H49.40
BillableProgressive external ophthalmoplegia, unspecified eye
Progressive external ophthalmoplegia, unspecified eye
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •diabetes mellitus related eye conditions, , ,E09.3, E10.3, E11.3, E13.3
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury (trauma) of eye and orbitS05
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •syphilis related eye disorders, , ,A50.01, A50.3, A51.43, A52.71
- •nystagmus and other irregular eye movementsH55
- •internal ophthalmoplegiaH52.51
- •internuclear ophthalmoplegiaH51.2
- •progressive supranuclear ophthalmoplegiaG23.1
Related Codes(3)
Also Known As / Clinical Terms(51)
SNOMED CT
- CPEO - chronic progressive external ophthalmoplegia46252003
- Chronic progressive external ophthalmoplegia46252003
- Chronic progressive ophthalmoplegia46252003
- Graefe's disease46252003
- PEO - Progressive external ophthalmoplegia46252003
- Progressive external ophthalmoplegia46252003
- Ophthalmoplegia plus syndrome77835008
- Painful ophthalmoplegia95794005
- Tolosa-Hunt syndrome95794005
- Oculomotor nerve finding106153001
- Third cranial nerve finding106153001
- Adult-onset CPEO (chronic progressive external ophthalmoplegia) with mitochondrial myopathy725464001
- Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy725464001
- Mitochondrial DNA (deoxyribonucleic acid) maintenance syndrome due to MGME1 (mitochondrial genome maintenance exonuclease 1) deficiency764733009
- PEO (progressive external ophthalmoplegia) myopathy emaciation syndrome764733009
- Progressive external ophthalmoplegia, myopathy, emaciation syndrome764733009
- Autosomal dominant progressive external ophthalmoplegia827115000
- adPEO - autosomal dominant progressive external ophthalmoplegia827115000
- Autosomal recessive progressive external ophthalmoplegia827117008
- arPEO- autosomal recessive progressive external ophthalmoplegia827117008
- Autosomal dominant progressive external ophthalmoplegia type 51156853004
- Autosomal dominant progressive external ophthalmoplegia type 31156855006
- Autosomal dominant progressive external ophthalmoplegia type 41156856007
- Autosomal dominant progressive external ophthalmoplegia type 11156857003
- Autosomal dominant progressive external ophthalmoplegia type 21156858008
Clinical Terms
- Adult-onset CPEO (chronic progressive external ophthalmoplegia) with mitochondrial myopathy
- Ophthalmoplegia plus syndrome
- Progressive external ophthalmoplegia
- Autosomal dominant progressive external ophthalmoplegia type 4
- Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy
- Graefe's disease
- CPEO - chronic progressive external ophthalmoplegia
- Chronic progressive external ophthalmoplegia
- Painful ophthalmoplegia
- arPEO- autosomal recessive progressive external ophthalmoplegia
- Oculomotor nerve finding
- Autosomal dominant progressive external ophthalmoplegia type 1
- adPEO - autosomal dominant progressive external ophthalmoplegia
- PEO (progressive external ophthalmoplegia) myopathy emaciation syndrome
- Third cranial nerve finding
- Autosomal dominant progressive external ophthalmoplegia type 3
- Autosomal dominant progressive external ophthalmoplegia type 2
- Progressive external ophthalmoplegia, myopathy, emaciation syndrome
- Autosomal dominant progressive external ophthalmoplegia type 5
- Mitochondrial DNA (deoxyribonucleic acid) maintenance syndrome due to MGME1 (mitochondrial genome maintenance exonuclease 1) deficiency
- Autosomal recessive progressive external ophthalmoplegia
- PEO - Progressive external ophthalmoplegia
- Chronic progressive ophthalmoplegia
- Autosomal dominant progressive external ophthalmoplegia
- Tolosa-Hunt syndrome
Frequently Asked Questions
What is the ICD-10 code for progressive external ophthalmoplegia, unspecified eye?
The ICD-10-CM code for progressive external ophthalmoplegia, unspecified eye is H49.40. The full clinical description is "Progressive external ophthalmoplegia, unspecified eye". H49.40 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code H49.40 mean?
ICD-10-CM code H49.40 represents “Progressive external ophthalmoplegia, unspecified eye”. It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a billable/specific code that can be used on a claim.
Is H49.40 a billable code?
Yes, H49.40 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is H49.40 in?
H49.40 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What codes cannot be used with H49.40?
H49.40 has Excludes1 notes indicating codes that cannot be used together with it, including: Kearns-Sayre syndrome (H49.81-).
What SNOMED CT codes does H49.40 map to?
H49.40 maps to 13 SNOMED CT concepts: 725464001, 827115000, 1156857003, 1156858008, 1156855006, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for H49.40?
H49.40 is linked to 1 UMLS Concept Unique Identifier: C2881296. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does H49.40 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like progressive external ophthalmoplegia, unspecified eye affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of H49.40?
There is no direct ICD-11 mapping available for H49.40 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.