E83.01
BillableWilson's disease
Wilson's disease
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •dietary mineral deficiencyE58-E61
- •parathyroid disordersE20-E21
- •vitamin D deficiencyE55
Code Also
A second code may be required; sequencing depends on circumstances
Related Codes(2)
Also Known As / Clinical Terms(193)
SNOMED CT
- Copper metabolism disorder79886009
- Disorder of copper metabolism79886009
- Copper storage disease88518009
- Hepatocerebral degeneration88518009
- Hepatolenticular degeneration88518009
- Hepatolenticular degeneration syndrome88518009
- Kinnier-Wilson disease88518009
- Neurohepatic degeneration88518009
- Progressive lenticular degeneration88518009
- WD - Wilson's disease88518009
- Wilson disease88518009
- Wilson's disease88518009
- Pseudosclerotic type of Wilson's disease190823004
- Westphal-Strumpell cerebral pseudosclerosis190823004
- Westphal-Strumpell form of Wilson's disease190823004
- Westphal-Strumpell syndrome190823004
- Chorea due to heredodegenerative disorder722966004
- Dementia due to metabolic abnormality722979008
- Chorea co-occurrent and due to Wilson disease724766009
- Chorea with Wilson disease724766009
- Disorder of liver due to disorder of mineral metabolism737204007
- Hypoparathyroidism due to Wilson disease1186797002
- Dementia due to genetic disease1259476008
- Dementia due to Wilson disease1259511006
- Dementia due to Wilson's disease1259511006
- Dementia due to hepatolenticular degeneration1259511006
- Chorea due to metabolic disorder1259619002
- Dystonia due to Wilson disease1263524000
UMLS
- Cerebral PseudosclerosesC0019202
- Cerebral PseudosclerosisC0019202
- Copper Storage DiseaseC0019202
- Copper Storage DiseasesC0019202
- Copper storage diseaseC0019202
- Degeneration Syndrome, HepatolenticularC0019202
- Degeneration Syndromes, HepatolenticularC0019202
- Degeneration, HepatocerebralC0019202
- Degeneration, HepatolenticularC0019202
- Degeneration, NeurohepaticC0019202
- Degeneration, Progressive LenticularC0019202
- Degenerations, HepatocerebralC0019202
- Degenerations, NeurohepaticC0019202
- Disease, Copper StorageC0019202
- Diseases, Copper StorageC0019202
- Diseases, Hepato-Neurologic WilsonC0019202
- Diseases, Kinnier-WilsonC0019202
- Gowers' choreaC0019202
- HEPATOLENTICULAR DEGENERATIONC0019202
- HEPATONEUROLOGIC WILSON DISC0019202
- Hepato Neurologic Wilson DiseaseC0019202
- Hepato-Neurologic Wilson DiseaseC0019202
- Hepato-Neurologic Wilson DiseasesC0019202
- Hepato-lenticular degenerationC0019202
- Hepatocerebral DegenerationC0019202
- Hepatocerebral DegenerationsC0019202
- Hepatocerebral degenerationC0019202
- Hepatolenticular DegenerationC0019202
- Hepatolenticular Degeneration SyndromeC0019202
- Hepatolenticular Degeneration SyndromesC0019202
- Hepatolenticular degenerationC0019202
- Hepatolenticular degeneration syndromeC0019202
- KINNIER WILSON DISC0019202
- Kinnier Wilson DiseaseC0019202
- Kinnier-Wilson DiseaseC0019202
- Kinnier-Wilson DiseasesC0019202
- Kinnier-Wilson diseaseC0019202
- Lenticular Degeneration, ProgressiveC0019202
- Neurohepatic DegenerationC0019202
- Neurohepatic DegenerationsC0019202
- Neurohepatic degenerationC0019202
- Progressive Lenticular DegenerationC0019202
- Progressive lenticular degenerationC0019202
- Pseudoscleroses, CerebralC0019202
- PseudosclerosisC0019202
- Pseudosclerosis, CerebralC0019202
- Pseudosclerotic type of Wilson's diseaseC0019202
- Storage Disease, CopperC0019202
- Storage Diseases, CopperC0019202
- Syndrome, Hepatolenticular DegenerationC0019202
- Syndromes, Hepatolenticular DegenerationC0019202
- WD - Wilson's diseaseC0019202
- WILSON DISC0019202
- WILSON DISEASEC0019202
- WILSONS DISC0019202
- WNDC0019202
- Westphal Strumpell SyndromeC0019202
- Westphal Strumpell diseaseC0019202
- Westphal pseudosclerosisC0019202
- Westphal-Strumpell SyndromeC0019202
- Westphal-Strumpell SyndromesC0019202
- Westphal-Strumpell cerebral pseudosclerosisC0019202
- Westphal-Strumpell form of Wilson's diseaseC0019202
- Westphal-Strumpell syndromeC0019202
- Westphal-Strumpell syndrome (disorder)C0019202
- Wilson DiseaseC0019202
- Wilson Disease, Hepato-NeurologicC0019202
- Wilson Diseases, Hepato-NeurologicC0019202
- Wilson diseaseC0019202
- Wilson's DiseaseC0019202
- Wilson's diseaseC0019202
- Wilson's disease (disorder)C0019202
- Wilsons DiseaseC0019202
- cerebral pseudosclerosisC0019202
- disease wilsonC0019202
- disease wilson'sC0019202
- disease wilsonsC0019202
- diseases wilsonC0019202
- familial hepatitisC0019202
- hepato-lenticular degenerationC0019202
- hepatocerebral degenerationC0019202
- hepatolenticular degenerationC0019202
- neurohepatic degenerationC0019202
- wilson diseaseC0019202
- wilson's diseaseC0019202
- wilsons diseaseC0019202
Clinical Terms
- Progressive lenticular degeneration
- Westphal-Strumpell cerebral pseudosclerosis
- Degeneration Syndromes, Hepatolenticular
- Kinnier-Wilson disease
- hepato-lenticular degeneration
- Hepatolenticular Degeneration Syndromes
- Westphal-Strumpell Syndrome
- Hepatocerebral Degeneration
- Dementia due to Wilson's disease
- Chorea co-occurrent and due to Wilson disease
- Dementia due to hepatolenticular degeneration
- Hepato-Neurologic Wilson Diseases
- WILSONS DIS
- Hypoparathyroidism due to Wilson disease
- Wilson Disease
- Diseases, Copper Storage
- Chorea due to metabolic disorder
- Wilsons Disease
- Degeneration, Neurohepatic
- Disorder of liver due to disorder of mineral metabolism
- diseases wilson
- Hepatolenticular Degeneration Syndrome
- disease wilson's
- HEPATONEUROLOGIC WILSON DIS
- Chorea with Wilson disease
- Diseases, Kinnier-Wilson
- Syndromes, Hepatolenticular Degeneration
- WD - Wilson's disease
- Westphal Strumpell disease
- Copper storage disease
- WND
- Dementia due to metabolic abnormality
- Westphal pseudosclerosis
- Hepatolenticular degeneration
- Wilson Disease, Hepato-Neurologic
- Kinnier Wilson Disease
- Degenerations, Neurohepatic
- Pseudosclerosis
- Gowers' chorea
- Cerebral Pseudosclerosis
- Wilson Diseases, Hepato-Neurologic
- Copper Storage Diseases
- Neurohepatic degeneration
- Disorder of copper metabolism
- Hepatocerebral Degenerations
- Dementia due to Wilson disease
- KINNIER WILSON DIS
- Degenerations, Hepatocerebral
- familial hepatitis
- Disease, Copper Storage
- WILSON DIS
- Degeneration, Hepatocerebral
- Pseudosclerosis, Cerebral
- Degeneration Syndrome, Hepatolenticular
- Chorea due to heredodegenerative disorder
- Westphal Strumpell Syndrome
- Neurohepatic Degenerations
- Dystonia due to Wilson disease
- Dementia due to genetic disease
- disease wilsons
- Westphal-Strumpell syndrome (disorder)
- Copper metabolism disorder
- Pseudoscleroses, Cerebral
- Cerebral Pseudoscleroses
- Syndrome, Hepatolenticular Degeneration
- Storage Diseases, Copper
- Westphal-Strumpell Syndromes
- Pseudosclerotic type of Wilson's disease
- Storage Disease, Copper
- Degeneration, Progressive Lenticular
- Lenticular Degeneration, Progressive
- Westphal-Strumpell form of Wilson's disease
- disease wilson
- Degeneration, Hepatolenticular
- Kinnier-Wilson Diseases
- Hepato Neurologic Wilson Disease
- Wilson's disease (disorder)
- Diseases, Hepato-Neurologic Wilson
- Hepato-Neurologic Wilson Disease
Frequently Asked Questions
What is the ICD-10 code for wilson's disease?
The ICD-10-CM code for wilson's disease is E83.01. The full clinical description is "Wilson's disease". E83.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E83.01 mean?
ICD-10-CM code E83.01 represents “Wilson's disease”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E83.01 a billable code?
Yes, E83.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E83.01 in?
E83.01 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E83.01?
E83.01 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E83.01 map to?
E83.01 maps to 12 SNOMED CT concepts: 724766009, 722966004, 1259619002, 79886009, 88518009, and 7 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E83.01?
E83.01 is linked to 1 UMLS Concept Unique Identifier: C0019202. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E83.01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like wilson's disease affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E83.01?
There is no direct ICD-11 mapping available for E83.01 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.