Q81.1
BillableEpidermolysis bullosa letalis
Epidermolysis bullosa letalis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Herlitz' syndrome
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(81)
SNOMED CT
- Generalised junctional epidermolysis bullosa254194001
- Generalized junctional epidermolysis bullosa254194001
- Epidermolysis bullosa letalis400140006
- Herlitz syndrome400140006
- Herlitz's disease400140006
- Junctional epidermolysis bullosa gravis of Herlitz400140006
- Junctional epidermolysis bullosa, lethal type, Herlitz400140006
UMLS
- Bullosa Letali, EpidermolysisC0079683
- Bullosa Letalis, EpidermolysisC0079683
- Bullosa, Herlitz-Pearson-Type EpidermolysisC0079683
- Disease, HerlitzC0079683
- Disease, Herlitz'sC0079683
- EPIDERMOLYSIS BULLOSA JUNCTIONALIS, HERLITZ TYPEC0079683
- EPIDERMOLYSIS BULLOSA LETALISC0079683
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL 1B, SEVEREC0079683
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL, GENERALIZED SEVEREC0079683
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL, HERLITZ TYPEC0079683
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL, HERLITZ-PEARSON TYPEC0079683
- Epidermolysis Bullosa Junctionalis, Herlitz TypeC0079683
- Epidermolysis Bullosa LetaliC0079683
- Epidermolysis Bullosa LetalisC0079683
- Epidermolysis Bullosa, Herlitz-Pearson-TypeC0079683
- Epidermolysis Bullosa, Junctional, Herlitz TypeC0079683
- Epidermolysis Bullosa, Junctional, Herlitz-Pearson TypeC0079683
- Epidermolysis bullosa hereditaria letalisC0079683
- Epidermolysis bullosa letalisC0079683
- Epidermolysis bullosa, junctional Herlitz-Pearson typeC0079683
- HERLITZ DISC0079683
- HERLITZ-PEARSON-TYPE EPIDERMOLYSIS BULLOSAC0079683
- HERLITZS DISC0079683
- Herlitz DiseaseC0079683
- Herlitz Pearson Type Epidermolysis BullosaC0079683
- Herlitz syndromeC0079683
- Herlitz' syndromeC0079683
- Herlitz's DiseaseC0079683
- Herlitz's diseaseC0079683
- Herlitz-Pearson Type Epidermolysis BullosaC0079683
- Herlitz-Pearson-Type Epidermolysis BullosaC0079683
- Herlitzs DiseaseC0079683
- JEB-HERLITZ TYPEC0079683
- JEB1BC0079683
- Junctional epidermolysis bullosa gravis of HerlitzC0079683
- Junctional epidermolysis bullosa gravis of Herlitz (disorder)C0079683
- Junctional epidermolysis bullosa, lethal type, HerlitzC0079683
- Letali, Epidermolysis BullosaC0079683
- Letalis, Epidermolysis BullosaC0079683
- Lethal Junctional Epidermolysis BullosaC0079683
Clinical Terms
- Epidermolysis Bullosa Letali
- HERLITZ DIS
- HERLITZ-PEARSON-TYPE EPIDERMOLYSIS BULLOSA
- Generalised junctional epidermolysis bullosa
- Disease, Herlitz's
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL, HERLITZ TYPE
- Epidermolysis bullosa hereditaria letalis
- JEB-HERLITZ TYPE
- Epidermolysis Bullosa, Junctional, Herlitz-Pearson Type
- Junctional epidermolysis bullosa gravis of Herlitz
- Letalis, Epidermolysis Bullosa
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL 1B, SEVERE
- Herlitz's disease
- Letali, Epidermolysis Bullosa
- Epidermolysis bullosa, junctional Herlitz-Pearson type
- HERLITZS DIS
- Herlitz syndrome
- Disease, Herlitz
- Junctional epidermolysis bullosa, lethal type, Herlitz
- Generalized junctional epidermolysis bullosa
- Herlitzs Disease
- Bullosa, Herlitz-Pearson-Type Epidermolysis
- Herlitz Disease
- Junctional epidermolysis bullosa gravis of Herlitz (disorder)
- Herlitz Pearson Type Epidermolysis Bullosa
- Herlitz' syndrome
- Bullosa Letali, Epidermolysis
- Bullosa Letalis, Epidermolysis
- Epidermolysis Bullosa, Herlitz-Pearson-Type
- Epidermolysis Bullosa Junctionalis, Herlitz Type
- JEB1B
- Lethal Junctional Epidermolysis Bullosa
- EPIDERMOLYSIS BULLOSA, JUNCTIONAL, GENERALIZED SEVERE
- Herlitz-Pearson Type Epidermolysis Bullosa
Frequently Asked Questions
What is the ICD-10 code for epidermolysis bullosa letalis?
The ICD-10-CM code for epidermolysis bullosa letalis is Q81.1. The full clinical description is "Epidermolysis bullosa letalis". Q81.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q81.1 mean?
ICD-10-CM code Q81.1 represents “Epidermolysis bullosa letalis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q81.1 a billable code?
Yes, Q81.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q81.1 in?
Q81.1 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q81.1 map to?
Q81.1 maps to 2 SNOMED CT concepts: 400140006, 254194001. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q81.1?
Q81.1 is linked to 1 UMLS Concept Unique Identifier: C0079683. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q81.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like epidermolysis bullosa letalis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q81.1?
Q81.1 maps to the ICD-11 code: EC31 (Junctional epidermolysis bullosa).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.