Q38.6

Billable

Other congenital malformations of mouth

Other congenital malformations of mouth

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital malformation of mouth NOS

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(185)

SNOMED CT

Clinical Terms

  • Fordyce disease
  • Abnormalities, Mouth
  • Congenital malformation of mouth NOS
  • Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
  • White sponge nevus
  • Brachymesophalangia
  • Congenital abnormality of oral cavity
  • Inflammatory odontogenic cyst
  • Congenital absence of mouth
  • Congenital oral malformation
  • White sponge naevus of mucosa
  • Cyst of oral soft tissue
  • Fordyce granules
  • Melanosis of mucosa of body orifice
  • Oral-facial-digital syndrome with short stature and brachymesophalangia
  • Gingival cyst
  • Oro-facial digital syndrome type 5
  • Cataract with aberrant oral frenula and growth delay syndrome
  • Fraenal attachment
  • Fordyce's granules
  • OFD18 - oral-facial-digital syndrome type 18
  • Fordyce's disease
  • Hypertrichosis with congenital macrogingivae
  • Oro-facial digital syndrome type 14
  • Hereditary white sponge naevus
  • Familial white folded mucosal dysplasia
  • MOUTH ABNORM
  • Fordyce's disease of mouth
  • Orofaciodigital syndrome type 11
  • Abnormal mouth
  • Gorlin-Psaume syndrome
  • Abnormality of the mouth
  • Buccal bifurcation cyst
  • Congenital anomaly of mouth
  • Ichthyosis, oral and digital anomalies syndrome
  • Clayton-Smith Donnai syndrome
  • Orofaciodigital syndrome type 14
  • Heterotopic oral gastrointestinal cyst
  • Hyperpigmentation of oral mucosa
  • Fordyce spots of lips
  • Hereditary white sponge nevus
  • White sponge naevus
  • Fordyce spots of mouth
  • Hereditary oral keratosis
  • Congenital malformation of tongue, mouth and pharynx
  • Congenital anomaly of oral mucosa
  • Orofaciodigital syndrome Thurston type
  • Hereditary leukokeratosis of mucosa
  • Orofacial cleft
  • Syngnathia
  • Ectopic oral gastrointestinal cyst
  • Microcephaly, cerebral malformation, orofaciodigital syndrome
  • Frenal attachment
  • Congenital anomaly of oral cavity
  • Facial milia, lobate tongue, lingual and labial frenula syndrome
  • Cleft palate lateral synechia syndrome
  • Ectopic oral sebaceous glands
  • Ectopic sebaceous glands
  • Congenital mouth malformation NOS
  • Gingival odontogenic cyst
  • Fordyce spots
  • Developmental anomaly of oral mucosa
  • ABNORM MOUTH
  • Abnormality, Mouth
  • Fordyce spots of buccal mucosa
  • Congenital anomaly of mouth (disorder)
  • Orofaciodigital syndrome Gabrielli type
  • CPLS - cleft palate-lateral synechia syndrome
  • Oro-facial digital syndrome type 11
  • Fraenal tag
  • Mouth Abnormalities
  • Wellesley Carman French syndrome
  • Astomia
  • Congenital anomalies of tongue, mouth and pharynx
  • Orofaciodigital syndrome type 18
  • Thurston syndrome
  • Short stature, nail dysplasia, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
  • Mouth Abnormality
  • Frenal tag
  • Ectodermal dysplasia short stature syndrome
  • Hereditary mucoepithelial dysplasia
  • Congenital oral malformation NOS
  • White sponge nevus of mucosa
  • Mucosal melanosis
  • Congenital malformation of mouth
  • Congenital malformation of oral cavity
  • Oral-facial-digital syndrome Gabrielli type
  • Ectopic sebaceous gland tissue
  • Melanin pigmentation of oral mucosa
  • Oral-facial-digital syndrome type 11
  • Orofaciodigital syndrome type 5
Frequently Asked Questions
What is the ICD-10 code for other congenital malformations of mouth?

The ICD-10-CM code for other congenital malformations of mouth is Q38.6. The full clinical description is "Other congenital malformations of mouth". Q38.6 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q38.6 mean?

ICD-10-CM code Q38.6 represents “Other congenital malformations of mouth”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q38.6 a billable code?

Yes, Q38.6 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q38.6 in?

Q38.6 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q38.6?

Q38.6 has Excludes1 notes indicating codes that cannot be used together with it, including: dentofacial anomalies (M26.-); macrostomia (Q18.4); microstomia (Q18.5).

What SNOMED CT codes does Q38.6 map to?

Q38.6 maps to 30 SNOMED CT concepts: 91946007, 205317004, 109552000, 403772000, 715988005, and 25 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q38.6?

Q38.6 is linked to 2 UMLS Concept Unique Identifiers: C0026633, C0478026. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q38.6 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital malformations of mouth affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q38.6?

Q38.6 maps to the ICD-11 code: LA31.Z (Structural developmental anomalies of mouth or tongue, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.