Q81.0
BillableEpidermolysis bullosa simplex
Epidermolysis bullosa simplex
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(99)
SNOMED CT
- Pyloric atresia27729002
- Atresia of stomach28828001
- Atretogastria28828001
- Gastric atresia28828001
- Imperforate stomach28828001
- Epidermolysis bullosa simplex67144006
- Epidermolysis bullosa simplex, Kobner type90496008
- Generalised epidermolysis bullosa simplex90496008
- Generalized epidermolysis bullosa simplex90496008
- Kobner disease90496008
- Koebner epidermolysis bullosa90496008
- Epidermolysis bullosa simplex with hypodontia254177003
- Kallin's syndrome254177003
- Dowling-Meara epidermolysis bullosa254179000
- Epidermolysis bullosa simplex herpetiformis254179000
- Simplex epidermolysis bullosa herpetiformis254179000
- Epidermolysis bullosa simplex with mottled pigmentation254180002
- Simple epidermolysis bullosa with mottled pigmentation254180002
- Epidermolysis simplex superficialis254181003
- Lethal autosomal recessive epidermolysis bullosa simplex254183000
- Epidermolysis bullosa simplex of Ogna398071000
- Epidermolysis bullosa simplex, Ogna type398071000
- Autosomal dominant epidermolysis bullosa simplex398170002
- EBS 1398170002
- Keratoderma due to Dowling-Meara type epidermolysis bullosa simplex403792007
- Ectodermal dysplasia skin fragility syndrome716699004
- Epidermolysis bullosa simplex due to plakophilin deficiency716699004
- McGrath syndrome716699004
- Epidermolysis bullosa simplex with circinate migratory erythema716700003
- Epidermolysis bullosa simplex co-occurrent with pyloric atresia716701004
- Epidermolysis bullosa simplex with pyloric atresia716701004
- Basal epidermolysis bullosa simplex723163000
- Epidermolysis bullosa simplex with muscular dystrophy723308003
- Limb girdle muscular dystrophy with epidermolysis bullosa simplex723308003
- EBS-AR KRT14 - epidermolysis bullosa simplex autosomal recessive keratin 14724206005
- KRT14 related epidermolysis bullosa simplex724206005
- Keratin 14 related epidermolysis bullosa simplex724206005
- Suprabasal epidermolysis bullosa simplex724840004
- DST (dystonin) related epidermolysis bullosa simplex773501006
- Epidermolysis bullosa simplex due to BP230 deficiency773501006
- Epidermolysis bullosa simplex due to exophilin 5 deficiency773503009
- Autosomal recessive epidermolysis bullosa simplex1156849001
- Intermediate epidermolysis bullosa simplex with cardiomyopathy1177176009
- Lethal acantholytic epidermolysis bullosa1230026002
- Lethal acantholytic erosive disorder1230026002
UMLS
Clinical Terms
- Kallin's syndrome
- Epidermolysis bullosa simplex of Ogna
- Generalised epidermolysis bullosa simplex
- Limb girdle muscular dystrophy with epidermolysis bullosa simplex
- Imperforate stomach
- Intermediate epidermolysis bullosa simplex with cardiomyopathy
- Epidermolysis bullosa simplex with mottled pigmentation
- Lethal acantholytic erosive disorder
- DST (dystonin) related epidermolysis bullosa simplex
- Atresia of stomach
- Pyloric atresia
- Epidermolysis bullosa simplex due to plakophilin deficiency
- Epidermolysis bullosa simplex co-occurrent with pyloric atresia
- Simple epidermolysis bullosa with mottled pigmentation
- Epidermolysis bullosa simplex with hypodontia
- Suprabasal epidermolysis bullosa simplex
- Epidermolysis bullosa simplex due to BP230 deficiency
- McGrath syndrome
- Epidermolysis Bullosa Simplices
- Epidermolysis bullosa simplex with circinate migratory erythema
- EBS-AR KRT14 - epidermolysis bullosa simplex autosomal recessive keratin 14
- Epidermolysis bullosa simplex with pyloric atresia
- Atretogastria
- Epidermolysis bullosa simplex (disorder)
- Simplex epidermolysis bullosa herpetiformis
- Epidermolysis bullosa simplex due to exophilin 5 deficiency
- Generalized epidermolysis bullosa simplex
- Kobner disease
- Autosomal recessive epidermolysis bullosa simplex
- Koebner epidermolysis bullosa
- Epidermolysis simplex superficialis
- Gastric atresia
- Lethal acantholytic epidermolysis bullosa
- Epidermolysis bullosa simplex, Kobner type
- Lethal autosomal recessive epidermolysis bullosa simplex
- KRT14 related epidermolysis bullosa simplex
- Autosomal dominant epidermolysis bullosa simplex
- Ectodermal dysplasia skin fragility syndrome
- EBS
- Dowling-Meara epidermolysis bullosa
- Keratoderma due to Dowling-Meara type epidermolysis bullosa simplex
- Epidermolysis bullosa simplex herpetiformis
- Epidermolysis bullosa simplex with muscular dystrophy
- Keratin 14 related epidermolysis bullosa simplex
- EBS 1
- Epidermolysis bullosa simplex, Ogna type
- Bullosa Simplices, Epidermolysis
- Basal epidermolysis bullosa simplex
Frequently Asked Questions
What is the ICD-10 code for epidermolysis bullosa simplex?
The ICD-10-CM code for epidermolysis bullosa simplex is Q81.0. The full clinical description is "Epidermolysis bullosa simplex". Q81.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q81.0 mean?
ICD-10-CM code Q81.0 represents “Epidermolysis bullosa simplex”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q81.0 a billable code?
Yes, Q81.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q81.0 in?
Q81.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q81.0?
Q81.0 has Excludes1 notes indicating codes that cannot be used together with it, including: Cockayne's syndrome (Q87.19).
What SNOMED CT codes does Q81.0 map to?
Q81.0 maps to 24 SNOMED CT concepts: 28828001, 398170002, 1156849001, 723163000, 773501006, and 19 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q81.0?
Q81.0 is linked to 1 UMLS Concept Unique Identifier: C0079298. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q81.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like epidermolysis bullosa simplex affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q81.0?
Q81.0 maps to the ICD-11 code: EC30 (Epidermolysis bullosa simplex).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.