K74.3
BillablePrimary biliary cirrhosis
Primary biliary cirrhosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Chronic nonsuppurative destructive cholangitis
- Primary biliary cholangitis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •hemochromatosisE83.11
- •Reye's syndromeG93.7
- •viral hepatitisB15-B19
- •Wilson's diseaseE83.01
- •primary sclerosing cholangitisK83.01
Code Also
A second code may be required; sequencing depends on circumstances
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(91)
SNOMED CT
- Biliary cirrhosis1761006
- Cholangitic cirrhosis1761006
- Cholestatic cirrhosis1761006
- Chronic nonsuppurative destructive cholangitis1761006
- Hanot's cirrhosis31712002
- Primary biliary cholangitis31712002
- Primary biliary cirrhosis31712002
- Cholangiolitis35571009
- Biliary duct fibrosis48124008
- Biliary sclerosis48124008
- Fibrosis of bile duct48124008
- Florid cirrhosis76301009
- Cholangiolitic cirrhosis123606000
- Autoimmune liver disease235890007
- Acrosclerosis298285004
- Limited cutaneous systemic sclerosis298285004
- Systemic sclerosis with limited cutaneous involvement298285004
- Limited scleroderma299276009
- Limited systemic sclerosis299276009
- Systemic sclerosis, limited299276009
- Cholangiohepatitis370489002
- Autoimmune hepatitis408335007
- PSS - Progressive systemic sclerosis444133002
- Progressive systemic sclerosis444133002
- Autoimmune cholangitis713654004
- Primary biliary cirrhosis co-occurrent with systemic scleroderma715401008
- Reynolds syndrome715401008
UMLS
- Biliary Cholangitides, PrimaryC0008312
- Biliary Cholangitis, PrimaryC0008312
- Biliary Cirrhosis, PrimaryC0008312
- Biliary cirrhosis primaryC0008312
- Cholangitides, Primary BiliaryC0008312
- Cholangitis, Chronic Nonsuppurative DestructiveC0008312
- Cholangitis, Primary BiliaryC0008312
- Chronic Non-Suppurative Destructive CholangitisC0008312
- Chronic non-suppurative destructive cholangitisC0008312
- Chronic nonsuppurative destructive cholangitisC0008312
- Hanot's cirrhosisC0008312
- PBCC0008312
- Primary Biliary CholangitidesC0008312
- Primary Biliary CholangitisC0008312
- Primary Biliary CirrhosisC0008312
- Primary Biliary Cirrhosis (PBC)C0008312
- Primary biliary cholangitisC0008312
- Primary biliary cholangitis (disorder)C0008312
- Primary biliary cirrhosisC0008312
- biliary cirrhosis pbc primaryC0008312
- biliary cirrhosis primaryC0008312
- cirrhosis primary biliaryC0008312
- pbcC0008312
- primary biliary cirrhosisC0008312
Clinical Terms
- PSS - Progressive systemic sclerosis
- Cholangiolitis
- Chronic nonsuppurative destructive cholangitis
- cirrhosis primary biliary
- Biliary duct fibrosis
- Primary Biliary Cholangitis
- Biliary Cholangitides, Primary
- Chronic Non-Suppurative Destructive Cholangitis
- Biliary cirrhosis
- Primary Biliary Cholangitides
- biliary cirrhosis primary
- Systemic sclerosis with limited cutaneous involvement
- Fibrosis of bile duct
- Progressive systemic sclerosis
- Cholangitides, Primary Biliary
- Limited cutaneous systemic sclerosis
- Biliary Cholangitis, Primary
- Cholangiohepatitis
- Biliary sclerosis
- Limited systemic sclerosis
- Reynolds syndrome
- Primary biliary cholangitis (disorder)
- pbc
- Autoimmune liver disease
- Cholangitis, Primary Biliary
- Systemic sclerosis, limited
- Autoimmune hepatitis
- Hanot's cirrhosis
- Cholangitic cirrhosis
- Acrosclerosis
- Autoimmune cholangitis
- Biliary Cirrhosis, Primary
- Cholangiolitic cirrhosis
- Limited scleroderma
- Primary biliary cirrhosis co-occurrent with systemic scleroderma
- Cholestatic cirrhosis
- Primary Biliary Cirrhosis (PBC)
- biliary cirrhosis pbc primary
- Florid cirrhosis
- Cholangitis, Chronic Nonsuppurative Destructive
Frequently Asked Questions
What is the ICD-10 code for primary biliary cirrhosis?
The ICD-10-CM code for primary biliary cirrhosis is K74.3. The full clinical description is "Primary biliary cirrhosis". K74.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code K74.3 mean?
ICD-10-CM code K74.3 represents “Primary biliary cirrhosis”. It is classified under Chapter 11: Diseases of the Digestive System and is a billable/specific code that can be used on a claim.
Is K74.3 a billable code?
Yes, K74.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is K74.3 in?
K74.3 is in Chapter 11: Diseases of the Digestive System (codes K00-K95).
What codes cannot be used with K74.3?
K74.3 has Excludes1 notes indicating codes that cannot be used together with it, including: jaundice NOS (R17); alcoholic cirrhosis (of liver) (K70.3); alcoholic fibrosis of liver (K70.2); and 4 more.
What SNOMED CT codes does K74.3 map to?
K74.3 maps to 14 SNOMED CT concepts: 298285004, 713654004, 408335007, 235890007, 1761006, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for K74.3?
K74.3 is linked to 1 UMLS Concept Unique Identifier: C0008312. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does K74.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like primary biliary cirrhosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of K74.3?
K74.3 maps to the ICD-11 code: DB96.1Z (Primary biliary cholangitis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.