D81.818
BillableOther biotin-dependent carboxylase deficiency
Other biotin-dependent carboxylase deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(2)
Also Known As / Clinical Terms(77)
SNOMED CT
UMLS
- Biotin-(propionyl-CoA-carboxylase) ligase deficiencyC0268581
- Biotin-(propionyl-coenzyme A-carboxylase) ligase deficiencyC0268581
- CARBOXYLASE DEFIC MULTIPLE NEONATAL FORMC0268581
- Carboxylase Deficiency, Multiple, Neonatal FormC0268581
- DEFIC HOLOCARBOXYLASE SYNTHETASEC0268581
- DEFIC MULTIPLE CARBOXYLASE NEONATAL FORMC0268581
- Deficiencies, HLCSC0268581
- Deficiencies, Holocarboxylase SynthetaseC0268581
- Deficiency, HLCSC0268581
- Deficiency, Holocarboxylase SynthetaseC0268581
- Deficiency, Multiple Carboxylase, Neonatal FormC0268581
- Early Onset Biotin Responsive Multiple Carboxylase DeficiencyC0268581
- Early Onset Combined Carboxylase DeficiencyC0268581
- Early-Onset Biotin-Responsive Multiple Carboxylase DeficiencyC0268581
- Early-Onset Combined Carboxylase DeficiencyC0268581
- Early-onset biotin-responsive multiple carboxylase deficiencyC0268581
- Early-onset combined carboxylase deficiencyC0268581
- Early-onset multiple carboxylase deficiencyC0268581
- HLCS DEFICIENCYC0268581
- HLCS DeficienciesC0268581
- HLCS DeficiencyC0268581
- HLCS deficiencyC0268581
- HOLOCARBOXYLASE SYNTHETASE DEFICC0268581
- HOLOCARBOXYLASE SYNTHETASE DEFICIENCYC0268581
- Holocarboxylase Synthetase DeficienciesC0268581
- Holocarboxylase Synthetase DeficiencyC0268581
- Holocarboxylase synthase deficiencyC0268581
- Holocarboxylase synthase deficiency (disorder)C0268581
- Holocarboxylase synthetase deficiencyC0268581
- Infantile Multiple Carboxylase DeficiencyC0268581
- Infantile multiple carboxylase deficiencyC0268581
- MULTIPLE CARBOXYLASE DEFIC NEONATAL FORMC0268581
- MULTIPLE CARBOXYLASE DEFICIENCY, EARLY ONSETC0268581
- MULTIPLE CARBOXYLASE DEFICIENCY, NEONATAL FORMC0268581
- Multiple Carboxylase DeficiencyC0268581
- Multiple Carboxylase Deficiency, Early OnsetC0268581
- Multiple Carboxylase Deficiency, Neonatal FormC0268581
- Neonatal Holocarboxylase Synthetase DeficiencyC0268581
- Neonatal Multiple Carboxylase DeficiencyC0268581
- Neonatal multiple carboxylase deficiencyC0268581
- Other biotin-dependent carboxylase deficiencyC2873845
- Other multiple carboxylase deficiencyC2873844
Clinical Terms
- HLCS deficiency
- Carboxylase Deficiency, Multiple, Neonatal Form
- Deficiency, HLCS
- Early-onset multiple carboxylase deficiency
- Early-onset biotin-responsive multiple carboxylase deficiency
- DEFIC MULTIPLE CARBOXYLASE NEONATAL FORM
- HOLOCARBOXYLASE SYNTHETASE DEFIC
- Multiple carboxylase deficiency
- Neonatal Holocarboxylase Synthetase Deficiency
- Early Onset Biotin Responsive Multiple Carboxylase Deficiency
- Biotin-(propionyl-CoA-carboxylase) ligase deficiency
- Multiple Carboxylase Deficiency, Neonatal Form
- Holocarboxylase Synthetase Deficiency
- Deficiencies, HLCS
- Early-onset combined carboxylase deficiency
- Neonatal Multiple Carboxylase Deficiency
- Deficiencies, Holocarboxylase Synthetase
- Holocarboxylase Synthetase Deficiencies
- DEFIC HOLOCARBOXYLASE SYNTHETASE
- Early Onset Combined Carboxylase Deficiency
- Deficiency, Multiple Carboxylase, Neonatal Form
- HLCS Deficiencies
- Infantile Multiple Carboxylase Deficiency
- Holocarboxylase synthase deficiency
- MULTIPLE CARBOXYLASE DEFIC NEONATAL FORM
- Deficiency, Holocarboxylase Synthetase
- Multiple Carboxylase Deficiency, Early Onset
- Other multiple carboxylase deficiency
- CARBOXYLASE DEFIC MULTIPLE NEONATAL FORM
- Holocarboxylase synthase deficiency (disorder)
- Biotin-(propionyl-coenzyme A-carboxylase) ligase deficiency
Frequently Asked Questions
What is the ICD-10 code for other biotin-dependent carboxylase deficiency?
The ICD-10-CM code for other biotin-dependent carboxylase deficiency is D81.818. The full clinical description is "Other biotin-dependent carboxylase deficiency". D81.818 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D81.818 mean?
ICD-10-CM code D81.818 represents “Other biotin-dependent carboxylase deficiency”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D81.818 a billable code?
Yes, D81.818 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.818 in?
D81.818 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.818?
D81.818 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 2 more.
What SNOMED CT codes does D81.818 map to?
D81.818 maps to 2 SNOMED CT concepts: 360369003, 1172966001. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.818?
D81.818 is linked to 3 UMLS Concept Unique Identifiers: C0268581, C2873845, C2873844. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D81.818 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other biotin-dependent carboxylase deficiency affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D81.818?
There is no direct ICD-11 mapping available for D81.818 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.