D64.0
BillableHereditary sideroblastic anemia
Hereditary sideroblastic anemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Sex-linked hypochromic sideroblastic anemia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(6)
Related Conditions
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(94)
SNOMED CT
- X chromosome-linked sideroblastic anaemia48983004
- X chromosome-linked sideroblastic anemia48983004
- X-linked sideroblastic anaemia48983004
- X-linked sideroblastic anemia48983004
- Autosomal recessive sideroblastic anaemia717050005
- Autosomal recessive sideroblastic anemia717050005
- X-linked sideroblastic anaemia with spinocerebellar ataxia719816006
- X-linked sideroblastic anemia with spinocerebellar ataxia719816006
- Adult-onset autosomal recessive sideroblastic anaemia720465002
- Adult-onset autosomal recessive sideroblastic anemia720465002
- GLRX5 (glutaredoxin 5) related sideroblastic anaemia720465002
- GLRX5 (glutaredoxin 5) related sideroblastic anemia720465002
- Mitochondrial myopathy with sideroblastic anaemia syndrome724138007
- Mitochondrial myopathy with sideroblastic anemia syndrome724138007
- Myopathy, lactic acidosis and sideroblastic anaemia724138007
- Myopathy, lactic acidosis and sideroblastic anemia724138007
- Severe congenital hypochromic anaemia with ringed sideroblasts725463007
- Severe congenital hypochromic anemia with ringed sideroblasts725463007
- Severe congenital hypochromic sideroblastic anaemia725463007
- Severe congenital hypochromic sideroblastic anemia725463007
- Congenital sideroblastic anaemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome765327005
- Congenital sideroblastic anemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome765327005
- Autosomal dominant sideroblastic anaemia1148914007
- Autosomal dominant sideroblastic anemia1148914007
UMLS
- ANEMIA, HEREDITARY SIDEROBLASTICC4551511
- ANEMIA, HYPOCHROMICC4551511
- ANEMIA, SIDEROBLASTIC, 1C4551511
- ANEMIA, SIDEROBLASTIC, X-LINKEDC4551511
- ANH1C4551511
- Anemia, Hereditary SideroblasticC4551511
- Anemia, Sex-Linked Hypochromic SideroblasticC4551511
- Anemia, Sideroblastic, X-LinkedC4551511
- Anemia, sex-linked hypochromic sideroblasticC4551511
- Congenital Sideroblastic AnaemiaC4551511
- Erythroid 5-Aminolevulinate Synthase DeficiencyC4551511
- Erythroid 5-aminolevulinate synthase deficiencyC4551511
- HEREDITARY IRON-LOADING ANEMIAC4551511
- Hereditary Iron-Loading AnemiaC4551511
- SIDBA1C4551511
- Sex-linked hypochromic sideroblastic anemiaC4551511
- X Chromosome-Linked Sideroblastic AnemiaC4551511
- X chromosome-linked sideroblastic anaemiaC4551511
- X chromosome-linked sideroblastic anemiaC4551511
- X chromosome-linked sideroblastic anemia (disorder)C4551511
- X-Linked Pyridoxine-Responsive Sideroblastic AnemiaC4551511
- X-linked pyridoxine-responsive sideroblastic anemiaC4551511
- X-linked sideroblastic anaemiaC4551511
- X-linked sideroblastic anemiaC4551511
- XLSAC4551511
- Anemia, hereditary sideroblasticC0221018
- Congenital sideroblastic anaemiaC0221018
- Hereditary Sideroblastic AnemiaC0221018
- Hereditary iron-loading anemiaC0221018
- Hereditary sideroblastic anaemiaC0221018
- Hereditary sideroblastic anemiaC0221018
Clinical Terms
- ANEMIA, HEREDITARY SIDEROBLASTIC
- X-linked pyridoxine-responsive sideroblastic anemia
- Adult-onset autosomal recessive sideroblastic anemia
- ANEMIA, SIDEROBLASTIC, 1
- Anemia, Sideroblastic, X-Linked
- GLRX5 (glutaredoxin 5) related sideroblastic anemia
- X-linked sideroblastic anemia
- GLRX5 (glutaredoxin 5) related sideroblastic anaemia
- Congenital sideroblastic anaemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome
- Hereditary sideroblastic anaemia
- Adult-onset autosomal recessive sideroblastic anaemia
- XLSA
- X-linked sideroblastic anaemia
- X-linked sideroblastic anemia with spinocerebellar ataxia
- Autosomal dominant sideroblastic anaemia
- ANEMIA, HYPOCHROMIC
- Anemia, Sex-Linked Hypochromic Sideroblastic
- ANH1
- Severe congenital hypochromic anaemia with ringed sideroblasts
- X-linked sideroblastic anaemia with spinocerebellar ataxia
- X chromosome-linked sideroblastic anemia
- Myopathy, lactic acidosis and sideroblastic anemia
- Congenital Sideroblastic Anaemia
- Myopathy, lactic acidosis and sideroblastic anaemia
- Severe congenital hypochromic sideroblastic anemia
- Mitochondrial myopathy with sideroblastic anemia syndrome
- Sex-linked hypochromic sideroblastic anemia
- X chromosome-linked sideroblastic anemia (disorder)
- Mitochondrial myopathy with sideroblastic anaemia syndrome
- HEREDITARY IRON-LOADING ANEMIA
- Congenital sideroblastic anemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome
- Erythroid 5-Aminolevulinate Synthase Deficiency
- Autosomal recessive sideroblastic anemia
- Severe congenital hypochromic sideroblastic anaemia
- SIDBA1
- Severe congenital hypochromic anemia with ringed sideroblasts
- Autosomal dominant sideroblastic anemia
- X chromosome-linked sideroblastic anaemia
- Autosomal recessive sideroblastic anaemia
Frequently Asked Questions
What is the ICD-10 code for hereditary sideroblastic anemia?
The ICD-10-CM code for hereditary sideroblastic anemia is D64.0. The full clinical description is "Hereditary sideroblastic anemia". D64.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D64.0 mean?
ICD-10-CM code D64.0 represents “Hereditary sideroblastic anemia”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D64.0 a billable code?
Yes, D64.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D64.0 in?
D64.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D64.0?
D64.0 has Excludes1 notes indicating codes that cannot be used together with it, including: refractory anemia (D46.-); refractory anemia with excess blasts in transformation [RAEB T] (C92.0-).
What SNOMED CT codes does D64.0 map to?
D64.0 maps to 8 SNOMED CT concepts: 720465002, 1148914007, 717050005, 765327005, 724138007, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D64.0?
D64.0 is linked to 2 UMLS Concept Unique Identifiers: C4551511, C0221018. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D64.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary sideroblastic anemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D64.0?
D64.0 maps to the ICD-11 code: 3A72.0Z (Congenital sideroblastic anaemias, unspecified).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.