D80.1
BillableNonfamilial hypogammaglobulinemia
Nonfamilial hypogammaglobulinemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
- Common variable agammaglobulinemia [CVAgamma]
- Hypogammaglobulinemia NOS
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(9)
D80.0Hereditary hypogammaglobulinemia
D80.2Selective deficiency of immunoglobulin A [IgA]
D80.3Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4Selective deficiency of immunoglobulin M [IgM]
D80.5Immunodeficiency with increased immunoglobulin M [IgM]
D80.6Antibody defic w near-norm immunoglob or w hyperimmunoglob
D80.7Transient hypogammaglobulinemia of infancy
D80.8Other immunodeficiencies with predominantly antibody defects
D80.9Immunodeficiency with predominantly antibody defects, unsp
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(58)
SNOMED CT
- Agammaglobulinaemia119249001
- Agammaglobulinemia119249001
- Hypogammaglobulinaemia119250001
- Hypogammaglobulinemia119250001
- Chromosome 22 abnormalities with hypogammaglobulinaemia234635007
- Chromosome 22 abnormalities with hypogammaglobulinemia234635007
- Deletion of X-chromosome and hypogammaglobulinaemia234637004
- Deletion of X-chromosome and hypogammaglobulinemia234637004
- Triple X syndrome, epilepsy, and hypogammaglobulinaemia234639001
- Triple X syndrome, epilepsy, and hypogammaglobulinemia234639001
- B-lymphocyte immunodeficiency402791005
- Hypogammaglobulinaemia due to monoclonal gammopathy of undetermined significance16318061000119108
- Hypogammaglobulinemia due to monoclonal gammopathy of undetermined significance16318061000119108
- Hypogammaglobulinaemia due to multiple myeloma16318001000119107
- Hypogammaglobulinemia due to multiple myeloma16318001000119107
- Multiple myeloma with hypogammaglobulinaemia16318001000119107
- Multiple myeloma with hypogammaglobulinemia16318001000119107
UMLS
- AgammaglobulinemiaC0086438
- Decreased circulating immunoglobulin concentrationC0086438
- HypogammaglobulinaemiaC0086438
- Hypogammaglobulinaemia NOSC0086438
- Hypogammaglobulinaemia, unspecifiedC0086438
- HypogammaglobulinemiaC0086438
- Hypogammaglobulinemia (finding)C0086438
- Hypogammaglobulinemia NOSC0086438
- Hypogammaglobulinemia, unspecifiedC0086438
- HypogammaglobulinemiasC0086438
- hypogammaglobulinaemiaC0086438
- hypogammaglobulinemiaC0086438
- Agammaglobulinemia with immunoglobulin-bearing B-lymphocytesC1386923
- Common variable agammaglobulinemia [CVAgamma]C2873843
- Nonfamilial hypogammaglobulinemiaC0494250
Clinical Terms
- hypogammaglobulinemia
- Chromosome 22 abnormalities with hypogammaglobulinemia
- Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
- Hypogammaglobulinemias
- B-lymphocyte immunodeficiency
- Agammaglobulinemia
- Hypogammaglobulinemia NOS
- Hypogammaglobulinemia due to monoclonal gammopathy of undetermined significance
- Chromosome 22 abnormalities with hypogammaglobulinaemia
- Triple X syndrome, epilepsy, and hypogammaglobulinemia
- Hypogammaglobulinemia (finding)
- Hypogammaglobulinaemia due to multiple myeloma
- Hypogammaglobulinaemia NOS
- hypogammaglobulinaemia
- Triple X syndrome, epilepsy, and hypogammaglobulinaemia
- Decreased circulating immunoglobulin concentration
- Multiple myeloma with hypogammaglobulinemia
- Common variable agammaglobulinemia [CVAgamma]
- Hypogammaglobulinaemia, unspecified
- Multiple myeloma with hypogammaglobulinaemia
- Deletion of X-chromosome and hypogammaglobulinaemia
- Agammaglobulinaemia
- Hypogammaglobulinemia, unspecified
- Hypogammaglobulinemia due to multiple myeloma
- Hypogammaglobulinaemia due to monoclonal gammopathy of undetermined significance
- Deletion of X-chromosome and hypogammaglobulinemia
Frequently Asked Questions
What is the ICD-10 code for nonfamilial hypogammaglobulinemia?
The ICD-10-CM code for nonfamilial hypogammaglobulinemia is D80.1. The full clinical description is "Nonfamilial hypogammaglobulinemia". D80.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D80.1 mean?
ICD-10-CM code D80.1 represents “Nonfamilial hypogammaglobulinemia”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D80.1 a billable code?
Yes, D80.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D80.1 in?
D80.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D80.1?
D80.1 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20).
What SNOMED CT codes does D80.1 map to?
D80.1 maps to 8 SNOMED CT concepts: 119249001, 402791005, 234635007, 234637004, 119250001, and 3 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D80.1?
D80.1 is linked to 4 UMLS Concept Unique Identifiers: C0086438, C1386923, C2873843, C0494250. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D80.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like nonfamilial hypogammaglobulinemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D80.1?
D80.1 maps to the ICD-11 code: 4A01.01 (Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.