D89.1
BillableCryoglobulinemia
Cryoglobulinemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Cryoglobulinemic purpura
- Cryoglobulinemic vasculitis
- Essential cryoglobulinemia
- Idiopathic cryoglobulinemia
- Mixed cryoglobulinemia
- Primary cryoglobulinemia
- Secondary cryoglobulinemia
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •transplant failure and rejectionT86
Related Codes(6)
D89.0Polyclonal hypergammaglobulinemia
D89.2Hypergammaglobulinemia, unspecified
D89.3Immune reconstitution syndrome
D89.4Mast cell activation syndrome and related disorders
D89.8Oth disrd involving the immune mechanism, NEC
D89.9Disorder involving the immune mechanism, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(162)
SNOMED CT
- Cryofibrinogenaemia10934005
- Cryofibrinogenemia10934005
- Primary cryoglobulinaemia11352009
- Primary cryoglobulinemia11352009
- Polyclonal gammopathy16618004
- Secondary cryoglobulinaemia28807005
- Secondary cryoglobulinemia28807005
- Mononeuritis multiplex30292005
- Cryoglobulinaemia30911005
- Cryoglobulinemia30911005
- Cryoimmunoglobulinaemia30911005
- Cryoimmunoglobulinemia30911005
- Mononeuritis32595002
- Monoclonal cryoimmunoglobulinaemia38675009
- Monoclonal cryoimmunoglobulinemia38675009
- Secondary cryofibrinogenaemia41816006
- Secondary cryofibrinogenemia41816006
- Mixed polyclonal cryoimmunoglobulinaemia44371002
- Mixed polyclonal cryoimmunoglobulinemia44371002
- Mixed cryoimmunoglobulinaemia with monoclonal component57390009
- Mixed cryoimmunoglobulinemia with monoclonal component57390009
- Cryoglobulinaemic purpura190814002
- Cryoglobulinemic purpura190814002
- Cryoglobulinaemic vasculitis190815001
- Cryoglobulinemic vasculitis190815001
- Neuropathy associated with dysproteinaemias230585004
- Neuropathy associated with dysproteinemias230585004
- Neuropathy in cryoglobulinaemia230589005
- Neuropathy in cryoglobulinemia230589005
- Secondary systemic vasculitis234019004
- Vasculitis caused by drug234020005
- Cryoglobulinaemic glomerulonephritis236505008
- Cryoglobulinemic glomerulonephritis236505008
- Essential cryoglobulinaemic vasculitis239947001
- Essential cryoglobulinemic vasculitis239947001
- Essential mixed cryoglobulinaemia239947001
- Essential mixed cryoglobulinemia239947001
- Necrotising cutaneous vasculitis402655006
- Necrotizing cutaneous vasculitis402655006
- Drug-induced necrotising vasculitis402659000
- Drug-induced necrotizing vasculitis402659000
- Necrotising vasculitis due to mixed cryoglobulinaemia402662002
- Necrotizing vasculitis due to mixed cryoglobulinemia402662002
- Cryofibrinogenemic purpura402853002
- Purpura due to cryofibrinogenaemia402853002
- Purpura due to cryofibrinogenemia402853002
- Peripheral neuropathy due to inflammation709145001
- Cryoglobulinaemia type 1723674005
- Cryoglobulinemia type 1723674005
- Simple cryoglobulinaemia723674005
- Simple cryoglobulinemia723674005
- Immune complex small vessel vasculitis724600007
- Small vessel vasculitis caused by immune complex724600007
- Mononeuritis multiplex due to cryoglobulinaemic vasculitis1144902007
- Mononeuritis multiplex due to cryoglobulinemic vasculitis1144902007
- Mononeuritis multiplex due to vasculitis1144906005
- Vasculitic mononeuritis multiplex1144906005
- Occlusion of microvasculature of skin caused by cryoglobulin type III1251423001
- Occlusion of microvasculature of skin caused by mixed cryoglobulin1251423001
- Cryoglobulinaemia due to chronic hepatitis C128971000119101
- Cryoglobulinemia due to chronic hepatitis C128971000119101
- Drug-induced nephritis111491000119107
- Nephritis caused by drug111491000119107
UMLS
- CryoglobulinaemiaC0010403
- CryoglobulinemiaC0010403
- Cryoglobulinemia (disorder)C0010403
- CryoglobulinemiasC0010403
- CryoimmunoglobulinaemiaC0010403
- CryoimmunoglobulinemiaC0010403
- Cryoprecipitable immune complexesC0010403
- cryoglobulinaemiaC0010403
- cryoglobulinemiaC0010403
- cryoglobulinemiasC0010403
- Cryoglobulinaemic purpuraC0340979
- Cryoglobulinemic purpuraC0340979
- Cryoglobulinemic purpura (disorder)C0340979
- Cryoglobulinaemic vasculitisC0340992
- Cryoglobulinemic vasculitisC0340992
- Cryoglobulinemic vasculitis (disorder)C0340992
- Essential cryoglobulinemiaC2873856
- Idiopathic cryoglobulinemiaC2873857
- Mixed cryoglobulinaemiaC0543697
- Mixed cryoglobulinemiaC0543697
- Primary cryoglobulinaemiaC0272258
- Primary cryoglobulinemiaC0272258
- Primary cryoglobulinemia (disorder)C0272258
- Secondary cryoglobulinaemiaC0272259
- Secondary cryoglobulinemiaC0272259
- Secondary cryoglobulinemia (disorder)C0272259
Clinical Terms
- Vasculitis caused by drug
- Essential cryoglobulinemic vasculitis
- Cryoglobulinemia type 1
- Purpura due to cryofibrinogenemia
- Vasculitic mononeuritis multiplex
- Neuropathy in cryoglobulinaemia
- Purpura due to cryofibrinogenaemia
- Small vessel vasculitis caused by immune complex
- Mononeuritis multiplex
- Necrotising cutaneous vasculitis
- Simple cryoglobulinaemia
- Cryoglobulinaemic purpura
- Cryoglobulinaemic glomerulonephritis
- Neuropathy associated with dysproteinaemias
- Drug-induced necrotizing vasculitis
- Mixed polyclonal cryoimmunoglobulinaemia
- Mononeuritis
- Secondary cryoglobulinaemia
- Essential mixed cryoglobulinaemia
- Cryoglobulinaemia type 1
- Necrotizing vasculitis due to mixed cryoglobulinemia
- Cryoglobulinemic purpura (disorder)
- Occlusion of microvasculature of skin caused by mixed cryoglobulin
- Nephritis caused by drug
- Cryoglobulinemic vasculitis (disorder)
- Primary cryoglobulinemia
- cryoglobulinaemia
- Cryoglobulinemic glomerulonephritis
- Mixed cryoimmunoglobulinaemia with monoclonal component
- Occlusion of microvasculature of skin caused by cryoglobulin type III
- Mononeuritis multiplex due to vasculitis
- Neuropathy in cryoglobulinemia
- Cryofibrinogenemia
- Secondary cryoglobulinemia
- Mixed cryoglobulinemia
- Mononeuritis multiplex due to cryoglobulinemic vasculitis
- Secondary systemic vasculitis
- Cryofibrinogenaemia
- Secondary cryofibrinogenaemia
- Neuropathy associated with dysproteinemias
- Cryoglobulinemias
- Monoclonal cryoimmunoglobulinemia
- Immune complex small vessel vasculitis
- Essential cryoglobulinaemic vasculitis
- Drug-induced necrotising vasculitis
- Cryoglobulinemia (disorder)
- Monoclonal cryoimmunoglobulinaemia
- Necrotising vasculitis due to mixed cryoglobulinaemia
- Mixed cryoimmunoglobulinemia with monoclonal component
- Necrotizing cutaneous vasculitis
- Cryoglobulinaemic vasculitis
- Mononeuritis multiplex due to cryoglobulinaemic vasculitis
- Cryoglobulinemia due to chronic hepatitis C
- Drug-induced nephritis
- Cryoglobulinemic vasculitis
- Mixed polyclonal cryoimmunoglobulinemia
- Cryoimmunoglobulinaemia
- Peripheral neuropathy due to inflammation
- Simple cryoglobulinemia
- Primary cryoglobulinaemia
- Polyclonal gammopathy
- Cryoglobulinemic purpura
- Primary cryoglobulinemia (disorder)
- Secondary cryoglobulinemia (disorder)
- Idiopathic cryoglobulinemia
- Essential mixed cryoglobulinemia
- Cryoimmunoglobulinemia
- Cryofibrinogenemic purpura
- Cryoprecipitable immune complexes
- Essential cryoglobulinemia
- Secondary cryofibrinogenemia
- Cryoglobulinaemia due to chronic hepatitis C
- Mixed cryoglobulinaemia
Frequently Asked Questions
What is the ICD-10 code for cryoglobulinemia?
The ICD-10-CM code for cryoglobulinemia is D89.1. The full clinical description is "Cryoglobulinemia". D89.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D89.1 mean?
ICD-10-CM code D89.1 represents “Cryoglobulinemia”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D89.1 a billable code?
Yes, D89.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D89.1 in?
D89.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D89.1?
D89.1 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 2 more.
What SNOMED CT codes does D89.1 map to?
D89.1 maps to 31 SNOMED CT concepts: 10934005, 402853002, 30911005, 128971000119101, 723674005, and 26 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D89.1?
D89.1 is linked to 8 UMLS Concept Unique Identifiers: C0010403, C0340979, C0340992, C2873856, C2873857, and 3 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D89.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cryoglobulinemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D89.1?
D89.1 maps to the ICD-11 code: 4B4Z (Diseases of the immune system, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.