AutoICD API

E83.110

Billable

Hereditary hemochromatosis

Hereditary hemochromatosis

Status

Billable / Specific

Block

E70-E88

Parent Code

E83.11

Coding Notes

Related Codes(3)
Also Known As / Clinical Terms(275)

SNOMED CT

UMLS

Clinical Terms

  • familial haemochromatosis
  • Microcytic anemia and hepatic iron overload
  • Haemochromatosis type 4A
  • Type 2B juvenile hereditary hemochromatosis
  • Primary (hereditary) hemochromatosis
  • Hemochromatosis, unspecified
  • HEMOCHROMATOSIS, HEREDITARY
  • Iron storage disorder
  • Haemochromatosis type 3
  • Microcytic anaemia with liver iron overload
  • HFE related haemochromatosis
  • Hypochromic microcytic anaemia
  • Digenic haemochromatosis
  • bronzed diabetes
  • Pigmentary cirrhosis
  • HLAH
  • Primary haemochromatosis
  • SLC40A1-related haemochromatosis
  • Recklenhausen-Applebaum Disease, Von
  • Haemochromatosis type 2
  • HJV or HAMP-related haemochromatosis
  • Bronzed Cirrhosis
  • Genetic hemochromatosis
  • disorders iron storage
  • Bronze cirrhosis
  • Hemochromatosis due to defect in ferroportin
  • haemochromatosis
  • FTH1-related iron overload
  • Cirrhoses, Pigmentary
  • Hypochromic microcytic anaemia with iron overload
  • hemochromatosis hereditary
  • Hemochromatosis, Genetic
  • hereditary haemochromatosis
  • Genetic Hemochromatoses
  • Microcytic anaemia and hepatic iron overload
  • Bronze diabetes
  • Pigmentary Cirrhoses
  • Hemochromatosis (disorder)
  • Disorder, Iron Storage
  • Disease, Von Recklenhausen-Applebaum
  • Familial Hemochromatosis
  • Ferritin heavy chain 1-related iron overload
  • Pigmentary cirrhosis (of liver)
  • Hemochromatosis type 1
  • Bronzed Cirrhoses
  • HFE related hemochromatosis
  • Hypochromic microcytic anemia
  • Juvenile haemochromatosis
  • Hemosiderosis
  • Diseases, Von Recklenhausen-Applebaum
  • Hemochromatosis type 3
  • Storage Disorders, Iron
  • Hypochromic microcytic anemia with iron overload
  • Solute carrier family 40 member 1-related haemochromatosis
  • hemochromatoses
  • Recklenhausen-Applebaum Diseases, Von
  • iron storage disease
  • Von Recklenhausen-Applebaum Diseases
  • TFR2 (transferrin receptor 2 gene) related haemochromatosis
  • Syndromes, Troisier-Hanot-Chauffard
  • Autosomal dominant hereditary haemochromatosis
  • SLC40A1-related hemochromatosis
  • Microcytic hypochromic anaemia
  • Iron Storage Disorders
  • Bronze diabetes (disorder)
  • Troisier-Hanot-Chauffard syndrome
  • diabetes bronze
  • Cirrhosis, Pigmentary
  • Symptomatic form of classic haemochromatosis
  • Disorders, Iron Storage
  • Symptomatic form of classic hemochromatosis
  • Primary hemochromatosis
  • Symptomatic form of hemochromatosis type 1
  • Haemochromatosis due to defect in ferroportin
  • Autosomal dominant hereditary hemochromatosis
  • Cirrhoses, Bronzed
  • Hemochromatosis type 2
  • Hemochromatosis type 4
  • Idiopathic haemochromatosis
  • Von Recklenhausen Applebaum Disease
  • Microcytic hypochromic anemia
  • Digenic hemochromatosis
  • Haemochromatoses
  • Troisier-Hanot-Chauffard Syndromes
  • Haemochromatosis type 4
  • Type 2B juvenile hereditary haemochromatosis
  • Iron overload disease
  • Troisier Hanot Chauffard Syndrome
  • hemochromatosis
  • Idiopathic hemochromatosis
  • Diabetes, Bronze
  • Hemochromatoses, Genetic
  • Syndrome, Troisier-Hanot-Chauffard
  • Storage Disorder, Iron
  • HJV or HAMP-related hemochromatosis
  • Hemochromatosis, Familial
  • FTH1 (ferritin heavy chain 1) related iron overload
  • FTH1-associated iron overload
  • Solute carrier family 40 member 1-related hemochromatosis
  • Juvenile hemochromatosis
  • TFR2 (transferrin receptor 2 gene) related hemochromatosis
  • Von Recklenhausen-Applebaum disease
  • Ferroportin disease
  • Cirrhosis, Bronzed
  • Microcytic anemia with liver iron overload
  • Haemochromatosis type 1
  • Type 2A juvenile hereditary hemochromatosis
  • Symptomatic form of haemochromatosis type 1
  • Hereditary hemochromatosis (disorder)
  • Pigment cirrhosis
  • Familial Hemochromatoses
  • Idiopathic hemochromatosis (disorder)
  • Hemochromatosis type 4A
  • Pigment cirrhosis (disorder)
  • Pigmentary cirrhosis of liver
  • Primary hemochromatosis (disorder)
  • Hemochromatoses, Familial
  • Hemochromatose
  • Type 2A juvenile hereditary haemochromatosis
Frequently Asked Questions
What is the ICD-10 code for hereditary hemochromatosis?

The ICD-10-CM code for hereditary hemochromatosis is E83.110. The full clinical description is "Hereditary hemochromatosis". E83.110 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E83.110 mean?

ICD-10-CM code E83.110 represents “Hereditary hemochromatosis”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E83.110 a billable code?

Yes, E83.110 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E83.110 in?

E83.110 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E83.110?

E83.110 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 11 more.

What SNOMED CT codes does E83.110 map to?

E83.110 maps to 17 SNOMED CT concepts: 719975002, 78208005, 399144008, 1299153008, 1230310007, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E83.110?

E83.110 is linked to 4 UMLS Concept Unique Identifiers: C0018995, C1442995, C0392514, C2921013. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E83.110 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary hemochromatosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E83.110?

There is no direct ICD-11 mapping available for E83.110 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.