Q18.4
BillableMacrostomia
Macrostomia
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •inborn errors of metabolismE70-E88
- •cleft lip and cleft palateQ35-Q37
- •congenital malformation of cervical spine, , ,Q05.0, Q05.5, Q67.5, Q76.0-Q76.4
- •congenital malformation of larynxQ31
- •congenital malformation of lip NECQ38.0
- •congenital malformation of noseQ30
- •congenital malformation of parathyroid glandQ89.2
- •congenital malformation of thyroid glandQ89.2
Related Codes(9)
Q18.0Sinus, fistula and cyst of branchial cleft
Q18.1Preauricular sinus and cyst
Q18.2Other branchial cleft malformations
Q18.3Webbing of neck
Q18.5Microstomia
Q18.6Macrocheilia
Q18.7Microcheilia
Q18.8Other specified congenital malformations of face and neck
Q18.9Congenital malformation of face and neck, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(60)
SNOMED CT
- Ablepharia13401001
- Ablepharon13401001
- Ablepharon - absent eyelids13401001
- Open eye13401001
- Eyes wide apart22006008
- Eyes widely set22006008
- Hypertelorism22006008
- Orbital hypertelorism22006008
- Orbital separation excessive22006008
- Congenital macrostomia40159009
- Macrostomia40159009
- Bilateral congenital macrostomia49813000
- Bilateral macrostomia49813000
- Sphenoidal dysostosis109414004
- Mass of preauricular region447868007
- Ablepharon macrostomia syndrome718575002
- Macrostomia, preauricular tag, external ophthalmoplegia syndrome723366001
- Congenital left sided macrostomia767031008
- Congenital macrostomia of left side of mouth767031008
- Congenital macrostomia of right side of mouth767032001
- Congenital right sided macrostomia767032001
- Macroblepharon, ectropion, hypertelorism, macrostomia syndrome773557002
- Mandibulofacial dysostosis, macroblepharon, macrostomia syndrome773557002
UMLS
Clinical Terms
- Eyes wide apart
- Macroblepharon, ectropion, hypertelorism, macrostomia syndrome
- Ablepharon
- Congenital left sided macrostomia
- Large oral aperture
- Mandibulofacial dysostosis, macroblepharon, macrostomia syndrome
- Bilateral macrostomia
- Congenital macrostomia
- Sphenoidal dysostosis
- Orbital separation excessive
- Ablepharon macrostomia syndrome
- Hypertelorism
- Ablepharon - absent eyelids
- Open eye
- Mass of preauricular region
- Congenital macrostomia (disorder)
- Wide mouth
- Macrostomia, preauricular tag, external ophthalmoplegia syndrome
- Bilateral congenital macrostomia
- Macrostomias
- Ablepharia
- Congenital right sided macrostomia
- Congenital macrostomia of left side of mouth
- Large mouth
- Orbital hypertelorism
- Broad mouth
- Congenital macrostomia of right side of mouth
- Eyes widely set
Frequently Asked Questions
What is the ICD-10 code for macrostomia?
The ICD-10-CM code for macrostomia is Q18.4. The full clinical description is "Macrostomia". Q18.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q18.4 mean?
ICD-10-CM code Q18.4 represents “Macrostomia”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q18.4 a billable code?
Yes, Q18.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q18.4 in?
Q18.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q18.4?
Q18.4 has Excludes1 notes indicating codes that cannot be used together with it, including: cleft lip and cleft palate (Q35-Q37); conditions classified to Q67.0-Q67.4; congenital malformations of skull and face bones (Q75.-); and 4 more.
What SNOMED CT codes does Q18.4 map to?
Q18.4 maps to 11 SNOMED CT concepts: 13401001, 718575002, 49813000, 767031008, 40159009, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q18.4?
Q18.4 is linked to 1 UMLS Concept Unique Identifier: C0024433. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q18.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like macrostomia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q18.4?
Q18.4 maps to the ICD-11 code: LA31.3 (Macrostomia).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.