AutoICD API

D89.82

Billable

Autoimmune lymphoproliferative syndrome [ALPS]

Autoimmune lymphoproliferative syndrome [ALPS]

Status

Billable / Specific

Block

D80-D89

Parent Code

D89.8

Coding Notes

Includes

Conditions included under this code

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(4)
D89.81

Graft-versus-host disease

D89.83

Cytokine release syndrome

D89.84

IgG4-related disease

BillableD89.89

Oth disrd involving the immune mechanism, NEC

Billable
Also Known As / Clinical Terms(74)

SNOMED CT

UMLS

Clinical Terms

  • Syndromes, Autoimmune Lymphoproliferative
  • Autoimmune lymphoproliferative syndrome due to CTLA4 haploinsufficiency
  • Syndrome, Canale-Smith
  • Canale-Smith syndrome
  • Dianzani autoimmune lymphoproliferative disease
  • Autoimmune lymphoproliferative syndrome type 4
  • Canale Smith Syndrome
  • DALD - Dianzani autoimmune lymphoproliferative disease
  • Lymphoproliferative Syndrome, Autoimmune
  • RALD - RAS-associated autoimmune leucoproliferative disease
  • autoimmune lymphoproliferative syndrome
  • STAT3-related early-onset multisystem autoimmune disease
  • ALPS - autoimmune lymphoproliferative syndrome
  • AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME, TYPE I, AUTOSOMAL DOMINANT
  • Autoimmune lymphoproliferative syndrome (disorder)
  • Syndrome, Autoimmune Lymphoproliferative
  • RAS-associated autoimmune leukoproliferative disease
  • Autoimmune lymphoproliferative syndrome with recurrent viral infection
  • Signal transducer and activator of transcription 3-related early-onset multisystem autoimmune disease
  • ALPS
  • CTLA-4 haploinsufficiency with autoimmune infiltration disease
  • Syndromes, Canale-Smith
  • Autoimmune lymphoproliferative syndrome due to cytotoxic T-lymphocyte associated protein 4 haploinsufficiency
  • RAS-associated autoimmune leucoproliferative disease
  • Canale-Smith Syndromes
  • Autoimmune Lymphoproliferative Syndromes
  • RALD - RAS-associated autoimmune leukoproliferative disease
  • Syndrome, Canale Smith
  • Caspase 8 deficiency syndrome
  • Autoimmune lymphoproliferative syndrome type IV
  • ALPS (autoimmune lymphoproliferative syndrome)
  • Lymphoproliferative Syndromes, Autoimmune
Frequently Asked Questions
What is the ICD-10 code for autoimmune lymphoproliferative syndrome [alps]?

The ICD-10-CM code for autoimmune lymphoproliferative syndrome [alps] is D89.82. The full clinical description is "Autoimmune lymphoproliferative syndrome [ALPS]". D89.82 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D89.82 mean?

ICD-10-CM code D89.82 represents “Autoimmune lymphoproliferative syndrome [ALPS]”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D89.82 a billable code?

Yes, D89.82 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D89.82 in?

D89.82 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D89.82?

D89.82 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 2 more.

What SNOMED CT codes does D89.82 map to?

D89.82 maps to 6 SNOMED CT concepts: 702444009, 1197361002, 723508002, 722290008, 721093000, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D89.82?

D89.82 is linked to 1 UMLS Concept Unique Identifier: C1328840. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D89.82 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like autoimmune lymphoproliferative syndrome [alps] affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D89.82?

There is no direct ICD-11 mapping available for D89.82 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.