D68.1
BillableHereditary factor XI deficiency
Hereditary factor XI deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Hemophilia C
- Plasma thromboplastin antecedent [PTA] deficiency
- Rosenthal's disease
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •coagulation defects complicating abortion or ectopic or molar pregnancy,O00-O07, O08.1
- •coagulation defects complicating pregnancy, childbirth and the puerperium, , ,O45.0, O46.0, O67.0, O72.3
Related Codes(8)
D68.0Von Willebrand disease
D68.2Hereditary deficiency of other clotting factors
D68.3Hemorrhagic disorder due to circulating anticoagulants
D68.4Acquired coagulation factor deficiency
D68.5Primary thrombophilia
D68.6Other thrombophilia
D68.8Other specified coagulation defects
D68.9Coagulation defect, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(105)
SNOMED CT
- Factor XI deficiency, type II33169001
- Factor XI deficiency, type III45963004
- Congenital factor XI deficiency disease49762007
- Haemophilia C49762007
- Hemophilia C49762007
- Hereditary factor XI deficiency disease49762007
- PTA deficiency49762007
- Plasma thromboplastin antecedent deficiency49762007
- Rosenthal's disease49762007
- Thromboplastin antecedent deficiency49762007
- Factor XI deficiency, type I88540000
- Factor XI deficiency767713001
UMLS
- Congenital factor XI deficiencyC0015523
- Congenital factor XI deficiency diseaseC0015523
- DEFIC FACTOR XIC0015523
- Deficiencies, Factor 11C0015523
- Deficiencies, Factor ElevenC0015523
- Deficiencies, Factor XIC0015523
- Deficiency, Factor 11C0015523
- Deficiency, Factor ElevenC0015523
- Deficiency, Factor XIC0015523
- F11 DEFICIENCYC0015523
- F11 deficiencyC0015523
- FACTOR XI DEFICC0015523
- FACTOR XI DEFICIENCYC0015523
- Factor 11 DeficienciesC0015523
- Factor 11 DeficiencyC0015523
- Factor 11 deficiencyC0015523
- Factor Eleven DeficienciesC0015523
- Factor Eleven DeficiencyC0015523
- Factor XI DeficienciesC0015523
- Factor XI DeficiencyC0015523
- Factor XI deficiencyC0015523
- Haemophilia CC0015523
- Haemophilia C (Factor XI)C0015523
- Hemophilia CC0015523
- Hemophilia C (Factor XI)C0015523
- Hereditary Factor XI DeficiencyC0015523
- Hereditary Factor XI Deficiency DiseaseC0015523
- Hereditary factor XI deficiencyC0015523
- Hereditary factor XI deficiency diseaseC0015523
- Hereditary factor XI deficiency disease (disorder)C0015523
- PLASMA THROMBOPLASTIN ANTECEDENT DEFICIENCYC0015523
- PTA DEFICIENCYC0015523
- PTA deficiencyC0015523
- Plasma Thromboplastin Antecedent DeficiencyC0015523
- Plasma thromboplastin antecedent [PTA] deficiencyC0015523
- Plasma thromboplastin antecedent deficiencyC0015523
- ROSENTHAL SYNDROMEC0015523
- Rosenthal SyndromeC0015523
- Rosenthal SyndromesC0015523
- Rosenthal factor deficiencyC0015523
- Rosenthal syndromeC0015523
- Rosenthal's SyndromeC0015523
- Rosenthal's SyndromesC0015523
- Rosenthal's diseaseC0015523
- Rosenthals SyndromeC0015523
- Syndrome, RosenthalC0015523
- Syndrome, Rosenthal'sC0015523
- Thromboplastin antecedent deficiencyC0015523
- c hemophiliaC0015523
- factor xi deficiencyC0015523
- haemophilia cC0015523
- hemophilia cC0015523
- rosenthal syndromeC0015523
Clinical Terms
- Thromboplastin antecedent deficiency
- Congenital factor XI deficiency
- PTA DEFICIENCY
- Plasma thromboplastin antecedent deficiency
- Deficiencies, Factor Eleven
- Syndrome, Rosenthal
- F11 deficiency
- Rosenthal's disease
- Deficiencies, Factor 11
- FACTOR XI DEFICIENCY
- Rosenthal's Syndrome
- Rosenthals Syndrome
- c hemophilia
- Rosenthal Syndrome
- Rosenthal factor deficiency
- Syndrome, Rosenthal's
- Deficiencies, Factor XI
- Rosenthal Syndromes
- Plasma thromboplastin antecedent [PTA] deficiency
- Deficiency, Factor XI
- Hereditary factor XI deficiency disease
- Factor 11 Deficiency
- DEFIC FACTOR XI
- Factor Eleven Deficiencies
- Hemophilia C (Factor XI)
- Factor XI deficiency, type III
- Factor Eleven Deficiency
- Hereditary factor XI deficiency disease (disorder)
- Factor XI deficiency, type II
- haemophilia c
- Rosenthal's Syndromes
- Factor 11 Deficiencies
- Factor XI Deficiencies
- Congenital factor XI deficiency disease
- hemophilia c
- Factor XI deficiency, type I
- Deficiency, Factor Eleven
- Haemophilia C (Factor XI)
- Deficiency, Factor 11
- FACTOR XI DEFIC
Frequently Asked Questions
What is the ICD-10 code for hereditary factor xi deficiency?
The ICD-10-CM code for hereditary factor xi deficiency is D68.1. The full clinical description is "Hereditary factor XI deficiency". D68.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D68.1 mean?
ICD-10-CM code D68.1 represents “Hereditary factor XI deficiency”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D68.1 a billable code?
Yes, D68.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D68.1 in?
D68.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D68.1?
D68.1 has Excludes1 notes indicating codes that cannot be used together with it, including: abnormal coagulation profile NOS (R79.1).
What SNOMED CT codes does D68.1 map to?
D68.1 maps to 5 SNOMED CT concepts: 49762007, 767713001, 88540000, 33169001, 45963004. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D68.1?
D68.1 is linked to 1 UMLS Concept Unique Identifier: C0015523. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D68.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary factor xi deficiency affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D68.1?
D68.1 maps to the ICD-11 code: 3B13 (Haemophilia C).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.