AutoICD API

Q80.8

Billable

Other congenital ichthyosis

Other congenital ichthyosis

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(6)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(145)

SNOMED CT

Clinical Terms

  • ICE (ichthyosis cheek eyebrow) syndrome
  • Autosomal recessive exfoliative ichthyosis
  • Ichthyosiform erythroderma with leukocyte vacuolation
  • Cutaneous syndrome with ichthyosis
  • Ichthyotic neutral lipid storage disease
  • KLICK syndrome
  • Keratitis, ichthyosis, deafness/hystrix-like ichthyosis deafness syndrome
  • IFAP - ichthyosis follicularis with alopecia and photophobia
  • Xeroderma in genetic syndrome
  • Ichthyosis hystrix
  • CHIME syndrome
  • Follicular ichthyosis
  • Exfoliative ichthyosis
  • Ichthyosis exfoliativa
  • Congenital bullous ichthyosiform erythroderma
  • Keratitis ichthyosis and deafness syndrome
  • Lipid storage myopathy AND congenital ichthyosis
  • Hyper-IgE syndrome
  • Keratosis linearis, ichthyosis congenita, sclerosing keratoderma syndrome
  • Sidransky Feinstein Goodman syndrome
  • BIE - Bullous ichthyosiform erythroderma
  • Trichorrhexis invaginata
  • Autosomal recessive keratitis-ichthyosis-deafness syndrome
  • Neuroectodermal dysplasia CHIME type
  • Hereditary skin fragility
  • Ichthyosis follicularis with alopecia and photophobia (IFAP)
  • Ichthyosis hystrix gravior
  • Trichodysplasia xeroderma syndrome
  • Triglyceride storage disease with ichthyosis
  • Zunich Kaye syndrome
  • Bullous ichthyosis
  • Autosomal recessive epidermolytic ichthyosis
  • KID/HID syndrome
  • Atypical ichthyosis vulgaris with hypogonadism
  • Dominant ichthyosis vulgaris
  • Ichthyosis hystrix Bäfverstedt type
  • KIDS - Keratitis ichthyosis and deafness syndrome
  • Netherton's syndrome
  • Trichorrhexis
  • Genetically determined skin fragility
  • Chanarin-Miranda syndrome
  • Congenital ichthyosis type 4
  • Ichthyosiform erythroderma with leucocyte vacuolation
  • Ichthyosis hystrix Rheydt type
  • CHIME (coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability, ear anomaly) syndrome
  • Ichthyosis linearis circumflexa
  • Autosomal recessive KID (keratitis, ichthyosis, deafness) syndrome
  • Ichthyosis vulgaris
  • KID syndrome
  • Keratinopathic ichthyosis
  • Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome
  • Neutral lipid storage disease
  • Ichthyosis hystrix of Curth-Macklin
  • Chanarin-Dorfman disease
  • Autosomal dominant ichthyosis
  • Bamboo hair
  • Trichoclasis
  • Annular epidermolytic ichthyosis
  • HIES - hyperimmunoglobulin E syndrome
  • Ichthyosis Lambert type
  • Hyperimmunoglobulin E syndrome
  • Autosomal recessive ichthyosis
  • Epidermolytic hyperkeratosis
  • Bullous ichthyosiform erythroderma
  • Netherton syndrome
  • Ichthyosis follicularis with alopecia and photophobia
  • Axial osteosclerosis with bamboo hair
  • Keratitis ichthyosis deafness syndrome
  • Maleformatio ectodermalis generalisata of Bafverstedt
  • Ichthyosis prematurity syndrome
  • Comel-Netherton syndrome
  • Ichthyosis cheek eyebrow syndrome
Frequently Asked Questions
What is the ICD-10 code for other congenital ichthyosis?

The ICD-10-CM code for other congenital ichthyosis is Q80.8. The full clinical description is "Other congenital ichthyosis". Q80.8 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q80.8 mean?

ICD-10-CM code Q80.8 represents “Other congenital ichthyosis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q80.8 a billable code?

Yes, Q80.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q80.8 in?

Q80.8 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q80.8?

Q80.8 has Excludes1 notes indicating codes that cannot be used together with it, including: Refsum's disease (G60.1).

What SNOMED CT codes does Q80.8 map to?

Q80.8 maps to 31 SNOMED CT concepts: 718631006, 239060009, 402770002, 403780007, 890235002, and 26 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q80.8?

Q80.8 is linked to 1 UMLS Concept Unique Identifier: C0478084. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q80.8 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital ichthyosis affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q80.8?

Q80.8 maps to the ICD-11 code: EC20.Y (Other specified genetic disorders of keratinisation).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.