E85.4

Q: What is the ICD-11 equivalent of E85.4?

E85.4 maps to the ICD-11 code: 5D00.0 (AL amyloidosis). This is an equivalent mapping.

Billable

Organ-limited amyloidosis

Status

Billable / Specific

Chapter

4: Endocrine, Nutritional and Metabolic Diseases

Block

E70-E88

Parent Code

E85

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

Localized amyloidosis
Transthyretin-related (ATTR) familial amyloid cardiomyopathy

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(6)

E85.0

Non-neuropathic heredofamilial amyloidosis

Billable E85.1

Neuropathic heredofamilial amyloidosis

Billable E85.2

Heredofamilial amyloidosis, unspecified

Billable E85.3

Secondary systemic amyloidosis

Billable E85.8

Other amyloidosis

E85.9

Amyloidosis, unspecified

Billable

ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

5D00.0AL amyloidosisequivalentPrimary

Also Known As / Clinical Terms(269)

SNOMED CT

UMLS

Clinical Terms

Isolated atrial amyloid
Localized non-hereditary amyloidosis
Amyloid arthropathy
Localised amyloidosis
Localized amyloidosis
Glomerular disorder due to amyloidosis
Renal amyloidosis
Primary localized cutaneous amyloidosis
Nephropathic amyloidosis
Pulmonary amyloidosis
Systemic amyloidosis affecting skin
Localised non-hereditary amyloidosis
Disorder of glomerulus due to amyloidosis
Disorder of glomerulus due to organ-limited amyloidosis
Primary familial cardiomyopathy
Organ limited non-hereditary amyloidosis
Secondary localized cutaneous amyloidosis
Waxy kidney
Familial cardiomyopathy
Danish type amyloidosis
Amyloid disease of the urethra
Hereditary cerebral haemorrhage with amyloidosis - Dutch type
Denmark type amyloidosis
Lardaceous kidney
Amyloid of ureter
Familial non-neuropathic amyloidosis of heart
Neuropathy associated with dysproteinaemias
Amyloid of bladder
Acquired atrial abnormality
Arthritis secondary to amyloidosis
Infiltrative cardiomyopathy
Neuropathic heredofamilial amyloidosis
Amyloidosis of spleen
Congophilic angiopathy
Organ limited hereditary amyloidosis
Beta-2 microglobulin arthropathy
Familial oculoleptomeningeal amyloidosis
Danish type familial amyloid cardiomyopathy
Gingival amyloidosis
Arthropathy in amyloidosis
Amyloidosis limited to skin
Bullous cutaneous amyloidosis
Amyloid of urinary bladder
Amyloid arthritis
Localized hereditary amyloidosis
Wild-type transthyretin cardiac amyloidosis
Amyloid of testes
Amyloid of vitreous
Cardiac amyloidosis
Senile brain amyloidosis
Primary localised cutaneous nodular amyloidosis
Lichen amyloidosus
Amyloid of cornea
Hereditary cerebral amyloid angiopathy, Dutch type
Primary localized cutaneous nodular amyloidosis
Ocular amyloid deposit
Poikilodermal cutaneous amyloid
HCHWA - hereditary cerebral hemorrhage with amyloidosis
Arthritis due to haemodialysis-associated amyloidosis
PLCNA - Primary localized cutaneous nodular amyloidosis
Deposit on gingivae
Hereditary cerebrovascular amyloidosis
Neuropathy associated with dysproteinemias
Amyloidosis of small intestine
Nonneuropathic heredofamilial amyloidosis
Isolated corneal amyloidosis
Arthritis due to hemodialysis-associated amyloidosis
Articular amyloid
Macroglossia due to amyloidosis
Laryngeal amyloidosis
Arthritis due to beta-2 microglobulin amyloidosis
Hereditary cerebral hemorrhage with amyloidosis - Dutch type
Senile cardiac amyloidosis
Stiff heart syndrome
Amyloidosis cutis dyschromica
Sporadic cerebral amyloid angiopathy
Vitreous amyloid
Familial generalised dyschromic amyloidosis cutis
Macular cutaneous amyloidosis
Conjunctival amyloidosis
Corneal amyloidosis
Amyloidosis VII
Familial amyloid cardiomyopathy
Familial amyloid polyneuropathy affecting skin
Localised hereditary amyloidosis
Hereditary oculoleptomeningeal amyloid angiopathy
Localized amyloidosis (disorder)
Age-related amyloidosis
Bullous cutaneous amyloid
Amyloidosis cutis dyschromia
Glomerular disorder due to organ-limited amyloidosis
Amyloidosis of skin
AS type amyloidosis
HCHWA - hereditary cerebral haemorrhage with amyloidosis
Familial neuropathic amyloidosis
Amyloid nephropathy
Amyloid heart muscle disease
Dominant primary localised cutaneous amyloidosis
Dutch type amyloidosis
Hereditary cerebral haemorrhage with amyloidosis
Primary localised cutaneous amyloidosis
Senile amyloidosis
Soapy kidney
Amyloidosis IX
Familial non-neuropathic amyloidosis
Hepatic amyloidosis
Macule of skin
AF type amyloidosis
Ohio type amyloidosis
Autonomic neuropathy due to amyloidosis
AS transthyretin amyloidosis
CAA - Cerebral amyloid angiopathy
Heredofamilial systemic amyloidosis affecting skin
Familial amyloid polyneuropathy with cutaneous amyloidosis
Dominant primary localized cutaneous amyloidosis
Familial amyloid heart disease
Transthyretin-related (ATTR) familial amyloid cardiomyopathy
Lichen amyloidosis
Testicular amyloid
Familial amyloid polyneuropathy
Hereditary cerebral hemorrhage with amyloidosis
Familial polyneuropathic amyloidosis
Acquired abnormality of atrium
Cerebral amyloid angiopathy
Nodular amyloidosis
Familial amyloidosis cutis
Secondary localised cutaneous amyloidosis
AS beta protein amyloidosis
Familial generalized dyschromic amyloidosis cutis
Cardiac familial non-neuropathic amyloidosis
PLCNA - Primary localised cutaneous nodular amyloidosis
Amyloid lichen
Amyloid of prostate

Frequently Asked Questions

What is the ICD-10 code for organ-limited amyloidosis?

The ICD-10-CM code for organ-limited amyloidosis is E85.4. The full clinical description is "Organ-limited amyloidosis". E85.4 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E85.4 mean?

ICD-10-CM code E85.4 represents “Organ-limited amyloidosis”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E85.4 a billable code?

Yes, E85.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E85.4 in?

E85.4 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E85.4?

E85.4 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E85.4 map to?

E85.4 maps to 60 SNOMED CT concepts: 42295001, 4645000, 16573007, 69078007, 735569003, and 55 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E85.4?

E85.4 is linked to 3 UMLS Concept Unique Identifiers: C0268392, C0494354, C4509596. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E85.4 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like organ-limited amyloidosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E85.4?

E85.4 maps to the ICD-11 code: 5D00.0 (AL amyloidosis).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.