D81.81
Non-billableBiotin-dependent carboxylase deficiency
Biotin-dependent carboxylase deficiency
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Multiple carboxylase deficiency
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Child Codes (3)
Related Codes(2)
Also Known As / Clinical Terms(23)
UMLS
- Biotin-dependent carboxylase deficiencyC1389901
- Biotin-dependent carboxylase deficiency, unspecifiedC1389901
- CARBOXYLASE DEFIC COMBINEDC0026755
- CARBOXYLASE DEFIC MULTIPLEC0026755
- COMBINED CARBOXYLASE DEFICC0026755
- Carboxylase Deficiencies, CombinedC0026755
- Carboxylase Deficiencies, MultipleC0026755
- Carboxylase Deficiency, CombinedC0026755
- Carboxylase Deficiency, MultipleC0026755
- Combined Carboxylase DeficienciesC0026755
- Combined Carboxylase DeficiencyC0026755
- DEFIC COMBINED CARBOXYLASEC0026755
- DEFIC MULTIPLE CARBOXYLASEC0026755
- Deficiencies, Combined CarboxylaseC0026755
- Deficiencies, Multiple CarboxylaseC0026755
- Deficiency, Combined CarboxylaseC0026755
- Deficiency, Multiple CarboxylaseC0026755
- MULTIPLE CARBOXYLASE DEFICC0026755
- Multiple Carboxylase DeficienciesC0026755
- Multiple Carboxylase DeficiencyC0026755
- Multiple carboxylase deficiencyC0026755
- Multiple carboxylase deficiency (disorder)C0026755
- Multiple carboxylase deficiency, unspecifiedC0026755
Frequently Asked Questions
What is the ICD-10 code for biotin-dependent carboxylase deficiency?
The ICD-10-CM code for biotin-dependent carboxylase deficiency is D81.81. The full clinical description is "Biotin-dependent carboxylase deficiency". D81.81 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code D81.81 mean?
ICD-10-CM code D81.81 represents “Biotin-dependent carboxylase deficiency”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a non-billable header code. Use a more specific child code for billing purposes.
Is D81.81 a billable code?
No, D81.81 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under D81.81.
What chapter is D81.81 in?
D81.81 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.81?
D81.81 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 2 more.
What are the subcategories under D81.81?
D81.81 has 3 child codes, including: D81.810 (Biotinidase deficiency), D81.818 (Other biotin-dependent carboxylase deficiency), D81.819 (Biotin-dependent carboxylase deficiency, unspecified).
What are the UMLS CUIs for D81.81?
D81.81 is linked to 2 UMLS Concept Unique Identifiers: C1389901, C0026755. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D81.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like biotin-dependent carboxylase deficiency affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D81.81?
There is no direct ICD-11 mapping available for D81.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.