H49.4
Non-billableProgressive external ophthalmoplegia
Progressive external ophthalmoplegia
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •diabetes mellitus related eye conditions, , ,E09.3, E10.3, E11.3, E13.3
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury (trauma) of eye and orbitS05
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •syphilis related eye disorders, , ,A50.01, A50.3, A51.43, A52.71
- •nystagmus and other irregular eye movementsH55
- •internal ophthalmoplegiaH52.51
- •internuclear ophthalmoplegiaH51.2
- •progressive supranuclear ophthalmoplegiaG23.1
Child Codes (4)
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(36)
UMLS
- CPEOC0162674
- CPEO - chronic progressive external ophthalmoplegiaC0162674
- Chronic Progressive External OphthalmoplegiaC0162674
- Chronic progressive external ophthalmoplegiaC0162674
- Chronic progressive ophthalmoplegiaC0162674
- Disease, GraefeC0162674
- Dystrophy, Ocular MuscularC0162674
- External Ophthalmoplegia, ProgressiveC0162674
- External ophthalmoplegia, progressiveC0162674
- External ophthalmoplegia, progressive (PEO)C0162674
- GRAEFE DISC0162674
- Graefe DiseaseC0162674
- Graefe's DiseaseC0162674
- Graefe's diseaseC0162674
- Mitochondrial Ocular MyopathyC0162674
- Muscular Dystrophies, OcularC0162674
- Muscular Dystrophy, OcularC0162674
- Myopathy, Mitochondrial OcularC0162674
- Ocular Muscular DystrophiesC0162674
- Ocular Muscular DystrophyC0162674
- Ocular Myopathy of Von Graefe FuchsC0162674
- Ocular Myopathy of Von Graefe-FuchsC0162674
- Ocular Myopathy, MitochondrialC0162674
- Ophthalmoplegia, Chronic Progressive ExternalC0162674
- Ophthalmoplegia, Progressive ExternalC0162674
- Ophthalmoplegia, progressive externalC0162674
- PEOC0162674
- PEO - Progressive external ophthalmoplegiaC0162674
- Progressive External OphthalmoplegiaC0162674
- Progressive external ophthalmoplegiaC0162674
- Progressive external ophthalmoplegia (disorder)C0162674
- Progressive paralysis or weakness of muscles of eye motilityC0162674
- Progressive paralysis or weakness of muscles of eye movementC0162674
- chronic progressive external ophthalmoplegia (CPEO)C0162674
- chronic progressive paralysis of the external eye muscleC0162674
- cpeoC0162674
Frequently Asked Questions
What is the ICD-10 code for progressive external ophthalmoplegia?
The ICD-10-CM code for progressive external ophthalmoplegia is H49.4. The full clinical description is "Progressive external ophthalmoplegia". H49.4 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code H49.4 mean?
ICD-10-CM code H49.4 represents “Progressive external ophthalmoplegia”. It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a non-billable header code. Use a more specific child code for billing purposes.
Is H49.4 a billable code?
No, H49.4 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 4 child codes under H49.4.
What chapter is H49.4 in?
H49.4 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What codes cannot be used with H49.4?
H49.4 has Excludes1 notes indicating codes that cannot be used together with it, including: Kearns-Sayre syndrome (H49.81-).
What are the subcategories under H49.4?
H49.4 has 4 child codes, including: H49.40 (Progressive external ophthalmoplegia, unspecified eye), H49.41 (Progressive external ophthalmoplegia, right eye), H49.42 (Progressive external ophthalmoplegia, left eye), H49.43 (Progressive external ophthalmoplegia, bilateral).
What are the UMLS CUIs for H49.4?
H49.4 is linked to 1 UMLS Concept Unique Identifier: C0162674. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does H49.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like progressive external ophthalmoplegia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of H49.4?
H49.4 maps to the ICD-11 code: 9C82.0 (Progressive external ophthalmoplegia).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.