E83.110
BillableHereditary hemochromatosis
Hereditary hemochromatosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Bronzed diabetes
- Pigmentary cirrhosis (of liver)
- Primary (hereditary) hemochromatosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •dietary mineral deficiencyE58-E61
- •parathyroid disordersE20-E21
- •vitamin D deficiencyE55
- •iron deficiency anemiaD50
- •sideroblastic anemiaD64.0-D64.3
- •GALDP78.84
- •Gestational alloimmune liver diseaseP78.84
- •Neonatal hemochromatosisP78.84
Related Codes(3)
Also Known As / Clinical Terms(275)
SNOMED CT
- Familial haemochromatosis35400008
- Familial hemochromatosis35400008
- Hereditary haemochromatosis35400008
- Hereditary hemochromatosis35400008
- Hypochromic microcytic anaemia44666001
- Hypochromic microcytic anemia44666001
- Microcytic hypochromic anaemia44666001
- Microcytic hypochromic anemia44666001
- HJV or HAMP-related haemochromatosis50855007
- HJV or HAMP-related hemochromatosis50855007
- Haemochromatosis type 250855007
- Hemochromatosis type 250855007
- Juvenile haemochromatosis50855007
- Juvenile hemochromatosis50855007
- Bronze cirrhosis78208005
- Pigment cirrhosis78208005
- Pigmentary cirrhosis of liver78208005
- Bronze diabetes399144008
- Bronzed diabetes399144008
- Primary haemochromatosis399170009
- Primary hemochromatosis399170009
- Hypochromic microcytic anaemia with iron overload711161006
- Hypochromic microcytic anemia with iron overload711161006
- Microcytic anaemia and hepatic iron overload711161006
- Microcytic anaemia with liver iron overload711161006
- Microcytic anemia and hepatic iron overload711161006
- Microcytic anemia with liver iron overload711161006
- Haemochromatosis type 3719974003
- Hemochromatosis type 3719974003
- TFR2 (transferrin receptor 2 gene) related haemochromatosis719974003
- TFR2 (transferrin receptor 2 gene) related hemochromatosis719974003
- Autosomal dominant hereditary haemochromatosis719975002
- Autosomal dominant hereditary hemochromatosis719975002
- Haemochromatosis due to defect in ferroportin719975002
- Haemochromatosis type 4719975002
- Hemochromatosis due to defect in ferroportin719975002
- Hemochromatosis type 4719975002
- Type 2B juvenile hereditary haemochromatosis1186844002
- Type 2B juvenile hereditary hemochromatosis1186844002
- HFE related haemochromatosis1186847009
- HFE related hemochromatosis1186847009
- Haemochromatosis type 11186847009
- Hemochromatosis type 11186847009
- Type 2A juvenile hereditary haemochromatosis1186849007
- Type 2A juvenile hereditary hemochromatosis1186849007
- FTH1 (ferritin heavy chain 1) related iron overload1230310007
- FTH1-associated iron overload1230310007
- FTH1-related iron overload1230310007
- Ferritin heavy chain 1-related iron overload1230310007
- Symptomatic form of classic haemochromatosis1237181009
- Symptomatic form of classic hemochromatosis1237181009
- Symptomatic form of haemochromatosis type 11237181009
- Symptomatic form of hemochromatosis type 11237181009
- Digenic haemochromatosis1299153008
- Digenic hemochromatosis1299153008
- SLC40A1-related haemochromatosis1303910000
- SLC40A1-related hemochromatosis1303910000
- Solute carrier family 40 member 1-related haemochromatosis1303910000
- Solute carrier family 40 member 1-related hemochromatosis1303910000
- Ferroportin disease1303911001
- Haemochromatosis type 4A1303911001
- Hemochromatosis type 4A1303911001
UMLS
- Bronze DiabetesC0018995
- Bronze diabetesC0018995
- Bronze diabetes (disorder)C0018995
- Bronzed CirrhosesC0018995
- Bronzed CirrhosisC0018995
- Bronzed diabetesC0018995
- Cirrhoses, BronzedC0018995
- Cirrhoses, PigmentaryC0018995
- Cirrhosis, BronzedC0018995
- Cirrhosis, PigmentaryC0018995
- Diabetes, BronzeC0018995
- Disease, Von Recklenhausen-ApplebaumC0018995
- Diseases, Von Recklenhausen-ApplebaumC0018995
- Disorder, Iron StorageC0018995
- Disorders, Iron StorageC0018995
- HaemochromatosesC0018995
- HaemochromatosisC0018995
- HemochromatoseC0018995
- HemochromatosesC0018995
- HemochromatosisC0018995
- Hemochromatosis (disorder)C0018995
- Hemochromatosis, unspecifiedC0018995
- HemosiderosisC0018995
- Iron Overload DiseaseC0018995
- Iron Storage DisorderC0018995
- Iron Storage DisordersC0018995
- Iron overload diseaseC0018995
- Iron storage diseaseC0018995
- Iron storage disorderC0018995
- Pigmentary CirrhosesC0018995
- Pigmentary CirrhosisC0018995
- Recklenhausen-Applebaum Disease, VonC0018995
- Recklenhausen-Applebaum Diseases, VonC0018995
- Storage Disorder, IronC0018995
- Storage Disorders, IronC0018995
- Syndrome, Troisier-Hanot-ChauffardC0018995
- Syndromes, Troisier-Hanot-ChauffardC0018995
- Troisier Hanot Chauffard SyndromeC0018995
- Troisier-Hanot-Chauffard SyndromeC0018995
- Troisier-Hanot-Chauffard SyndromesC0018995
- Troisier-Hanot-Chauffard syndromeC0018995
- Von Recklenhausen Applebaum DiseaseC0018995
- Von Recklenhausen-Applebaum DiseaseC0018995
- Von Recklenhausen-Applebaum DiseasesC0018995
- Von Recklenhausen-Applebaum diseaseC0018995
- bronze diabetesC0018995
- bronzed diabetesC0018995
- diabetes bronzeC0018995
- disorders iron storageC0018995
- haemochromatosisC0018995
- hemochromatosesC0018995
- hemochromatosisC0018995
- iron storage diseaseC0018995
- iron storage disorderC0018995
- Bronze cirrhosisC1442995
- Bronzed cirrhosisC1442995
- Pigment cirrhosisC1442995
- Pigment cirrhosis (disorder)C1442995
- Pigmentary cirrhosisC1442995
- Pigmentary cirrhosis (of liver)C1442995
- Pigmentary cirrhosis of liverC1442995
- Familial HemochromatosesC0392514
- Familial HemochromatosisC0392514
- Familial haemochromatosisC0392514
- Familial hemochromatosisC0392514
- Genetic HemochromatosesC0392514
- Genetic HemochromatosisC0392514
- Genetic hemochromatosisC0392514
- HEMOCHROMATOSIS, HEREDITARYC0392514
- HLAHC0392514
- Hemochromatoses, FamilialC0392514
- Hemochromatoses, GeneticC0392514
- Hemochromatosis, FamilialC0392514
- Hemochromatosis, GeneticC0392514
- Hereditary HemochromatosisC0392514
- Hereditary haemochromatosisC0392514
- Hereditary hemochromatosisC0392514
- Hereditary hemochromatosis (disorder)C0392514
- Idiopathic haemochromatosisC0392514
- Idiopathic hemochromatosisC0392514
- Idiopathic hemochromatosis (disorder)C0392514
- Primary HemochromatosisC0392514
- Primary haemochromatosisC0392514
- Primary hemochromatosisC0392514
- Primary hemochromatosis (disorder)C0392514
- familial haemochromatosisC0392514
- familial hemochromatosisC0392514
- hemochromatosis hereditaryC0392514
- hereditary haemochromatosisC0392514
- hereditary hemochromatosisC0392514
- idiopathic hemochromatosisC0392514
- primary haemochromatosisC0392514
- primary hemochromatosisC0392514
- Primary (hereditary) hemochromatosisC2921013
Clinical Terms
- familial haemochromatosis
- Microcytic anemia and hepatic iron overload
- Haemochromatosis type 4A
- Type 2B juvenile hereditary hemochromatosis
- Primary (hereditary) hemochromatosis
- Hemochromatosis, unspecified
- HEMOCHROMATOSIS, HEREDITARY
- Iron storage disorder
- Haemochromatosis type 3
- Microcytic anaemia with liver iron overload
- HFE related haemochromatosis
- Hypochromic microcytic anaemia
- Digenic haemochromatosis
- bronzed diabetes
- Pigmentary cirrhosis
- HLAH
- Primary haemochromatosis
- SLC40A1-related haemochromatosis
- Recklenhausen-Applebaum Disease, Von
- Haemochromatosis type 2
- HJV or HAMP-related haemochromatosis
- Bronzed Cirrhosis
- Genetic hemochromatosis
- disorders iron storage
- Bronze cirrhosis
- Hemochromatosis due to defect in ferroportin
- haemochromatosis
- FTH1-related iron overload
- Cirrhoses, Pigmentary
- Hypochromic microcytic anaemia with iron overload
- hemochromatosis hereditary
- Hemochromatosis, Genetic
- hereditary haemochromatosis
- Genetic Hemochromatoses
- Microcytic anaemia and hepatic iron overload
- Bronze diabetes
- Pigmentary Cirrhoses
- Hemochromatosis (disorder)
- Disorder, Iron Storage
- Disease, Von Recklenhausen-Applebaum
- Familial Hemochromatosis
- Ferritin heavy chain 1-related iron overload
- Pigmentary cirrhosis (of liver)
- Hemochromatosis type 1
- Bronzed Cirrhoses
- HFE related hemochromatosis
- Hypochromic microcytic anemia
- Juvenile haemochromatosis
- Hemosiderosis
- Diseases, Von Recklenhausen-Applebaum
- Hemochromatosis type 3
- Storage Disorders, Iron
- Hypochromic microcytic anemia with iron overload
- Solute carrier family 40 member 1-related haemochromatosis
- hemochromatoses
- Recklenhausen-Applebaum Diseases, Von
- iron storage disease
- Von Recklenhausen-Applebaum Diseases
- TFR2 (transferrin receptor 2 gene) related haemochromatosis
- Syndromes, Troisier-Hanot-Chauffard
- Autosomal dominant hereditary haemochromatosis
- SLC40A1-related hemochromatosis
- Microcytic hypochromic anaemia
- Iron Storage Disorders
- Bronze diabetes (disorder)
- Troisier-Hanot-Chauffard syndrome
- diabetes bronze
- Cirrhosis, Pigmentary
- Symptomatic form of classic haemochromatosis
- Disorders, Iron Storage
- Symptomatic form of classic hemochromatosis
- Primary hemochromatosis
- Symptomatic form of hemochromatosis type 1
- Haemochromatosis due to defect in ferroportin
- Autosomal dominant hereditary hemochromatosis
- Cirrhoses, Bronzed
- Hemochromatosis type 2
- Hemochromatosis type 4
- Idiopathic haemochromatosis
- Von Recklenhausen Applebaum Disease
- Microcytic hypochromic anemia
- Digenic hemochromatosis
- Haemochromatoses
- Troisier-Hanot-Chauffard Syndromes
- Haemochromatosis type 4
- Type 2B juvenile hereditary haemochromatosis
- Iron overload disease
- Troisier Hanot Chauffard Syndrome
- hemochromatosis
- Idiopathic hemochromatosis
- Diabetes, Bronze
- Hemochromatoses, Genetic
- Syndrome, Troisier-Hanot-Chauffard
- Storage Disorder, Iron
- HJV or HAMP-related hemochromatosis
- Hemochromatosis, Familial
- FTH1 (ferritin heavy chain 1) related iron overload
- FTH1-associated iron overload
- Solute carrier family 40 member 1-related hemochromatosis
- Juvenile hemochromatosis
- TFR2 (transferrin receptor 2 gene) related hemochromatosis
- Von Recklenhausen-Applebaum disease
- Ferroportin disease
- Cirrhosis, Bronzed
- Microcytic anemia with liver iron overload
- Haemochromatosis type 1
- Type 2A juvenile hereditary hemochromatosis
- Symptomatic form of haemochromatosis type 1
- Hereditary hemochromatosis (disorder)
- Pigment cirrhosis
- Familial Hemochromatoses
- Idiopathic hemochromatosis (disorder)
- Hemochromatosis type 4A
- Pigment cirrhosis (disorder)
- Pigmentary cirrhosis of liver
- Primary hemochromatosis (disorder)
- Hemochromatoses, Familial
- Hemochromatose
- Type 2A juvenile hereditary haemochromatosis
Frequently Asked Questions
What is the ICD-10 code for hereditary hemochromatosis?
The ICD-10-CM code for hereditary hemochromatosis is E83.110. The full clinical description is "Hereditary hemochromatosis". E83.110 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E83.110 mean?
ICD-10-CM code E83.110 represents “Hereditary hemochromatosis”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E83.110 a billable code?
Yes, E83.110 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E83.110 in?
E83.110 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E83.110?
E83.110 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 11 more.
What SNOMED CT codes does E83.110 map to?
E83.110 maps to 17 SNOMED CT concepts: 719975002, 78208005, 399144008, 1299153008, 1230310007, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E83.110?
E83.110 is linked to 4 UMLS Concept Unique Identifiers: C0018995, C1442995, C0392514, C2921013. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E83.110 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary hemochromatosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E83.110?
There is no direct ICD-11 mapping available for E83.110 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.