E74.89

Billable

Other specified disorders of carbohydrate metabolism

Status

Billable / Specific

Chapter

4: Endocrine, Nutritional and Metabolic Diseases

Block

E70-E88

Parent Code

E74.8

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

Essential pentosuria

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

•Ehlers-Danlos syndromesQ79.6

Related Codes(2)

E74.81

Disorders of glucose transport, not elsewhere classified

E74.82

Disorders of citrate metabolism

Also Known As / Clinical Terms(581)

SNOMED CT

UMLS

Clinical Terms

Deficiency of phosphomannomutase 2
Deficiency of glycosyltransferase
Disorder of glucose metabolism
Carbohydrate deficient glycoprotein syndrome type Ix
Congenital disorder of glycosylation type In
Congenital disorder of glycosylation type IIm
Congenital disorder of glycosylation type Iy
Congenital disorder of glycosylation type Iq
Congenital disorder of glycosylation type 1p
Deficiency of glyceraldehyde-3-phosphate dehydrogenase
Deficiency of glucose oxyhydrase
Carbohydrate deficient glycoprotein syndrome type If
Deficiency of transglycosylase
Congenital myasthenia
Congenital disorder of glycosylation type Ih
Dolichyl-diphosphooligosaccharide-protein glycosyltransferase congenital disorder of glycosylation
Deficiency of beta-amylase
Carbohydrate deficient glycoprotein syndrome type V
Congenital disorder of glycosylation type 1d
Deficiency of maltose phosphorylase
Congenital disorder of glycosylation type 1cc
Deficiency of rhamnulokinase
COG1 congenital disorder of glycosylation
Deficiency of polyol dehydrogenase (NADP^+^)
Hyper-IgE syndrome
Deficiency of aldehyde reductase
Deficiency of glycosulphatase
Phosphoglucomutase deficiency
Congenital disorder of glycosylation type 1G
Xylitol dehydrogenase deficiency
CDG2M - congenital disorder of glycosylation type 2m
MOGS CDG - mannosyl-oligosaccharide glycosidase congenital disorder of glycosylation
Congenital myasthenic syndrome with ALG14-CDG (congenital disorder of glycosylation)
PENTOSURIA
Deficiency of beta-fructofuranosidase
Mannose-P-dolichol utilization defect 1
Congenital disorder of glycosylation type Ir
Deficiency of glucose-1-phosphatase
Carbohydrate deficient glycoprotein syndrome type Ir
ALG13-CDG (congenital disorder of glycosylation)
Deficiency of saccharogen amylase
Glycerol kinase deficiency
SLC35A1 (solute carrier family 35 member A1) congenital disorder of glycosylation
MPDU1-CDG - mannose-P-dolichol utilisation defect 1 - congenital disorder of glycosylation
Trehalose intolerance
Deficiency of alpha-amylase
Deficiency of amygdalase
Congenital disorder of glycosylation type IIb
ALG8 congenital disorder of glycosylation
ALG1-CDG - asparagine-linked glycosylation 1 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type IL
D-Glyceric aciduria
Deficiency of aldose 1-epimerase
Essential pentosuria
Deficiency of gluconolactonase
Magnesium transporter 1-congenital disorder of glycosylation
Deficiency of laminarinase
Deficiency of amylopectin 6-glucanohydrolase
SLC39A8-CDG - solute carrier family 39 member 8 congenital disorder of glycosylation
COG7 (component of oligomeric golgi complex 7) congenital disorder of glycosylation
MAGT1-CDG (congenital disorder of glycosylation)
Carbohydrate deficient glycoprotein syndrome type Ie
CDG2J - carbohydrate deficient glycoprotein syndrome type 2J
DDOST-CDG - dolichyl-diphosphooligosaccharide-protein glycosyltransferase congenital disorder of glycosylation
L-XYLULOSE REDUCTASE DEFICIENCY
Congenital disorder of glycosylation type 1e
GSD X - glycogen storage disease type X
Congenital disorder of glycosylation type IIh
Hyperglycerolaemia
COG8 (component of oligomeric golgi complex 8) congenital disorder of glycosylation
Component of oligomeric golgi complex 8 congenital disorder of glycosylation
CDG2I - carbohydrate deficient glycoprotein syndrome type IIi
Hyperimmunoglobulin E syndrome
Mannosyltransferase 1 deficiency
Asparagine-linked glycosylation 9 congenital disorder of glycosylation
PGM1-CDG - Phosphoglucomutase 1-related congenital disorder of glycosylation
Congenital disorder of glycosylation type IIn
MPDU1-CDG - mannose-P-dolichol utilization defect 1 - congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type IIf
Deficiency of xylulokinase
SRD5A3-CDG - steroid 5 alpha-reductase 3 congenital disorder of glycosylation
Deficiency of amylase
CMP-sialic acid transporter deficiency
Glucosyltransferase 2 deficiency
COG4 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type Id
Deficiency of phosphoglucoisomerase
CDG1CC - congenital disorder of glycosylation type 1cc
RFT1-congenital disorder of glycosylation
L-XYLULOSURIA
Congenital disorder of glycosylation type 1K
Deficiency of beta-glucuronidase
COG1 (component of oligomeric golgi complex 1) congenital disorder of glycosylation
Congenital disorder of glycosylation type 1w
Carbohydrate deficient glycoprotein syndrome type 2g
CCDC115 congenital disorder of glycosylation
Deficiency of glucose dehydrogenase
Deficiency of endo-1,3(4)-beta-glucanase
Deficiency of gentiobiase
Congenital disorder of glycosylation type 1s
Congenital disorder of glycosylation type 2h
Glycogen storage disease type X
Disorder of glucose regulation
Carbohydrate deficient glycoprotein syndrome type 2j
Deficiency of cellobiase
Pentose disorder
RFT1-CDG (congenital disorder of glycosylation)
Familial hyperglycerolaemia
Congenital disorder of glycosylation type Ix
Component of oligomeric golgi complex 5 congenital disorder of glycosylation
Deficiency of saccharase
DPM1-CDG - dolichyl-phosphate mannosyltransferase 1 catalytic subunit congenital disorder of glycosylation
Congenital disorder of glycosylation type IIi
Hyperglycerolemia
Congenital myasthenic syndrome with glycosylation defect due to ALG14 UDP-N-acetylglucosaminyltransferase subunit gene mutation
Coiled-coil domain containing 115 congenital disorder of glycosylation
Solute carrier family 35 member A2 congenital disorder of glycosylation
ALG9 congenital disorder of glycosylation
Deficiency of bisphosphoglycerate synthase
ALG3-CDG - asparagine-linked glycosylation 3 congenital disorder of glycosylation
Congenital disorder of glycosylation type 1t
Asparagine-linked glycosylation 1 congenital disorder of glycosylation
Component of oligomeric golgi complex 4 congenital disorder of glycosylation
COG4 (component of oligomeric golgi complex 4) congenital disorder of glycosylation
Deficiency of glucosamine-6-phosphate isomerase
Solute carrier family 35 member A1 congenital disorder of glycosylation
Asparagine-linked glycosylation 11 congenital disorder of glycosylation
DPAGT1-CDG - dolichyl-phosphate n-acetylglucosamine phosphotransferase congenital disorder of glycosylation
Non glucose melituria
Congenital disorder of glycosylation type 1q
Congenital disorder of glycosylation type 1x
Phosphoglucomutase-1 deficiency
Component of oligomeric golgi complex 1 congenital disorder of glycosylation
GKD - Glycerol kinase deficiency
Congenital disorder of glycosylation type 2f
Congenital disorder of glycosylation type Ij
Alpha, alpha-trehalase deficiency
PGM3-related congenital disorder of glycosylation
Congenital disorder of glycosylation type Iw
PNTSU
Trehalase deficiency
Deficiency of triosephosphate dehydrogenase
Carbohydrate deficient glycoprotein syndrome type IIe
Carbohydrate deficient glycoprotein syndrome type 1c
Deficiency of glucose oxidase
Congenital disorder of glycosylation type Icc
Disorder of glycerate metabolism
Syndrome of carbohydrate intolerance
Deficiency of glucose-6-phosphate isomerase
Mannosyltransferase 7-9 deficiency
Carbohydrate deficient glycoprotein syndrome type IIb
Congenital myasthenia syndrome
Deficiency of diphosphoglycerate mutase
Man5GlcNAc2-dolichylpyrophosphate flippase deficiency
Congenital disorder of glycosylation type 2o
Deficiency of mutarotase
Congenital disorder of glycosylation type 1r
Deficiency of oxoisomerase
Asparagine-linked glycosylation 3 congenital disorder of glycosylation
Glycogen storage disease due to phosphoglycerate kinase 1 deficiency
ALG3 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type IIg
Congenital disorder of glycosylation type Ig
Congenital disorder of glycosylation type 1f
Congenital myasthenic syndrome
Deficiency of glucokinase
Congenital disorder of glycosylation type 2m
Deficiency of protein kinase
Essential benign pentosuria
Glucosidase 1 deficiency
Deficiency of glycosidase
Deficiency of dextrin
PGM1-related congenital disorder of glycosylation
Congenital disorder of glycosylation type 1y
CCDC115-CDG - coiled-coil domain containing 115 congenital disorder of glycosylation
Deficiency of glucan 1,3-alpha-glucosidase
Asparagine-linked glycosylation 8 congenital disorder of glycosylation
Deficiency of phosphoglycerate kinase
Dolichol-phosphate-mannose synthase 1 deficiency
Congenital disorder of glycosylation type 1i
Deficiency of glycerate phosphomutase
Carbohydrate deficient glycoprotein syndrome type IIj
Deficiency of phosphohexose isomerase
Congenital disorder of glycosylation type IIo
Deficiency of amylo-1,6-glucosidase
Phosphoglucomutase 3-related congenital disorder of glycosylation
deficiency dehydrogenase xylitol
Solute carrier family 39 member 8 congenital disorder of glycosylation
Deficiency of endo-1,3-beta-glucanase
Congenital disorder of glycosylation type 2n
ALG1 congenital disorder of glycosylation
Xylosuria
Congenital disorder of glycosylation type Ip
XYLT1-CDG
Congenital disorder of glycosylation type Is
Deficiency of glucose-phosphate kinase
SLC35A1 congenital disorder of glycosylation
Muscle phosphoglycerate mutase deficiency
Deficiency of glucosyltransferase 1
Deficiency of mannokinase
Deficiency of phosphorylase b kinase
Deficiency of glucosulphatase
Deficiency of glycerol kinase
Congenital disorder of glycosylation type 1j
HIES - hyperimmunoglobulin E syndrome
SSR4-CDG - signal sequence receptor subunit 4 congenital disorder of glycosylation
Glycogenosis due to phosphoglycerate kinase 1 deficiency
Congenital disorder of glycosylation type Id
STT3B-CDG (congenital disorder of glycosylation)
CDG2G - carbohydrate deficient glycoprotein syndrome type 2G
Carbohydrate deficient glycoprotein syndrome type In
COG7 congenital disorder of glycosylation
Combined immunodeficiency due to PGM3 (phosphoglucomutase 3) deficiency
Congenital disorder of glycosylation type 1L
Familial hyperglycerolemia
Congenital disorder of glycosylation type IL
MAGT1-congenital disorder of glycosylation
Deficiency of invertase
Congenital disorder of glycosylation type 1h
Glycerol kinase deficiency - isolated
Deficiency of ALR2
GK1 deficiency
Carbohydrate deficient glycoprotein syndrome type Ij
Deficiency of 6-alpha-D-glucosidase
Carbohydrate deficient glycoprotein syndrome type Ip
Congenital disorder of glycosylation type IIg
Carbohydrate deficient glycoprotein syndrome type IIn
STT3A-CDG (congenital disorder of glycosylation)
COG8 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type IIo
ALG9-CDG - asparagine-linked glycosylation 9 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type Iy
ALG11-CDG - asparagine-linked glycosylation 11 congenital disorder of glycosylation
Deficiency of aldose mutarotase
Deficiency of beta-glucosidase
Deficiency of exo-1,3-alpha-glucanase
Deficiency of bisphosphoglycerate mutase
Congenital myasthenic syndrome with glycosylation defect due to ALG14 gene mutation
ALG12-congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type IIh
Carbohydrate deficient glycoprotein syndrome type IIi
Component of oligomeric golgi complex 7 congenital disorder of glycosylation
Congenital disorder of glycosylation type IIe
ALG8-CDG - asparagine-linked glycosylation 8 congenital disorder of glycosylation
Genetically determined myasthenia
Nonglucosuric melituria
XYLT1-CDG - xylosyltransferase 1 congenital disorder of glycosylation
SLC39A8 congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type Ik
Congenital disorder of glycosylation type 2e
Deficiency of glucosulfatase
Essential pentosuria (disorder)
COG5 (component of oligomeric golgi complex 5) congenital disorder of glycosylation
Deficiency of alpha-mannosidase
Phosphoglucomutase 1-related congenital disorder of glycosylation
Carbohydrate deficient glycoprotein syndrome type Ih
PGM3-CDG - phosphoglucomutase 3-related congenital disorder of glycosylation
Xylosyltransferase 1 congenital disorder of glycosylation
Deficiency of glycogenase
Congenital disorder of glycosylation type 1c
Deficiency of hexosephosphate isomerase
Mannosyltransferase 2 deficiency
COG5 congenital disorder of glycosylation
Congenital disorder of glycosylation type 2b
Deficiency of glycosulfatase
Disorder of glycerol metabolism
Congenital disorder of glycosylation type 1n
Deficiency of phosphoglucokinase
Deficiency of benzaldehyde dehydrogenase (nicotinamide adenine dinucleotide phosphate ^+^)
Signal sequence receptor subunit 4 congenital disorder of glycosylation
Mannosyltransferase 6 deficiency
Mannose-P-dolichol utilisation defect 1
Deficiency of gluconate 2-dehydrogenase
Congenital disorder of glycosylation type It
Deficiency of aldonolactonase
Deficiency of bisphosphoglycerate phosphatase
Deficiency of gluconokinase
Congenital disorder of glycosylation type IIf
Dolichyl-phosphate N-acetylgalactosamine phosphotransferase deficiency
SLC35A2-CDG - solute carrier family 35 member A2 congenital disorder of glycosylation
Disacchariduria
Glycerol intolerance syndrome
Mannosyl-oligosaccharide glycosidase congenital disorder of glycosylation
Deficiency of benzaldehyde dehydrogenase (NADP^+^)

Frequently Asked Questions

What is the ICD-10 code for other specified disorders of carbohydrate metabolism?

The ICD-10-CM code for other specified disorders of carbohydrate metabolism is E74.89. The full clinical description is "Other specified disorders of carbohydrate metabolism". E74.89 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E74.89 mean?

ICD-10-CM code E74.89 represents “Other specified disorders of carbohydrate metabolism”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E74.89 a billable code?

Yes, E74.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E74.89 in?

E74.89 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E74.89?

E74.89 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 7 more.

What SNOMED CT codes does E74.89 map to?

E74.89 maps to 93 SNOMED CT concepts: 720941007, 733085004, 711155008, 733451007, 720976009, and 88 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E74.89?

E74.89 is linked to 2 UMLS Concept Unique Identifiers: C0268162, C0348487. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E74.89 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other specified disorders of carbohydrate metabolism affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E74.89?

There is no direct ICD-11 mapping available for E74.89 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.