AutoICD API

Q38.0

Billable

Congenital malformations of lips, not elsewhere classified

Congenital malformations of lips, not elsewhere classified

Status

Billable / Specific

Parent Code

Q38

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital fistula of lip
  • Congenital malformation of lip NOS
  • Van der Woude's syndrome

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
Q38.1

Ankyloglossia

BillableQ38.2

Macroglossia

BillableQ38.3

Other congenital malformations of tongue

BillableQ38.4

Congenital malformations of salivary glands and ducts

BillableQ38.5

Congenital malformations of palate, not elsewhere classified

BillableQ38.6

Other congenital malformations of mouth

BillableQ38.7

Congenital pharyngeal pouch

BillableQ38.8

Other congenital malformations of pharynx

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LA5ZStructural developmental anomalies of the face, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(156)

SNOMED CT

UMLS

Clinical Terms

  • Collodion baby
  • LIP-PIT SYNDROME
  • Congenital pits of lip
  • Lip pit syndrome
  • Congenital malformation of lip NOS
  • Observation of arrangement of lip
  • Congenital anomaly of lip (disorder)
  • Congenital hyperplasia of sebaceous glands of lip
  • Congenital commissural pits
  • Enlarged labial frenum
  • Syncheilia
  • Congenital lip pits
  • Wide frenum attachment
  • Commissural lip fistula
  • Congenital central ridge of philtrum
  • Prominent labial frenum
  • Benign seborrhoeic hyperplasia
  • Short philtrum
  • Congenital lip fistula
  • Abnormal labial frenal attachment
  • Enlarged labial fraenum
  • Prominent labial fraenum
  • Cleft lip and-or palate with mucous cysts of lower lip
  • Broad attachment of labial frenum
  • Lip-pit-cleft lip syndrome
  • Lip pits
  • LPS
  • CLEFT LIP AND/OR PALATE WITH MUCOUS CYSTS OF LOWER LIP
  • Finding of arrangement of lip
  • High smile line
  • Congenital midline sinus of philtrum
  • PIT
  • van der Woude syndrome
  • Congenital malformation of lips
  • Aberrant pull of labial frenulum
  • Labial pit
  • Congenital ectropion of lip
  • Commissural lip pits
  • Van der Woude's syndrome
  • Sebaceous hyperplasia
  • Broad attachment of labial fraenum
  • Synchilia
  • Congenital lower lip fistula
  • Congenital lower lip pits
  • Van der Woude syndrome (disorder)
  • Congenital midline ridge of philtrum
  • Congenital fistula of commissure of lips
  • Congenital fistula of lip
  • Sebaceous gland hyperplasia
  • VWS
  • Benign seborrheic hyperplasia
  • High upper lip line
  • Median nodule of upper lip
  • Congenital midline raphe of philtrum
  • Lamellar ichthyosis
  • Congenital midline sinus of upper lip
  • Abnormal labial fraenal attachment
  • Congenital anomaly of lip
  • Midline sinus of upper lip
  • VDWS
  • Congenital double lip
  • der syndrome van woudes
  • Developmental anomaly of lip
  • Calibre persistent labial artery
  • Jagell, Holmgren, Hofer syndrome
  • Caliber persistent labial artery
  • Fistula of lip
  • Double lip
  • Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome
  • Aberrant insertion of labial frenulum
  • Congenital fistula of lip (disorder)
Frequently Asked Questions
What is the ICD-10 code for congenital malformations of lips, not elsewhere classified?

The ICD-10-CM code for congenital malformations of lips, not elsewhere classified is Q38.0. The full clinical description is "Congenital malformations of lips, not elsewhere classified". Q38.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q38.0 mean?

ICD-10-CM code Q38.0 represents “Congenital malformations of lips, not elsewhere classified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q38.0 a billable code?

Yes, Q38.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q38.0 in?

Q38.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q38.0?

Q38.0 has Excludes1 notes indicating codes that cannot be used together with it, including: dentofacial anomalies (M26.-); macrostomia (Q18.4); microstomia (Q18.5); and 4 more.

What SNOMED CT codes does Q38.0 map to?

Q38.0 maps to 25 SNOMED CT concepts: 109551007, 235135002, 238748009, 698037004, 711100005, and 20 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q38.0?

Q38.0 is linked to 4 UMLS Concept Unique Identifiers: C0175697, C0431561, C0158670, C0495545. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q38.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformations of lips, not elsewhere classified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q38.0?

Q38.0 maps to the ICD-11 code: LA5Z (Structural developmental anomalies of the face, unspecified).

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try FreeView API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.