Q81.2
BillableEpidermolysis bullosa dystrophica
Epidermolysis bullosa dystrophica
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(144)
SNOMED CT
- Dominant dystrophic epidermolysis bullosa with absence of skin2689001
- Epidermolysis bullosa dystrophica, Bart type2689001
- Dysplastic epidermolysis bullosa dystrophica48528004
- Polydysplastic epidermolysis bullosa48528004
- Recessive dystrophic epidermolysis bullosa48528004
- Albopapuloid dystrophic epidermolysis bullosa of Pasini75875004
- Dominant dystrophic epidermolysis bullosa of Pasini75875004
- Dominant dystrophic epidermolysis bullosa, albopapular type75875004
- Epidermolysis bullosa dystrophica, Pasini type75875004
- Cockayne Touraine epidermolysis bullosa111389006
- Dominant dystrophic epidermolysis bullosa111389006
- Epidermolysis bullosa dystrophica dominans111389006
- Epidermolysis bullosa, Cockayne-Touraine type111389006
- Hyperplastic dystrophic epidermolysis bullosa111389006
- Hyperplastic epidermolysis bullosa111389006
- EBR 3254176007
- Epidermolysis bullosa dystrophica neurotrophica254176007
- Goldscheider disease254176007
- Goldscheider's disease254176007
- Progressive recessive dystrophic epidermolysis bullosa254176007
- DEB - Dystrophic epidermolysis bullosa254185007
- Dystrophic epidermolysis bullosa254185007
- Epidermolysis bullosa dystrophica254185007
- Localised dystrophic epidermolysis bullosa254186008
- Localized dystrophic epidermolysis bullosa254186008
- Localised recessive dystrophic epidermolysis bullosa254187004
- Localized recessive dystrophic epidermolysis bullosa254187004
- Generalised dystrophic epidermolysis bullosa254188009
- Generalized dystrophic epidermolysis bullosa254188009
- Generalised recessive dystrophic epidermolysis bullosa mitis254189001
- Generalized recessive dystrophic epidermolysis bullosa mitis254189001
- Dystrophic epidermolysis bullosa generalisata mitis403808006
- Generalised recessive non-mutilating dystrophic epidermolysis bullosa403808006
- Generalized recessive non-mutilating dystrophic epidermolysis bullosa403808006
- Dystrophic epidermolysis bullosa inverse type403809003
- Dystrophic epidermolysis bullosa nails only722436002
- Nails only DEB (dystrophic epidermolysis bullosa)722436002
- Autosomal recessive dystrophic epidermolysis bullosa Hallopeau Siemens type723716009
- Autosomal recessive dystrophic epidermolysis bullosa generalisata gravis723716009
- Severe generalised recessive dystrophic epidermolysis bullosa723716009
- Severe generalized recessive dystrophic epidermolysis bullosa723716009
- RDEB-O - recessive dystrophic epidermolysis bullosa-generalised other725407006
- RDEB-O - recessive dystrophic epidermolysis bullosa-generalized other725407006
- Recessive dystrophic epidermolysis bullosa non-Hallopeau Siemens type725407006
- Centripetal recessive dystrophic epidermolysis bullosa725419003
- Centripetalis recessive dystrophic epidermolysis bullosa725419003
- RDEB-Ce - recessive dystrophic epidermolysis bullosa centripetalis725419003
- Acral DEB (dystrophic epidermolysis bullosa)733638006
- Acral dystrophic epidermolysis bullosa733638006
- Autosomal dominant generalised dystrophic epidermolysis bullosa1231284001
- Autosomal dominant generalized dystrophic epidermolysis bullosa1231284001
- DDEB (dominant dystrophic epidermolysis bullosa) intermediate1231284001
- Generalised DDEB (generalised dystrophic epidermolysis bullosa)1231284001
- Generalized DDEB (generalized dystrophic epidermolysis bullosa)1231284001
UMLS
- Bullosa Dystrophica, EpidermolysisC0079294
- Bullosa Dystrophicas, EpidermolysisC0079294
- Bullosa, Dystrophic EpidermolysisC0079294
- Bullosas, Dystrophic EpidermolysisC0079294
- DEBC0079294
- DEB - Dystrophic epidermolysis bullosaC0079294
- Dystrophic Epidermolysis BullosaC0079294
- Dystrophic Epidermolysis BullosasC0079294
- Dystrophic epidermolysis bullosaC0079294
- Dystrophic epidermolysis bullosa (disorder)C0079294
- Dystrophica, Epidermolysis BullosaC0079294
- Dystrophicas, Epidermolysis BullosaC0079294
- Epidermolysis Bullosa DystrophicaC0079294
- Epidermolysis Bullosa DystrophicasC0079294
- Epidermolysis Bullosa, DystrophicC0079294
- Epidermolysis Bullosas, DystrophicC0079294
- Epidermolysis bullosa dystrophicaC0079294
- Epidermolysis bullosa, dystrophicC0079294
- bullosa dystrophic epidermolysisC0079294
- bullosa dystrophica epidermolysisC0079294
- dystrophic epidermolysis bullosaC0079294
- epidermolysis bullosa dystrophicC0079294
Clinical Terms
- Dystrophic epidermolysis bullosa
- DEB
- Dominant dystrophic epidermolysis bullosa with absence of skin
- Generalized dystrophic epidermolysis bullosa
- Epidermolysis bullosa, dystrophic
- Localized dystrophic epidermolysis bullosa
- bullosa dystrophic epidermolysis
- Nails only DEB (dystrophic epidermolysis bullosa)
- Generalised recessive non-mutilating dystrophic epidermolysis bullosa
- Acral dystrophic epidermolysis bullosa
- Dominant dystrophic epidermolysis bullosa of Pasini
- Autosomal recessive dystrophic epidermolysis bullosa generalisata gravis
- Generalised dystrophic epidermolysis bullosa
- Generalized DDEB (generalized dystrophic epidermolysis bullosa)
- Bullosa Dystrophica, Epidermolysis
- Dystrophic epidermolysis bullosa inverse type
- Bullosa, Dystrophic Epidermolysis
- Albopapuloid dystrophic epidermolysis bullosa of Pasini
- Autosomal dominant generalised dystrophic epidermolysis bullosa
- Dominant dystrophic epidermolysis bullosa, albopapular type
- Goldscheider's disease
- Localised dystrophic epidermolysis bullosa
- RDEB-O - recessive dystrophic epidermolysis bullosa-generalized other
- Dystrophic epidermolysis bullosa (disorder)
- Dystrophic epidermolysis bullosa nails only
- Recessive dystrophic epidermolysis bullosa
- Generalized recessive non-mutilating dystrophic epidermolysis bullosa
- Epidermolysis bullosa dystrophica, Pasini type
- RDEB-O - recessive dystrophic epidermolysis bullosa-generalised other
- Centripetal recessive dystrophic epidermolysis bullosa
- Bullosa Dystrophicas, Epidermolysis
- epidermolysis bullosa dystrophic
- Polydysplastic epidermolysis bullosa
- Recessive dystrophic epidermolysis bullosa non-Hallopeau Siemens type
- Dystrophicas, Epidermolysis Bullosa
- Generalised recessive dystrophic epidermolysis bullosa mitis
- Hyperplastic epidermolysis bullosa
- Bullosas, Dystrophic Epidermolysis
- Goldscheider disease
- DDEB (dominant dystrophic epidermolysis bullosa) intermediate
- Dysplastic epidermolysis bullosa dystrophica
- Localised recessive dystrophic epidermolysis bullosa
- Severe generalised recessive dystrophic epidermolysis bullosa
- bullosa dystrophica epidermolysis
- Epidermolysis Bullosas, Dystrophic
- Centripetalis recessive dystrophic epidermolysis bullosa
- Dominant dystrophic epidermolysis bullosa
- Progressive recessive dystrophic epidermolysis bullosa
- Epidermolysis Bullosa Dystrophicas
- Epidermolysis bullosa dystrophica, Bart type
- DEB - Dystrophic epidermolysis bullosa
- Autosomal recessive dystrophic epidermolysis bullosa Hallopeau Siemens type
- Epidermolysis bullosa dystrophica dominans
- RDEB-Ce - recessive dystrophic epidermolysis bullosa centripetalis
- Dystrophic Epidermolysis Bullosas
- Cockayne Touraine epidermolysis bullosa
- Autosomal dominant generalized dystrophic epidermolysis bullosa
- EBR 3
- Localized recessive dystrophic epidermolysis bullosa
- Severe generalized recessive dystrophic epidermolysis bullosa
- Epidermolysis bullosa dystrophica neurotrophica
- Hyperplastic dystrophic epidermolysis bullosa
- Generalized recessive dystrophic epidermolysis bullosa mitis
- Dystrophica, Epidermolysis Bullosa
- Dystrophic epidermolysis bullosa generalisata mitis
- Generalised DDEB (generalised dystrophic epidermolysis bullosa)
- Acral DEB (dystrophic epidermolysis bullosa)
- Epidermolysis bullosa, Cockayne-Touraine type
Frequently Asked Questions
What is the ICD-10 code for epidermolysis bullosa dystrophica?
The ICD-10-CM code for epidermolysis bullosa dystrophica is Q81.2. The full clinical description is "Epidermolysis bullosa dystrophica". Q81.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q81.2 mean?
ICD-10-CM code Q81.2 represents “Epidermolysis bullosa dystrophica”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q81.2 a billable code?
Yes, Q81.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q81.2 in?
Q81.2 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q81.2 map to?
Q81.2 maps to 18 SNOMED CT concepts: 733638006, 75875004, 1231284001, 723716009, 725419003, and 13 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q81.2?
Q81.2 is linked to 1 UMLS Concept Unique Identifier: C0079294. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q81.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like epidermolysis bullosa dystrophica affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q81.2?
Q81.2 maps to the ICD-11 code: EC32 (Dystrophic epidermolysis bullosa).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.