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E71.318

Billable

Other disorders of fatty-acid oxidation

Other disorders of fatty-acid oxidation

Status

Billable / Specific

Block

E70-E88

Parent Code

E71.31

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(5)
E71.310

Long chain/very long chain acyl CoA dehydrogenase deficiency

BillableE71.311

Medium chain acyl CoA dehydrogenase deficiency

BillableE71.312

Short chain acyl CoA dehydrogenase deficiency

BillableE71.313

Glutaric aciduria type II

BillableE71.314

Muscle carnitine palmitoyltransferase deficiency

Billable
Also Known As / Clinical Terms(101)

SNOMED CT

UMLS

Clinical Terms

  • Isolated long chain hydroxyacyl-CoA dehydrogenase deficiency
  • Isolated long-chain 3-keto-acyl CoA thiolase deficiency
  • Deficiency of enoyl hydrase
  • Combined deficiency of long chain 3-hydroxyacyl-coenzyme A dehydrogenase and enoyl-coenzyme A hydratase
  • 3-Ketoacyl-coenzyme A triolase deficiency
  • Deficiency of beta-keto-reductase
  • Combined long chain hydroxyacyl-coenzyme A dehydrogenase deficiency
  • Muscle form of carnitine palmitoyltransferase deficiency
  • Beta ketothiolase deficiency
  • Mitochondrial complex I deficiency due to deficiency of acyl-coenzyme A dehydrogenase 9
  • Succinyl-coenzyme A acetoacetate transferase deficiency
  • Succinyl-CoA acetoacetate transferase deficiency
  • Trifunctional protein deficiency
  • Deficiency of unsaturated acyl-CoA hydratase
  • Deficiency of 3-ketoacyl-CoA thiolase
  • Deficiency of acyl-coenzyme A dehydrogenase 9
  • CPTII - Carnitine palmitoyltransferase deficiency type II
  • Enoyl-CoA hydratase deficiency
  • Deficiency of enoyl-coenzyme A hydratase
  • Neonatal form of carnitine palmitoyltransferase II deficiency
  • CPT2 - Carnitine palmitoyltransferase II deficiency
  • Fatty acid oxidation disorder
  • LCHAD - Isolated long chain hydroxyacyl-CoA dehydrogenase deficiency
  • 3-Ketoacid CoA transferase deficiency
  • FAOD - fatty acid oxidation defect
  • ACAD9 (acyl-CoA dehydrogenase 9) deficiency
  • Combined long chain hydroxyacyl-CoA dehydrogenase deficiency
  • Deficiency of isolated LCKAT (long-chain 3-keto-acyl coenzyme A thiolase)
  • Succinyl-CoA 3-ketoacid transferase deficiency
  • Severe infantile form of carnitine palmitoyltransferase II deficiency
  • 3-Ketoacyl-CoA triolase deficiency
  • Fatty acid oxidation defect
  • Deficiency of beta-hydroxyacyl dehydrogenase
  • Human trifunctional protein deficiency
  • Deficiency of enoyl-CoA hydratase
  • Mitochondrial trifunctional protein deficiency
  • Thioacyl transferase deficiency
  • Deficiency of 2-methylbutyryl-CoA dehydrogenase
  • Deficiency of 3-hydroxyacyl-CoA dehydrogenase
  • Deficiency of acetyl-CoA acyltransferase
  • Combined deficiency of long chain 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase
  • Carnitine palmitoyltransferase II deficiency
  • Deficiency of 2-methylbutyryl-coenzyme A dehydrogenase
  • Trifunctional enzyme deficiency
  • Carnitine palmitoyltransferase deficiency
  • Deficiency of beta-ketothiolase
  • Deficiency of acetyl-coenzyme A acyltransferase
  • Acyl-CoA dehydrogenase 9 deficiency
  • Isolated deficiency of long-chain 3-keto-acyl coenzyme A thiolase
  • Carnitine palmitoyltransferase deficiency type 2
Frequently Asked Questions
What is the ICD-10 code for other disorders of fatty-acid oxidation?

The ICD-10-CM code for other disorders of fatty-acid oxidation is E71.318. The full clinical description is "Other disorders of fatty-acid oxidation". E71.318 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E71.318 mean?

ICD-10-CM code E71.318 represents “Other disorders of fatty-acid oxidation”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E71.318 a billable code?

Yes, E71.318 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E71.318 in?

E71.318 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E71.318?

E71.318 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.

What SNOMED CT codes does E71.318 map to?

E71.318 maps to 17 SNOMED CT concepts: 238004006, 307130006, 725046003, 124265004, 238002005, and 12 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E71.318?

E71.318 is linked to 1 UMLS Concept Unique Identifier: C1829846. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E71.318 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other disorders of fatty-acid oxidation affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E71.318?

There is no direct ICD-11 mapping available for E71.318 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.