Q80.1
BillableX-linked ichthyosis
X-linked ichthyosis
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(61)
SNOMED CT
- Arylsulfatase C deficiency3642008
- Arylsulphatase C deficiency3642008
- Deficiency of steryl-sulfatase3642008
- Deficiency of steryl-sulphatase3642008
- Disorder involving deficiency of steryl-sulfatase (EC 3.1.6.2)3642008
- Steryl-sulfate sulfohydrolase deficiency3642008
- Steryl-sulphate sulphohydrolase deficiency3642008
- Sex-linked ichthyosis72523005
- X-linked ichthyosis72523005
- X-linked ichthyosis with steryl-sulfatase deficiency72523005
- X-linked ichthyosis with steryl-sulphatase deficiency72523005
- Autosomal dominant ichthyosis402770002
- Syndromic X-linked ichthyosis717041008
- Syndromic recessive X-linked ichthyosis717041008
UMLS
- ICHTHYOSIS, X-LINKEDC0079588
- Ichthyoses, Sex-LinkedC0079588
- Ichthyoses, X-LinkedC0079588
- Ichthyosis, Sex LinkedC0079588
- Ichthyosis, Sex-LinkedC0079588
- Ichthyosis, X LinkedC0079588
- Ichthyosis, X-LinkedC0079588
- Ichthyosis, X-linkedC0079588
- Sex-linked ichthyosisC0079588
- X-Linked IchthyosisC0079588
- X-linked ichthyosisC0079588
- X-linked ichthyosis (STS, SSDD)C0079588
- X-linked ichthyosis with steryl-sulfatase deficiencyC0079588
- X-linked ichthyosis with steryl-sulfatase deficiency (disorder)C0079588
- X-linked ichthyosis with steryl-sulphatase deficiencyC0079588
- XLIC0079588
- ssddC0079588
- stsC0079588
- x linked ichthyosisC0079588
- x-linked ichthyosisC0079588
- x-linked recessive ichthyosisC0079588
Clinical Terms
- x-linked recessive ichthyosis
- X-linked ichthyosis with steryl-sulfatase deficiency
- sts
- Ichthyosis, X-Linked
- Syndromic X-linked ichthyosis
- Steryl-sulphate sulphohydrolase deficiency
- Arylsulphatase C deficiency
- Ichthyoses, Sex-Linked
- Ichthyosis, Sex-Linked
- Deficiency of steryl-sulfatase
- Syndromic recessive X-linked ichthyosis
- Disorder involving deficiency of steryl-sulfatase (EC 3.1.6.2)
- Ichthyoses, X-Linked
- X-linked ichthyosis with steryl-sulfatase deficiency (disorder)
- X-linked ichthyosis (STS, SSDD)
- ssdd
- Ichthyosis, Sex Linked
- XLI
- Autosomal dominant ichthyosis
- Ichthyosis, X Linked
- X-linked ichthyosis with steryl-sulphatase deficiency
- Sex-linked ichthyosis
- Deficiency of steryl-sulphatase
- Steryl-sulfate sulfohydrolase deficiency
- x linked ichthyosis
- Arylsulfatase C deficiency
Frequently Asked Questions
What is the ICD-10 code for x-linked ichthyosis?
The ICD-10-CM code for x-linked ichthyosis is Q80.1. The full clinical description is "X-linked ichthyosis". Q80.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q80.1 mean?
ICD-10-CM code Q80.1 represents “X-linked ichthyosis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q80.1 a billable code?
Yes, Q80.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q80.1 in?
Q80.1 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q80.1?
Q80.1 has Excludes1 notes indicating codes that cannot be used together with it, including: Refsum's disease (G60.1).
What SNOMED CT codes does Q80.1 map to?
Q80.1 maps to 4 SNOMED CT concepts: 3642008, 402770002, 72523005, 717041008. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q80.1?
Q80.1 is linked to 1 UMLS Concept Unique Identifier: C0079588. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q80.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like x-linked ichthyosis affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q80.1?
Q80.1 maps to the ICD-11 code: EC20.01 (X-linked ichthyosis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.