E71.313
BillableGlutaric aciduria type II
Glutaric aciduria type II
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Glutaric aciduria type II A
- Glutaric aciduria type II B
- Glutaric aciduria type II C
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •peroxisomal disordersE71.5
- •Refsum's diseaseG60.1
- •Schilder's diseaseG37.0
- •glutaric aciduria (type 1) NOSE72.3
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(5)
E71.310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311Medium chain acyl CoA dehydrogenase deficiency
E71.312Short chain acyl CoA dehydrogenase deficiency
E71.314Muscle carnitine palmitoyltransferase deficiency
E71.318Other disorders of fatty-acid oxidation
Also Known As / Clinical Terms(99)
SNOMED CT
- Ethylmalonic-adipicaciduria22886006
- Glutaric acidaemia, type 222886006
- Glutaric acidemia, type 222886006
- Glutaric aciduria type II22886006
- Glutaric aciduria, type 222886006
- MAD - Multiple acyl-CoA dehydrogenase deficiency22886006
- MADD - multiple acyl-CoA dehydrogenase deficiency22886006
- Glutaric aciduria28987007
- Electron transfer flavoprotein-ubiquinone oxidoreductase deficiency1187534001
- Beta chain electron transfer flavoprotein deficiency1187541007
- Alpha chain electron transfer flavoprotein deficiency1187542000
UMLS
- Aciduria, Ethylmalonic-AdipicC0268596
- Acidurias, Ethylmalonic-AdipicC0268596
- EMAC0268596
- ETHYLMALONIC-ADIPICACIDURIAC0268596
- Electron Transfer Flavoprotein DeficiencyC0268596
- Electron transfer flavoprotein deficiencyC0268596
- Ethylmalonic Adipic AciduriaC0268596
- Ethylmalonic AdipicaciduriaC0268596
- Ethylmalonic-Adipic AciduriaC0268596
- Ethylmalonic-Adipic AciduriasC0268596
- Ethylmalonic-AdipicaciduriaC0268596
- Ethylmalonic-adipicaciduriaC0268596
- GA IIC0268596
- GA2C0268596
- GLUTARIC ACIDEMIA IIC0268596
- GLUTARIC ACIDURIA IIC0268596
- Glutaric Acidemia Type 2C0268596
- Glutaric Acidemia Type IIC0268596
- Glutaric Acidemia, Type 2C0268596
- Glutaric Aciduria IIC0268596
- Glutaric Aciduria Type 2C0268596
- Glutaric Aciduria Type IIC0268596
- Glutaric Aciduria, Type 2C0268596
- Glutaric acidaemia, type 2C0268596
- Glutaric acidemia type IIC0268596
- Glutaric acidemia, type 2C0268596
- Glutaric aciduria type IIC0268596
- Glutaric aciduria, type 2C0268596
- Glutaric aciduria, type 2 (disorder)C0268596
- MADC0268596
- MAD - Multiple acyl-CoA dehydrogenase deficiencyC0268596
- MADDC0268596
- MADD (Multiple Acyl CoA Dehydrogenase Deficiency)C0268596
- MADD (Multiple Acyl-CoA Dehydrogenase Deficiency)C0268596
- MADD - multiple acyl-CoA dehydrogenase deficiencyC0268596
- MADDs (Multiple Acyl-CoA Dehydrogenase Deficiency)C0268596
- MULTIPLE ACYL-CoA DEHYDROGENASE DEFICIENCYC0268596
- Multiple Acyl CoA Dehydrogenase DeficiencyC0268596
- Multiple Acyl Coenzyme A Dehydrogenase DeficiencyC0268596
- Multiple Acyl-CoA Dehydrogenase DeficiencyC0268596
- Multiple FAD Dehydrogenase DeficiencyC0268596
- Multiple FAD dehydrogenase deficiencyC0268596
- Multiple acyl-CoA dehydrogenase deficiencyC0268596
- Multiple acyl-coenzyme A dehydrogenase deficiencyC0268596
- emaC0268596
- glutaric acidemia type 2C0268596
- Glutaric aciduria type II AC2874240
- Glutaric aciduria type II BC2874241
- Glutaric aciduria type II CC2874242
Clinical Terms
- Ethylmalonic-adipicaciduria
- Glutaric acidemia type II
- MAD
- Ethylmalonic Adipicaciduria
- GA II
- GA2
- Glutaric aciduria type II C
- Multiple Acyl-CoA Dehydrogenase Deficiency
- MADD
- Multiple FAD dehydrogenase deficiency
- MADDs (Multiple Acyl-CoA Dehydrogenase Deficiency)
- Glutaric aciduria type II B
- glutaric acidemia type 2
- Electron transfer flavoprotein deficiency
- MADD (Multiple Acyl-CoA Dehydrogenase Deficiency)
- Electron transfer flavoprotein-ubiquinone oxidoreductase deficiency
- Acidurias, Ethylmalonic-Adipic
- Multiple Acyl Coenzyme A Dehydrogenase Deficiency
- Glutaric Aciduria, Type 2
- Multiple acyl-coenzyme A dehydrogenase deficiency
- Glutaric aciduria, type 2 (disorder)
- EMA
- Glutaric Aciduria Type 2
- Ethylmalonic-Adipic Aciduria
- MADD (Multiple Acyl CoA Dehydrogenase Deficiency)
- Alpha chain electron transfer flavoprotein deficiency
- GLUTARIC ACIDURIA II
- Glutaric acidemia, type 2
- Ethylmalonic-Adipic Acidurias
- MADD - multiple acyl-CoA dehydrogenase deficiency
- GLUTARIC ACIDEMIA II
- MAD - Multiple acyl-CoA dehydrogenase deficiency
- Glutaric aciduria type II A
- Aciduria, Ethylmalonic-Adipic
- Multiple Acyl CoA Dehydrogenase Deficiency
- Glutaric acidaemia, type 2
- Beta chain electron transfer flavoprotein deficiency
- Ethylmalonic Adipic Aciduria
- Glutaric aciduria
Frequently Asked Questions
What is the ICD-10 code for glutaric aciduria type ii?
The ICD-10-CM code for glutaric aciduria type ii is E71.313. The full clinical description is "Glutaric aciduria type II". E71.313 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.313 mean?
ICD-10-CM code E71.313 represents “Glutaric aciduria type II”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.313 a billable code?
Yes, E71.313 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.313 in?
E71.313 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.313?
E71.313 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 7 more.
What SNOMED CT codes does E71.313 map to?
E71.313 maps to 5 SNOMED CT concepts: 1187542000, 1187541007, 1187534001, 22886006, 28987007. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.313?
E71.313 is linked to 4 UMLS Concept Unique Identifiers: C0268596, C2874240, C2874241, C2874242. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E71.313 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like glutaric aciduria type ii affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E71.313?
There is no direct ICD-11 mapping available for E71.313 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.