E85.1
BillableNeuropathic heredofamilial amyloidosis
Neuropathic heredofamilial amyloidosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Amyloid polyneuropathy (Portuguese)
- Transthyretin-related (ATTR) familial amyloid polyneuropathy
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(219)
SNOMED CT
- Amyloidosis, Indiana-Maryland type4463009
- Familial amyloid polyneuropathy type II4463009
- Familial amyloid polyneuropathy, 84 Ser-for-Ile4463009
- Familial amyloid polyneuropathy, Indiana-Swiss type4463009
- Familial amyloid polyneuropathy, type II4463009
- German type amyloid polyneuropathy4463009
- Hereditary neuropathic amyloidosis, type II4463009
- Indiana-Maryland type amyloid polyneuropathy4463009
- Rakavina type amyloidosis4463009
- Swiss type amyloid polyneuropathy4463009
- Familial amyloid polyneuropathy, 60 Ala-for-Thr5134006
- Familial amyloid polyneuropathy, Appalachian type5134006
- Familial amyloid polyneuropathy, type VI5134006
- Familial amyloid polyneuropathy type III9133005
- Familial amyloid polyneuropathy, Iowa type9133005
- Iowa type amyloid polyneuropathy9133005
- Iowa type amyloidosis9133005
- Van Allen type amyloid polyneuropathy9133005
- van Allen type amyloidosis9133005
- Familial amyloid polyneuropathy, 33 Ile-for-Phe41590007
- Familial amyloid polyneuropathy, Jewish type41590007
- Jewish type amyloid polyneuropathy41590007
- AF type amyloidosis42295001
- Familial amyloid polyneuropathy42295001
- Familial neuropathic amyloidosis42295001
- Familial polyneuropathic amyloidosis42295001
- Neuropathic heredofamilial amyloidosis42295001
- Amyloidosis VI45639009
- Hereditary cerebral amyloid angiopathy, Icelandic type45639009
- Hereditary cerebral haemorrhage with amyloidosis - Icelandic type45639009
- Hereditary cerebral hemorrhage with amyloidosis - Icelandic type45639009
- Hereditary cystatin C amyloid angiopathy45639009
- Iceland type amyloidosis45639009
- Icelandic type amyloidosis45639009
- Amyloid polyneuropathy193187004
- Polyneuropathy due to amyloidosis193187004
- Polyneuropathy in amyloidosis193187004
- Neuropathy associated with dysproteinaemias230585004
- Neuropathy associated with dysproteinemias230585004
- CAA - Cerebral amyloid angiopathy230724001
- Cerebral amyloid angiopathy230724001
- Congophilic angiopathy230724001
- Hereditary cerebrovascular amyloidosis237867001
- Localised hereditary amyloidosis237869003
- Localized hereditary amyloidosis237869003
- Organ limited hereditary amyloidosis237869003
- Amyloid polyneuropathy type I398229007
- Amyloidosis, type I398229007
- Andrade syndrome398229007
- Andrade type amyloid polyneuropathy398229007
- Corino de Andrade paramyloidosis398229007
- Familial amyloid neuropathy, Andrade type398229007
- Familial amyloid neuropathy, Portuguese type398229007
- Familial amyloid polyneuropathy, 30 Met-for-Val398229007
- Hereditary amyloid polyneuropathy Portuguese type398229007
- Hereditary neuropathic amyloidosis, type I398229007
- Japanese type amyloid polyneuropathy398229007
- Portuguese polyneuritic amyloidosis398229007
- Portuguese type amyloid polyneuropathy398229007
- Swedish type amyloid polyneuropathy398229007
- Wohlwill-Corino Andrade syndrome398229007
- Heredofamilial systemic amyloidosis affecting skin402459005
- Familial amyloid polyneuropathy affecting skin402460000
- Familial amyloid polyneuropathy with cutaneous amyloidosis402460000
- Systemic amyloidosis affecting skin402719006
- HCHWA - hereditary cerebral haemorrhage with amyloidosis724357007
- HCHWA - hereditary cerebral hemorrhage with amyloidosis724357007
- Hereditary cerebral haemorrhage with amyloidosis724357007
- Hereditary cerebral hemorrhage with amyloidosis724357007
- Disorder of glomerulus due to familial disease1148882003
- Glomerular disease due to familial disease1148882003
- Disorder of glomerulus due to familial amyloid polyneuropathy1187554000
- Disorder of glomerulus due to neuropathic heredofamilial amyloidosis1187554000
- Glomerular disorder due to neuropathic heredofamilial amyloidosis1187554000
- Disorder of glomerulus due to amyloidosis1187557007
- Glomerular disorder due to amyloidosis1187557007
- ATTRv amyloidosis1354544003
- Familial TTR-related amyloidosis1354544003
- Familial transthyretin-related amyloidosis1354544003
- Hereditary ATTR amyloidosis1354544003
- Hereditary TTR amyloid polyneuropathy1354544003
- Hereditary TTR amyloidosis1354544003
- Hereditary transthyretin amyloid polyneuropathy1354544003
- Hereditary transthyretin related amyloidosis1354544003
- hATTR - hereditary transthyretin related amyloidosis1354544003
UMLS
- AF type amyloidosisC0206245
- Amyloid Neuropathies, FamilialC0206245
- Amyloid Neuropathy, FamilialC0206245
- Amyloid Polyneuropathies, FamilialC0206245
- Amyloid Polyneuropathy, FamilialC0206245
- Amyloidoses, Hereditary NeuropathicC0206245
- Amyloidosis, Hereditary NeuropathicC0206245
- Familial Amyloid NeuropathiesC0206245
- Familial Amyloid NeuropathyC0206245
- Familial Amyloid PolyneuropathiesC0206245
- Familial Amyloid PolyneuropathyC0206245
- Familial amyloid polyneuropathyC0206245
- Familial amyloid polyneuropathy (disorder)C0206245
- Familial neuropathic amyloidosisC0206245
- Familial polyneuropathic amyloidosisC0206245
- Hereditary Neuropathic AmyloidosesC0206245
- Hereditary Neuropathic AmyloidosisC0206245
- Hereditary neuropathic amyloidosisC0206245
- Neuropathic Amyloidoses, HereditaryC0206245
- Neuropathic Amyloidosis, HereditaryC0206245
- Neuropathic heredofamilial amyloidosisC0206245
- Neuropathies, Familial AmyloidC0206245
- Neuropathy, Familial AmyloidC0206245
- Polyneuropathies, Familial AmyloidC0206245
- Polyneuropathy, Familial AmyloidC0206245
- amyloid familial polyneuropathiesC0206245
- familial amyloid polyneuropathyC0206245
- Amyloid polyneuropathy (Portuguese)C2874309
- Transthyretin-related (ATTR) familial amyloid polyneuropathyC4509022
Clinical Terms
- Hereditary cerebral haemorrhage with amyloidosis - Icelandic type
- Disorder of glomerulus due to neuropathic heredofamilial amyloidosis
- Amyloid Neuropathies, Familial
- Glomerular disorder due to amyloidosis
- Amyloidosis, type I
- Systemic amyloidosis affecting skin
- Disorder of glomerulus due to amyloidosis
- van Allen type amyloidosis
- Amyloidosis, Indiana-Maryland type
- Amyloidosis, Hereditary Neuropathic
- Neuropathy associated with dysproteinaemias
- Iowa type amyloid polyneuropathy
- Neuropathic Amyloidoses, Hereditary
- Hereditary cystatin C amyloid angiopathy
- Glomerular disorder due to neuropathic heredofamilial amyloidosis
- Hereditary TTR amyloidosis
- Andrade syndrome
- Familial amyloid polyneuropathy, Iowa type
- amyloid familial polyneuropathies
- Congophilic angiopathy
- Organ limited hereditary amyloidosis
- Familial amyloid neuropathy, Andrade type
- Hereditary Neuropathic Amyloidosis
- Hereditary TTR amyloid polyneuropathy
- Familial amyloid polyneuropathy, Jewish type
- Iowa type amyloidosis
- Hereditary neuropathic amyloidosis, type I
- Localized hereditary amyloidosis
- Corino de Andrade paramyloidosis
- Amyloid polyneuropathy
- Familial amyloid polyneuropathy, Appalachian type
- Familial Amyloid Neuropathy
- Glomerular disease due to familial disease
- Familial amyloid polyneuropathy, 30 Met-for-Val
- Jewish type amyloid polyneuropathy
- Familial Amyloid Neuropathies
- Amyloid polyneuropathy type I
- Van Allen type amyloid polyneuropathy
- Hereditary transthyretin related amyloidosis
- Familial amyloid polyneuropathy type II
- Familial TTR-related amyloidosis
- Familial amyloid polyneuropathy, 84 Ser-for-Ile
- HCHWA - hereditary cerebral hemorrhage with amyloidosis
- Amyloidoses, Hereditary Neuropathic
- Hereditary cerebrovascular amyloidosis
- Neuropathy associated with dysproteinemias
- Hereditary neuropathic amyloidosis, type II
- Hereditary ATTR amyloidosis
- Polyneuropathy, Familial Amyloid
- Swedish type amyloid polyneuropathy
- Familial Amyloid Polyneuropathy
- Disorder of glomerulus due to familial disease
- Hereditary cerebral amyloid angiopathy, Icelandic type
- Portuguese polyneuritic amyloidosis
- Transthyretin-related (ATTR) familial amyloid polyneuropathy
- Hereditary cerebral hemorrhage with amyloidosis - Icelandic type
- Familial amyloid polyneuropathy, Indiana-Swiss type
- Polyneuropathy in amyloidosis
- Neuropathy, Familial Amyloid
- Neuropathic Amyloidosis, Hereditary
- Familial amyloid polyneuropathy affecting skin
- Localised hereditary amyloidosis
- ATTRv amyloidosis
- Familial amyloid polyneuropathy type III
- HCHWA - hereditary cerebral haemorrhage with amyloidosis
- Familial neuropathic amyloidosis
- Rakavina type amyloidosis
- Portuguese type amyloid polyneuropathy
- Hereditary cerebral haemorrhage with amyloidosis
- hATTR - hereditary transthyretin related amyloidosis
- Polyneuropathy due to amyloidosis
- Hereditary Neuropathic Amyloidoses
- Indiana-Maryland type amyloid polyneuropathy
- Andrade type amyloid polyneuropathy
- Familial Amyloid Polyneuropathies
- Amyloid Polyneuropathies, Familial
- Familial amyloid polyneuropathy, 60 Ala-for-Thr
- Hereditary transthyretin amyloid polyneuropathy
- Disorder of glomerulus due to familial amyloid polyneuropathy
- Neuropathies, Familial Amyloid
- AF type amyloidosis
- Hereditary amyloid polyneuropathy Portuguese type
- Familial transthyretin-related amyloidosis
- Wohlwill-Corino Andrade syndrome
- Familial amyloid neuropathy, Portuguese type
- Icelandic type amyloidosis
- CAA - Cerebral amyloid angiopathy
- Heredofamilial systemic amyloidosis affecting skin
- Familial amyloid polyneuropathy with cutaneous amyloidosis
- Familial amyloid polyneuropathy (disorder)
- German type amyloid polyneuropathy
- Swiss type amyloid polyneuropathy
- Familial amyloid polyneuropathy, type VI
- Amyloid Polyneuropathy, Familial
- Amyloid polyneuropathy (Portuguese)
- Amyloid Neuropathy, Familial
- Hereditary cerebral hemorrhage with amyloidosis
- Familial polyneuropathic amyloidosis
- Cerebral amyloid angiopathy
- Familial amyloid polyneuropathy, 33 Ile-for-Phe
- Polyneuropathies, Familial Amyloid
- Familial amyloid polyneuropathy, type II
- Amyloidosis VI
- Japanese type amyloid polyneuropathy
- Iceland type amyloidosis
Frequently Asked Questions
What is the ICD-10 code for neuropathic heredofamilial amyloidosis?
The ICD-10-CM code for neuropathic heredofamilial amyloidosis is E85.1. The full clinical description is "Neuropathic heredofamilial amyloidosis". E85.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E85.1 mean?
ICD-10-CM code E85.1 represents “Neuropathic heredofamilial amyloidosis”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E85.1 a billable code?
Yes, E85.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E85.1 in?
E85.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E85.1?
E85.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E85.1 map to?
E85.1 maps to 20 SNOMED CT concepts: 42295001, 1354544003, 193187004, 398229007, 45639009, and 15 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E85.1?
E85.1 is linked to 3 UMLS Concept Unique Identifiers: C0206245, C2874309, C4509022. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E85.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like neuropathic heredofamilial amyloidosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E85.1?
E85.1 maps to the ICD-11 code: 5D00.20 (Hereditary ATTR amyloidosis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.