D80.5

Billable

Immunodeficiency with increased immunoglobulin M [IgM]

Immunodeficiency with increased immunoglobulin M [IgM]

Status

Billable / Specific

Block

D80-D89

Parent Code

D80

ICD-11 Mapping

1 equivalent

Coding Notes

Related Codes(9)
ICD-11 Equivalents(1)
Also Known As / Clinical Terms(103)

SNOMED CT

Clinical Terms

  • Autosomal recessive hyperimmunoglobulin M syndrome due to CTNNBL1 deficiency
  • Autosomal recessive hyperimmunoglobulin M syndrome due to UNG deficiency
  • Hyper-IgM syndrome due to uracil N-glycosylase
  • Hyper IgM syndrome due to INO80
  • Hyper-IgM syndrome type 1
  • Autosomal recessive hyper- immunoglobulin M syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to APRIL deficiency
  • Autosomal recessive activation-induced cytidine deaminase deficiency
  • Autosomal recessive hyperimmunoglobulin M syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to AID deficiency
  • Hyper-IgM syndrome due to CD40 deficiency
  • Autosomal dominant hyperimmunoglobulin M syndrome due to activation induced cytidine deaminase deficiency
  • Immunodeficiency with IgM hypergammaglobulinemia
  • Hyper-IgM syndrome due to CD40 ligand deficiency
  • Autosomal recessive combined immunodeficiency due to CD40 mutation
  • Autosomal dominant activation-induced cytidine deaminase deficiency
  • Hyperimmunoglobulin M syndrome with susceptibility to opportunistic infection
  • Hyperimmunoglobulin M syndrome without susceptibility to opportunistic infection
  • Immunodeficiency with increased immunoglobulin M
  • Autosomal dominant hyper-IgM syndrome type 2
  • Hyperimmunoglobulin M syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to mutator S homolog 6 deficiency
  • CMMR-D (constitutional mismatch repair deficiency) syndrome
  • Hyper-IgM syndrome due to UNG
  • Autosomal recessive hyperimmunoglobulin M syndrome due to uracil DNA glycosylase deficiency
  • Hyper-IgM syndrome due to CD40L deficiency
  • Constitutional mismatch repair deficiency syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to INO80 complex ATPase subunit deficiency
  • Hyper-IgM syndrome type 5
  • Hyper IgM syndrome due to MSH6
  • Autosomal recessive hyperimmunoglobulin M syndrome due to mutS homolog 6 deficiency
  • Immunodeficiency with IgM hypergammaglobulinaemia
  • X-linked hyper-immunoglobulin M syndrome
  • Hyper-IgM syndrome with susceptibility to opportunistic infections
  • Autosomal dominant hyper IgM syndrome due to AICDA
  • Autosomal recessive hyper-IgM syndrome type 2
  • HIGM3 - hyperimmunoglobulin M syndrome type 3
  • Autosomal recessive hyperimmunoglobulin M syndrome due to activation induced cytidine deaminase deficiency
  • Hyper IgM syndrome due to TNFSF13
  • Autosomal dominant hyperimmunoglobulin M syndrome due to AID deficiency
  • Hyper-IgM syndrome without susceptibility to opportunistic infections
  • Hyperimmunoglobulin M syndrome type 3
  • Autosomal recessive hyper-IgM syndrome
  • Hyper IgM syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to MSH6 deficiency
  • X-linked hyper-IgM syndrome
  • Autosomal recessive hyperimmunoglobulin M syndrome due to catenin beta like 1deficiency
  • Autosomal recessive hyper IgM syndrome due to AICDA
  • Autosomal recessive hyperimmunoglobulin M syndrome due to INO80 deficiency
  • Hyper IgM syndrome due to CTNNBL1
  • X-linked with hyper-IgM immunodeficiency
Frequently Asked Questions
What is the ICD-10 code for immunodeficiency with increased immunoglobulin m [igm]?

The ICD-10-CM code for immunodeficiency with increased immunoglobulin m [igm] is D80.5. The full clinical description is "Immunodeficiency with increased immunoglobulin M [IgM]". D80.5 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D80.5 mean?

ICD-10-CM code D80.5 represents “Immunodeficiency with increased immunoglobulin M [IgM]”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D80.5 a billable code?

Yes, D80.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D80.5 in?

D80.5 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D80.5?

D80.5 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20).

What SNOMED CT codes does D80.5 map to?

D80.5 maps to 14 SNOMED CT concepts: 1351570003, 1351572006, 1362020006, 403836001, 1351573001, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D80.5?

D80.5 is linked to 1 UMLS Concept Unique Identifier: C0740331. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D80.5 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like immunodeficiency with increased immunoglobulin m [igm] affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D80.5?

D80.5 maps to the ICD-11 code: 4A01.05 (Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.