Q80.3
BillableCongenital bullous ichthyosiform erythroderma
Congenital bullous ichthyosiform erythroderma
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(122)
SNOMED CT
- Dwarfism-ichthyosiform erythroderma-mental deficiency syndrome2355008
- Rud syndrome2355008
- Rud's syndrome2355008
- Alligator skin254156001
- Congenital ichthyosiform erythroderma254156001
- BIE - Bullous ichthyosiform erythroderma254167000
- Bullous ichthyosiform erythroderma254167000
- Bullous ichthyosis254167000
- Congenital bullous ichthyosiform erythroderma254167000
- Dominant ichthyosis vulgaris254167000
- Epidermolytic hyperkeratosis254167000
- Localised bullous ichthyosiform erythroderma254168005
- Localized bullous ichthyosiform erythroderma254168005
- Ichthyosis bullosa of Siemens254169002
- Congenital non bullous ichthyosiform erythroderma267372009
- Ichthyosiform dermatosis268282005
- Ichthyosiform erythroderma268282005
- Autosomal dominant ichthyosis402770002
- CRIE - Congenital reticular ichthyosiform erythroderma703504006
- Congenital reticular ichthyosiform erythroderma703504006
- Ichthyosis variegata703504006
- Ichthyosis with confetti703504006
- Genetically determined skin fragility724851004
- Hereditary skin fragility724851004
UMLS
- BCIEC0079153
- BIEC0079153
- BIE - Bullous ichthyosiform erythrodermaC0079153
- BULLOUS CONGEN ICHTHYOSIFORM ERYTHRODERMAC0079153
- BULLOUS CONGENITAL ICHTHYOSIFORM ERYTHRODERMAC0079153
- BULLOUS ERYTHRODERMA ICHTHYOSIFORMIS CONGENITA OF BROCQC0079153
- BULLOUS ICHTHYOSIFORM ERYTHRODERMAC0079153
- Bullous Congenital Ichthyosiform ErythrodermaC0079153
- Bullous Erythroderma IchthyosiformeC0079153
- Bullous Erythroderma IchthyosiformesC0079153
- Bullous Erythroderma Ichthyosiformis Congenita of BrocqC0079153
- Bullous Ichthyosiform ErythrodermaC0079153
- Bullous Ichthyosiform Erythroderma CongenitalC0079153
- Bullous Ichthyosiform ErythrodermasC0079153
- Bullous congenital ichthyosiform erythrodermaC0079153
- Bullous erythroderma ichthyosiformeC0079153
- Bullous erythroderma ichthyosiformis congenita of BrocqC0079153
- Bullous ichthyosiform erythrodermaC0079153
- Bullous ichthyosiform erythroderma (disorder)C0079153
- Bullous ichthyosisC0079153
- CONGEN BULLOUS ICHTHYOSIFORM ERYTHRODERMAC0079153
- Congenital Bullous Ichthyosiform ErythrodermaC0079153
- Congenital Ichthyosiform Erythroderma, BullousC0079153
- Congenital bullous ichthyosiform erythrodermaC0079153
- Dominant ichthyosis vulgarisC0079153
- EHKC0079153
- EPIDERMOLYTIC ICHTHYOSISC0079153
- Epidermolytic HyperkeratosesC0079153
- Epidermolytic HyperkeratosisC0079153
- Epidermolytic IchthyosisC0079153
- Epidermolytic hyperkeratosisC0079153
- Epidermolytic ichthyosisC0079153
- Epidermolytic palmoplantar hyperkeratosisC0079153
- Erythroderma Ichthyosiforme, BullousC0079153
- Erythroderma Ichthyosiformes, BullousC0079153
- Erythroderma, Bullous IchthyosiformC0079153
- Erythrodermas, Bullous IchthyosiformC0079153
- Hyperkeratoses, EpidermolyticC0079153
- Hyperkeratosis, EpidermolyticC0079153
- Hyperkeratosis, epidermolyticC0079153
- ICHTHYOSIFORM ERYTHRODERMA BULLOUS CONGENC0079153
- Ichthyosiform Erythroderma, BullousC0079153
- Ichthyosiform Erythroderma, Bullous CongenitalC0079153
- Ichthyosiform Erythrodermas, BullousC0079153
- Ichthyosiforme, Bullous ErythrodermaC0079153
- Ichthyosiformes, Bullous ErythrodermaC0079153
- epidermolytic hyperkeratosisC0079153
Clinical Terms
- Rud's syndrome
- Bullous Erythroderma Ichthyosiformis Congenita of Brocq
- BULLOUS CONGENITAL ICHTHYOSIFORM ERYTHRODERMA
- ICHTHYOSIFORM ERYTHRODERMA BULLOUS CONGEN
- Ichthyosiforme, Bullous Erythroderma
- EPIDERMOLYTIC ICHTHYOSIS
- Localised bullous ichthyosiform erythroderma
- BIE
- Bullous Erythroderma Ichthyosiforme
- CONGEN BULLOUS ICHTHYOSIFORM ERYTHRODERMA
- Ichthyosiform Erythrodermas, Bullous
- BIE - Bullous ichthyosiform erythroderma
- Erythrodermas, Bullous Ichthyosiform
- epidermolytic hyperkeratosis
- Ichthyosis variegata
- CRIE - Congenital reticular ichthyosiform erythroderma
- Hereditary skin fragility
- Hyperkeratosis, epidermolytic
- Ichthyosiformes, Bullous Erythroderma
- Congenital reticular ichthyosiform erythroderma
- Bullous ichthyosis
- EHK
- Bullous Ichthyosiform Erythrodermas
- Congenital non bullous ichthyosiform erythroderma
- Dominant ichthyosis vulgaris
- Localized bullous ichthyosiform erythroderma
- Epidermolytic Hyperkeratoses
- Ichthyosis bullosa of Siemens
- Rud syndrome
- Epidermolytic palmoplantar hyperkeratosis
- Genetically determined skin fragility
- Erythroderma Ichthyosiforme, Bullous
- Erythroderma Ichthyosiformes, Bullous
- Hyperkeratoses, Epidermolytic
- BULLOUS ICHTHYOSIFORM ERYTHRODERMA
- Alligator skin
- Autosomal dominant ichthyosis
- Ichthyosiform erythroderma
- Bullous ichthyosiform erythroderma (disorder)
- Bullous Erythroderma Ichthyosiformes
- Dwarfism-ichthyosiform erythroderma-mental deficiency syndrome
- BULLOUS CONGEN ICHTHYOSIFORM ERYTHRODERMA
- Bullous Ichthyosiform Erythroderma Congenital
- Erythroderma, Bullous Ichthyosiform
- Ichthyosiform dermatosis
- Congenital Ichthyosiform Erythroderma, Bullous
- Ichthyosiform Erythroderma, Bullous Congenital
- Ichthyosiform Erythroderma, Bullous
- BCIE
- Ichthyosis with confetti
- Congenital ichthyosiform erythroderma
Frequently Asked Questions
What is the ICD-10 code for congenital bullous ichthyosiform erythroderma?
The ICD-10-CM code for congenital bullous ichthyosiform erythroderma is Q80.3. The full clinical description is "Congenital bullous ichthyosiform erythroderma". Q80.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q80.3 mean?
ICD-10-CM code Q80.3 represents “Congenital bullous ichthyosiform erythroderma”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q80.3 a billable code?
Yes, Q80.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q80.3 in?
Q80.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q80.3?
Q80.3 has Excludes1 notes indicating codes that cannot be used together with it, including: Refsum's disease (G60.1).
What SNOMED CT codes does Q80.3 map to?
Q80.3 maps to 10 SNOMED CT concepts: 254156001, 402770002, 254167000, 703504006, 267372009, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q80.3?
Q80.3 is linked to 1 UMLS Concept Unique Identifier: C0079153. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q80.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital bullous ichthyosiform erythroderma affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q80.3?
Q80.3 maps to the ICD-11 code: EC20.03 (Keratinopathic ichthyoses).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.