AutoICD API

D68.2

Billable

Hereditary deficiency of other clotting factors

Hereditary deficiency of other clotting factors

Status

Billable / Specific

Block

D65-D69

Parent Code

D68

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Related Codes(8)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(481)

SNOMED CT

UMLS

Clinical Terms

  • Acquired neonatal factor II deficiency disease
  • Haemorrhagic disease of the newborn due to factor II deficiency
  • Complement factor 3i deficiency
  • Factor Five Deficiencies
  • Hypofibrinogenemia, Congenital
  • Fibrinogen Deficiency
  • Alpha chain defect dysfibrinogenemia
  • Hereditary combined coagulation factor deficiency
  • Prekallikrein deficiency
  • Hereditary dysfibrinogenemia (disorder)
  • Dysplasminogenaemia
  • Hereditary Stuart factor deficiency disease
  • Hereditary Factor V Deficiency
  • deficiency factor v
  • Deficiencies, Factor Seven
  • Prothrombin conversion accelerator deficiency
  • Parahemophilia, Owren
  • Afibrinogenemias, Familial
  • Circulating anticoagulant disorder
  • Elevated fibrinogen level
  • Factor X deficiency
  • Deficiencies, Labile Factor
  • Congenital dysfibrinogenaemia
  • Congenital afibrinogenemia (disorder)
  • Hereditary hypoprothrombinaemia
  • Autosomal dominant deficiency of profibrinolysin
  • Congenital Hypofibrinogenemia
  • Congenital Afibrinogenaemias
  • Dysfibrinogenemia
  • Dysprothrombinemia
  • parahemophilia
  • Labile Factor Deficiency
  • Platelet procoagulant activity deficiency
  • factor ii deficiency
  • factor v deficiencies
  • Hereditary Hageman factor deficiency disease
  • factor vii deficiency
  • Factor V deficiency
  • deficiency factor ii
  • F7 DEFICIENCY
  • disorder deficiency vii factor
  • Hereditary factor XIII type II deficiency
  • Contact factor deficiency
  • Hereditary dysplasminogenaemia
  • Owren Parahemophilia
  • Dysfibrinogenemia (congenital)
  • Deficiency of factor I [fibrinogen]
  • Afibrinogenemias, Congenital
  • DYSFIBRINOGENEMIA, CONGENITAL
  • Hereditary hypoproconvertinaemia
  • Factor 7 Deficiency
  • Hereditary hypoplasminogenaemia
  • Deficiency, Factor Five
  • Fibrinogen Deficiencies
  • Owren's Disease
  • Hereditary Stuart-Prower deficiency disease
  • Proaccelerin deficiency
  • Hereditary hypoproaccelerinaemia
  • Hereditary thrombophilic dysfibrinogenemia
  • Congenital Hypofibrinogenemias
  • Platelet factor V deficiency (factor V Quebec)
  • Congenital Afibrinogenemia
  • Deficiencies, Factor 7
  • Factor I deficiency disease
  • Factor XIII deficiency
  • Proconvertin deficiency
  • Familial Afibrinogenemias
  • Owren Disease
  • Stable factor deficiency
  • Hereditary factor II deficiency disease
  • Hereditary factor XIII type III deficiency
  • Factor I deficiency
  • Stuart-Prower factor deficiency
  • Deficiency of factor X [Stuart-Prower]
  • Familial afibrinogenemia
  • Heparin cofactor II deficiency
  • Hypofibrinogenemias, Congenital
  • Factor V and factor VIII combined deficiency
  • Deficiency, Factor 5
  • Hereditary combined deficiency of vitamin K-dependent clotting factors
  • Deficiency, Fibrinogen
  • Beta chain defect dysfibrinogenaemia
  • Factor XIII deficiency disease
  • Deficiency, Factor 7
  • Factor Five Deficiency
  • Deficiency, Labile Factor
  • Combined deficiency of factor V and factor VIII
  • Dysplasminogenemia
  • Factor 7 Deficiencies
  • Factor VII Deficiencies
  • Hereditary dysfibrinogenaemia
  • Factor VII deficiency (disorder)
  • Congenital hypofibrinogenemia (disorder)
  • hypoprothrombinaemia
  • Hereditary factor I deficiency disease
  • Factor V short isoforms related bleeding disorder
  • Hereditary combined deficiency of factors II, VII, IX and X
  • Hereditary factor VII deficiency syndrome
  • AFIBRINOGENEMIA, CONGENITAL
  • DEFIC FACTOR V
  • HYPOPROCONVERTINEMIA
  • Parahemophilias
  • Hereditary factor V deficiency disease (disorder)
  • Fibrinolytic bleeding syndrome
  • Fibrin stabilizing factor deficiency
  • Owrens Disease
  • Autosomal dominant deficiency of plasminogen
  • Drug-induced coagulation inhibitor disorder
  • Gamma chain defect dysfibrinogenemia
  • Acquired anticoagulants
  • Hyperfibrinogenaemia
  • Deficiency of factor VII [stable]
  • Afibrinogenaemia, Congenital
  • Fibrin stabilising factor deficiency
  • Hereditary dysplasminogenemia
  • Fitzgerald-Flaujeac-Williams-Reid trait
  • Laki-Lorand factor deficiency disease
  • Disease, Owren
  • Complete factor I deficiency
  • Deficiency factor I
  • Fibrinogen abnormality
  • Hereditary hypoprothrombinemia
  • Hyperfibrinogenemia
  • Deficiencies, Factor V
  • Congenital dysfibrinogenemia
  • Hypoproconvertinemias
  • Hereditary hypoproaccelerinemia
  • Hypofibrinogenemia
  • Hereditary dysfibrinogenemia
  • Factor XIII inhibitor disorder
  • Hereditary factor X deficiency disease
  • FACTOR VII DEFIC
  • Deficiency, Factor VII
  • Serum prothrombin conversion accelerator deficiency
  • Beta chain defect dysfibrinogenemia
  • Alpha chain defect dysfibrinogenaemia
  • Deficiency of stable factor
  • Deficiency of factor XIII [fibrin stabilizing]
  • DEFIC FACTOR VII
  • Passovoy factor deficiency
  • Congenital Fletcher factor deficiency
  • Dysfibrinogenaemia
  • Deficiency, Factor V
  • Factor II deficiency (disorder)
  • Hereditary thrombophilic dysfibrinogenaemia
  • Congenital Afibrinogenemias
  • Hypoplasminogenaemia
  • DEFIC FIBRINOGEN
  • Factor Seven Deficiencies
  • Familial multiple coagulation factor deficiency
  • Hereditary hypoproconvertinemia
  • FIBRINOGEN DEFIC
  • Hereditary factor XIII B subunit deficiency
  • F7 - Factor VII deficiency
  • Prothrombin complex deficiency
  • Disease, Owren's
  • Factor 5 Deficiencies
  • Congenital hypofibrinogenaemia
  • Hereditary hypoplasminogenemia
  • hypoprothrombinemia
  • Congenital plasminogen activator inhibitor deficiency type 1
  • Factor 10 deficiency
  • Factor XII deficiency disease
  • Acquired coagulation factor inhibitor disorder
  • Hereditary factor XIII alpha subunit deficiency
  • Hereditary factor XIII A subunit deficiency
  • Afibrinogenemia, Familial
  • Plasminogen deficiency
  • Fibrinogen deficiency (disorder)
  • Factor XII deficiency
  • Fitzgerald factor deficiency
  • Neonatal coagulation disorder
  • Prothrombin deficiency
  • Labile Factor Deficiencies
  • Hereditary factor XIII deficiency disease
  • Deficiency, Factor Seven
  • Hereditary factor VII deficiency disease
  • Hereditary factor XIII beta subunit deficiency
  • Congenital fibrinogen deficiency
  • Complement component 3 inactivator deficiency
  • Deficiency of factor XII [Hageman]
  • Factor Seven Deficiency
  • Deficiencies, Factor 5
  • Deficiencies, Factor VII
  • Hereditary congenital prekallikrein deficiency
  • Congenital fibrinogen abnormality
  • Hageman factor deficiency
  • Deficiency of factor V [labile]
  • Immunodeficiency with factor I anomaly
  • Afibrinogenaemias, Congenital
  • Hereditary factor XIII A subunit and B subunit deficiency
  • Gamma chain defect dysfibrinogenaemia
  • Hereditary dysfunctional plasminogen
  • Deficiencies, Factor Five
  • Hereditary hypofibrinogenaemia
  • Fibrinogen in blood above reference range
  • Hereditary hypofibrinogenemia
  • Hypodysfibrinogenaemia
  • Congenital Afibrinogenaemia
  • Hemorrhagic disease of the newborn due to factor II deficiency
  • FACTOR V DEFIC
  • AC globulin deficiency
  • Deficiency of factor II [prothrombin]
  • Hereditary factor V deficiency disease
  • High molecular weight kininogen deficiency
  • Fletcher trait
  • Hereditary factor XIII type I deficiency
  • Hypodysfibrinogenemia
  • Hypoplasminogenemia
  • Factor 5 Deficiency
  • Fletcher factor deficiency
  • Hereditary factor XII deficiency disease
  • Parahaemophilia
Frequently Asked Questions
What is the ICD-10 code for hereditary deficiency of other clotting factors?

The ICD-10-CM code for hereditary deficiency of other clotting factors is D68.2. The full clinical description is "Hereditary deficiency of other clotting factors". D68.2 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D68.2 mean?

ICD-10-CM code D68.2 represents “Hereditary deficiency of other clotting factors”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D68.2 a billable code?

Yes, D68.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D68.2 in?

D68.2 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D68.2?

D68.2 has Excludes1 notes indicating codes that cannot be used together with it, including: abnormal coagulation profile NOS (R79.1).

What SNOMED CT codes does D68.2 map to?

D68.2 maps to 57 SNOMED CT concepts: 88776002, 64509006, 24149006, 234459007, 95842004, and 52 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D68.2?

D68.2 is linked to 12 UMLS Concept Unique Identifiers: C0015499, C2584774, C0272350, C0015503, C4316812, and 7 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D68.2 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary deficiency of other clotting factors affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D68.2?

D68.2 maps to the ICD-11 code: 3B1Z (Congenital or constitutional haemorrhagic condition, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.