AutoICD API

D56.0

Billable

Alpha thalassemia

Alpha thalassemia

Status

Billable / Specific

Block

D55-D59

Parent Code

D56

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Alpha thalassemia major
  • Hemoglobin H Constant Spring
  • Hemoglobin H disease
  • Hydrops fetalis due to alpha thalassemia
  • Severe alpha thalassemia
  • Triple gene defect alpha thalassemia

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Use Additional Code

Additional codes that should follow this code

Related Codes(7)
D56.1

Beta thalassemia

BillableD56.2

Delta-beta thalassemia

BillableD56.3

Thalassemia minor

BillableD56.4

Hereditary persistence of fetal hemoglobin [HPFH]

BillableD56.5

Hemoglobin E-beta thalassemia

BillableD56.8

Other thalassemias

BillableD56.9

Thalassemia, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

3A50.0ZAlpha thalassaemia, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(235)

SNOMED CT

UMLS

Clinical Terms

  • Hemoglobin S-F disease
  • Alpha thalassaemia 2
  • ALPHA-THALASSEMIA
  • Thalassemia, Alpha
  • Alpha plus thalassaemia non deletion type
  • Alpha plus thalassemia deletion type
  • Hemoglobin H Constant Spring
  • Alpha plus thalassemia
  • Hemoglobin S-S disease
  • Thalassemia-alpha
  • Haemoglobin S-S disease
  • Hb SS disease
  • Acquired hemoglobin H disease
  • Hemoglobin H constant spring thalassemia (disorder)
  • Homozygous alpha thalassaemia
  • Alpha thalassemia X-linked intellectual deficit
  • Foetus with hereditary disease
  • Hemoglobin Bart's hydrops syndrome
  • Drepanocythemia
  • Alpha-thalassaemia intellectual disability syndrome linked to chromosome 16
  • Sickle cell anemia
  • Haemoglobin Barts hydrops
  • Hb S disease
  • Alpha thalassemia syndrome
  • Alpha thalassemia intellectual disability syndrome, deletion type
  • Thalassaemia alpha
  • Microdrepanocytosis
  • Hydrops foetalis
  • Haemoglobin S-F disease
  • Homozygous alpha thalassemia
  • Sickle cell anemia with coexistent alpha-thalassemia
  • Disease, Hemoglobin H
  • Hemoglobin H constant spring thalassemia
  • Hydrops fetalis due to alpha thalassemia
  • Alpha thalassaemia 1
  • Deletion of part of short arm of chromosome 16
  • Α-thalassemia
  • alpha-Thalassemias
  • Hemoglobin H Disease
  • Sickle cell-thalassemia disease
  • Sickle cell-thalassaemia disease
  • Fetal anemia
  • Hemoglobin Bart's disease
  • Fetal hereditary disease
  • Drepanocythaemia
  • Hemoglobin Bart's hydrops syndrome (disorder)
  • Hereditary hemoglobinopathy disorder homozygous for hemoglobin S
  • Foetal anaemia
  • Sickle cell anaemia
  • Hereditary haemoglobinopathy disorder homozygous for haemoglobin S
  • Alpha thalassemia (disorder)
  • Haemoglobin Seal Rock disease
  • alpha thalassaemia
  • Alpha thalassaemia major
  • Alpha-thalassaemia
  • Alpha thalassemia X-linked intellectual disability syndrome
  • Alpha zero thalassaemia
  • Hemoglobin Bart hydrops syndrome
  • Sickle cell-haemoglobin SS disease
  • thalassemia alpha
  • Alpha plus thalassemia non deletion type
  • HEMOGLOBIN H DIS
  • Alpha thalassaemia X-linked intellectual deficit
  • Hemoglobin Seal Rock disease
  • Severe alpha thalassemia
  • Acquired haemoglobin H disease
  • Hereditary disorder of fetus
  • Microdrepanocytic disease
  • Haemoglobin Bart hydrops syndrome
  • Alpha thalassemia 1
  • Hydrops fetalis
  • Alpha thalassaemia X-linked intellectual disability syndrome
  • HF - Hydrops fetalis
  • Hemoglobin S disease
  • Sickle cell anaemia with coexistent alpha-thalassaemia
  • alpha thalassemias
  • Haemoglobin Bart's disease
  • Alpha thalassemia 2
  • Alpha thalassemia major
  • Alpha-thalassemia intellectual disability syndrome linked to chromosome 16
  • Haemoglobin H constant spring thalassaemia
  • Haemoglobin S disease
  • Thalassemia-hemoglobin S disease
  • Thalassaemia-haemoglobin S disease
  • Alpha thalassaemia intellectual disability syndrome, deletion type
  • Hemoglobin Paksé disease
  • Sickle cell thalassaemia disease
  • Sickle cell thalassemia disease
  • Triple gene defect alpha thalassemia
  • Fetus with hereditary disease
  • Haemoglobin H disease
  • ATR-16 syndrome
  • Hemoglobin Barts hydrops
  • Alpha plus thalassaemia
  • A-Thalassemia
  • Sickle cell-hemoglobin SS disease
  • Haemoglobin Bart's hydrops syndrome
  • HF - Hydrops foetalis
  • Alpha thalassaemia syndrome
  • Fetal anaemia
  • Alpha zero thalassemia
  • Haemoglobin Paksé disease
  • Alpha plus thalassaemia deletion type
Frequently Asked Questions
What is the ICD-10 code for alpha thalassemia?

The ICD-10-CM code for alpha thalassemia is D56.0. The full clinical description is "Alpha thalassemia". D56.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D56.0 mean?

ICD-10-CM code D56.0 represents “Alpha thalassemia”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D56.0 a billable code?

Yes, D56.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D56.0 in?

D56.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D56.0?

D56.0 has Excludes1 notes indicating codes that cannot be used together with it, including: sickle-cell thalassemia (D57.4-); alpha thalassemia trait or minor (D56.3); asymptomatic alpha thalassemia (D56.3); and 2 more.

Are additional codes required with D56.0?

Yes, when using D56.0, also report: code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99).

What SNOMED CT codes does D56.0 map to?

D56.0 maps to 21 SNOMED CT concepts: 734349003, 307343001, 36467003, 86242003, 85422000, and 16 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D56.0?

D56.0 is linked to 6 UMLS Concept Unique Identifiers: C0002312, C0272005, C2960096, C3161175, C2873754, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D56.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like alpha thalassemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D56.0?

D56.0 maps to the ICD-11 code: 3A50.0Z (Alpha thalassaemia, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.