Q38.6
BillableOther congenital malformations of mouth
Other congenital malformations of mouth
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital malformation of mouth NOS
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q38.0Congenital malformations of lips, not elsewhere classified
Q38.1Ankyloglossia
Q38.2Macroglossia
Q38.3Other congenital malformations of tongue
Q38.4Congenital malformations of salivary glands and ducts
Q38.5Congenital malformations of palate, not elsewhere classified
Q38.7Congenital pharyngeal pouch
Q38.8Other congenital malformations of pharynx
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(185)
SNOMED CT
- Ectopic oral sebaceous glands50584008
- Ectopic sebaceous gland tissue50584008
- Ectopic sebaceous glands50584008
- Fordyce disease50584008
- Fordyce granules50584008
- Fordyce spots50584008
- Fordyce spots of mouth50584008
- Fordyce's disease50584008
- Fordyce's disease of mouth50584008
- Fordyce's granules50584008
- Gingival cyst58271001
- Gingival odontogenic cyst58271001
- Astomia91946007
- Congenital absence of mouth91946007
- Congenital anomaly of oral mucosa109434003
- Developmental anomaly of oral mucosa109434003
- Buccal bifurcation cyst109552000
- Ectopic oral gastrointestinal cyst109554004
- Heterotopic oral gastrointestinal cyst109554004
- Congenital anomaly of mouth128334002
- Congenital malformation of mouth128334002
- Cyst of oral soft tissue196546001
- Brachymesophalangia205317004
- Hyperpigmentation of oral mucosa235038002
- Melanin pigmentation of oral mucosa235038002
- Inflammatory odontogenic cyst235112000
- Congenital anomalies of tongue, mouth and pharynx253750008
- Congenital malformation of tongue, mouth and pharynx253750008
- Congenital abnormality of oral cavity282041002
- Congenital anomaly of oral cavity282041002
- Congenital malformation of oral cavity282041002
- Familial white folded mucosal dysplasia389203001
- Hereditary leukokeratosis of mucosa389203001
- Hereditary oral keratosis389203001
- Hereditary white sponge naevus389203001
- Hereditary white sponge nevus389203001
- White sponge naevus389203001
- White sponge naevus of mucosa389203001
- White sponge nevus389203001
- White sponge nevus of mucosa389203001
- Fordyce spots of lips403368002
- Fordyce spots of buccal mucosa403369005
- Hereditary mucoepithelial dysplasia403442005
- Hypertrichosis with congenital macrogingivae403532006
- CPLS - cleft palate-lateral synechia syndrome403772000
- Cleft palate lateral synechia syndrome403772000
- Syngnathia403772000
- Facial milia, lobate tongue, lingual and labial frenula syndrome403773005
- Gorlin-Psaume syndrome403773005
- Orofacial cleft449790007
- Fraenal attachment698842006
- Fraenal tag698842006
- Frenal attachment698842006
- Frenal tag698842006
- Cataract with aberrant oral frenula and growth delay syndrome715988005
- Wellesley Carman French syndrome715988005
- Oral-facial-digital syndrome Gabrielli type718681002
- Oral-facial-digital syndrome type 11718681002
- Oro-facial digital syndrome type 11718681002
- Orofaciodigital syndrome Gabrielli type718681002
- Orofaciodigital syndrome type 11718681002
- Oro-facial digital syndrome type 5722105002
- Orofaciodigital syndrome Thurston type722105002
- Orofaciodigital syndrome type 5722105002
- Thurston syndrome722105002
- Melanosis of mucosa of body orifice724847001
- Mucosal melanosis724847001
- Clayton-Smith Donnai syndrome732950006
- Ichthyosis, oral and digital anomalies syndrome732950006
- Microcephaly, cerebral malformation, orofaciodigital syndrome763837007
- Oro-facial digital syndrome type 14763837007
- Orofaciodigital syndrome type 14763837007
- Ectodermal dysplasia short stature syndrome764995008
- Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome764995008
- Short stature, nail dysplasia, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome764995008
- OFD18 - oral-facial-digital syndrome type 181177179002
- Oral-facial-digital syndrome with short stature and brachymesophalangia1177179002
- Orofaciodigital syndrome type 181177179002
UMLS
- ABNORM MOUTHC0026633
- Abnormal mouthC0026633
- Abnormalities, MouthC0026633
- Abnormality of the mouthC0026633
- Abnormality, MouthC0026633
- Congenital anomaly of mouthC0026633
- Congenital anomaly of mouth (disorder)C0026633
- Congenital malformation of mouthC0026633
- Congenital malformation of mouth NOSC0026633
- Congenital mouth malformation NOSC0026633
- Congenital oral malformationC0026633
- Congenital oral malformation NOSC0026633
- MOUTH ABNORMC0026633
- Mouth AbnormalitiesC0026633
- Mouth AbnormalityC0026633
- Other congenital malformations of mouthC0478026
Clinical Terms
- Fordyce disease
- Abnormalities, Mouth
- Congenital malformation of mouth NOS
- Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
- White sponge nevus
- Brachymesophalangia
- Congenital abnormality of oral cavity
- Inflammatory odontogenic cyst
- Congenital absence of mouth
- Congenital oral malformation
- White sponge naevus of mucosa
- Cyst of oral soft tissue
- Fordyce granules
- Melanosis of mucosa of body orifice
- Oral-facial-digital syndrome with short stature and brachymesophalangia
- Gingival cyst
- Oro-facial digital syndrome type 5
- Cataract with aberrant oral frenula and growth delay syndrome
- Fraenal attachment
- Fordyce's granules
- OFD18 - oral-facial-digital syndrome type 18
- Fordyce's disease
- Hypertrichosis with congenital macrogingivae
- Oro-facial digital syndrome type 14
- Hereditary white sponge naevus
- Familial white folded mucosal dysplasia
- MOUTH ABNORM
- Fordyce's disease of mouth
- Orofaciodigital syndrome type 11
- Abnormal mouth
- Gorlin-Psaume syndrome
- Abnormality of the mouth
- Buccal bifurcation cyst
- Congenital anomaly of mouth
- Ichthyosis, oral and digital anomalies syndrome
- Clayton-Smith Donnai syndrome
- Orofaciodigital syndrome type 14
- Heterotopic oral gastrointestinal cyst
- Hyperpigmentation of oral mucosa
- Fordyce spots of lips
- Hereditary white sponge nevus
- White sponge naevus
- Fordyce spots of mouth
- Hereditary oral keratosis
- Congenital malformation of tongue, mouth and pharynx
- Congenital anomaly of oral mucosa
- Orofaciodigital syndrome Thurston type
- Hereditary leukokeratosis of mucosa
- Orofacial cleft
- Syngnathia
- Ectopic oral gastrointestinal cyst
- Microcephaly, cerebral malformation, orofaciodigital syndrome
- Frenal attachment
- Congenital anomaly of oral cavity
- Facial milia, lobate tongue, lingual and labial frenula syndrome
- Cleft palate lateral synechia syndrome
- Ectopic oral sebaceous glands
- Ectopic sebaceous glands
- Congenital mouth malformation NOS
- Gingival odontogenic cyst
- Fordyce spots
- Developmental anomaly of oral mucosa
- ABNORM MOUTH
- Abnormality, Mouth
- Fordyce spots of buccal mucosa
- Congenital anomaly of mouth (disorder)
- Orofaciodigital syndrome Gabrielli type
- CPLS - cleft palate-lateral synechia syndrome
- Oro-facial digital syndrome type 11
- Fraenal tag
- Mouth Abnormalities
- Wellesley Carman French syndrome
- Astomia
- Congenital anomalies of tongue, mouth and pharynx
- Orofaciodigital syndrome type 18
- Thurston syndrome
- Short stature, nail dysplasia, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
- Mouth Abnormality
- Frenal tag
- Ectodermal dysplasia short stature syndrome
- Hereditary mucoepithelial dysplasia
- Congenital oral malformation NOS
- White sponge nevus of mucosa
- Mucosal melanosis
- Congenital malformation of mouth
- Congenital malformation of oral cavity
- Oral-facial-digital syndrome Gabrielli type
- Ectopic sebaceous gland tissue
- Melanin pigmentation of oral mucosa
- Oral-facial-digital syndrome type 11
- Orofaciodigital syndrome type 5
Frequently Asked Questions
What is the ICD-10 code for other congenital malformations of mouth?
The ICD-10-CM code for other congenital malformations of mouth is Q38.6. The full clinical description is "Other congenital malformations of mouth". Q38.6 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q38.6 mean?
ICD-10-CM code Q38.6 represents “Other congenital malformations of mouth”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q38.6 a billable code?
Yes, Q38.6 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q38.6 in?
Q38.6 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q38.6?
Q38.6 has Excludes1 notes indicating codes that cannot be used together with it, including: dentofacial anomalies (M26.-); macrostomia (Q18.4); microstomia (Q18.5).
What SNOMED CT codes does Q38.6 map to?
Q38.6 maps to 30 SNOMED CT concepts: 91946007, 205317004, 109552000, 403772000, 715988005, and 25 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q38.6?
Q38.6 is linked to 2 UMLS Concept Unique Identifiers: C0026633, C0478026. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q38.6 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital malformations of mouth affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q38.6?
Q38.6 maps to the ICD-11 code: LA31.Z (Structural developmental anomalies of mouth or tongue, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.