063006, 128067007, 128065004, and 4 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q26.5?
Q26.5 is linked to 1 UMLS Concept Unique Identifier: C0265922. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q26.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like anomalous portal venous connection affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q26.5?
Q26.5 maps to the ICD-11 code: LA90.21 (Congenital portosystemic shunt).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.