D55.8
BillableOther anemias due to enzyme disorders
Other anemias due to enzyme disorders
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(5)
D55.0Anemia due to glucose-6-phosphate dehydrogenase deficiency
D55.1Anemia due to other disorders of glutathione metabolism
D55.2Anemia due to disorders of glycolytic enzymes
D55.3Anemia due to disorders of nucleotide metabolism
D55.9Anemia due to enzyme disorder, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(55)
SNOMED CT
- Adenosine deaminase superactivity5315003
- HNSHA (hereditary nonspherocytic haemolytic anaemia) due to increased adenosine deaminase activity5315003
- HNSHA (hereditary nonspherocytic hemolytic anemia) due to increased adenosine deaminase activity5315003
- Haemolytic anaemia due to erythrocyte adenosine deaminase overproduction5315003
- Hemolytic anemia due to erythrocyte adenosine deaminase overproduction5315003
- Hereditary nonspherocytic haemolytic anaemia due to increased adenosine deaminase activity5315003
- Hereditary nonspherocytic hemolytic anemia due to increased adenosine deaminase activity5315003
- Drug-induced enzyme deficiency anaemia15276008
- Drug-induced enzyme deficiency anemia15276008
- Anaemia due to pentose phosphate pathway defect29177004
- Anemia due to pentose phosphate pathway defect29177004
- HNSHA due to diphosphoglycerate mutase deficiency62268000
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to diphosphoglycerate mutase deficiency62268000
- Hereditary nonspherocytic haemolytic anaemia due to diphosphoglycerate mutase deficiency62268000
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to diphosphoglycerate mutase deficiency62268000
- Hereditary nonspherocytic hemolytic anemia due to diphosphoglycerate mutase deficiency62268000
- HNSHA due to decreased adenosine deaminase activity78908001
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to decreased adenosine deaminase activity78908001
- Hereditary nonspherocytic haemolytic anaemia due to decreased adenosine deaminase activity78908001
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to decreased adenosine deaminase activity78908001
- Hereditary nonspherocytic hemolytic anemia due to decreased adenosine deaminase activity78908001
- Anaemia due to adenosine triphosphatase deficiency725057008
- Anemia due to adenosine triphosphatase deficiency725057008
- Nonspherocytic haemolytic anaemia due to deficiency of adenosinetriphosphatase725057008
- Nonspherocytic hemolytic anemia due to deficiency of adenosinetriphosphatase725057008
- Haemolytic anaemia due to adenylate kinase deficiency766982000
- Hemolytic anemia due to adenylate kinase deficiency766982000
Clinical Terms
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to diphosphoglycerate mutase deficiency
- Hemolytic anemia due to erythrocyte adenosine deaminase overproduction
- Hereditary nonspherocytic hemolytic anemia due to decreased adenosine deaminase activity
- Hereditary nonspherocytic hemolytic anemia due to increased adenosine deaminase activity
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to diphosphoglycerate mutase deficiency
- Hereditary nonspherocytic haemolytic anaemia due to increased adenosine deaminase activity
- Haemolytic anaemia due to adenylate kinase deficiency
- Hereditary nonspherocytic hemolytic anemia due to diphosphoglycerate mutase deficiency
- Haemolytic anaemia due to erythrocyte adenosine deaminase overproduction
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to decreased adenosine deaminase activity
- Anemia due to adenosine triphosphatase deficiency
- Hereditary nonspherocytic haemolytic anaemia due to diphosphoglycerate mutase deficiency
- HNSHA (hereditary nonspherocytic hemolytic anemia) due to increased adenosine deaminase activity
- Drug-induced enzyme deficiency anaemia
- HNSHA due to decreased adenosine deaminase activity
- Drug-induced enzyme deficiency anemia
- Adenosine deaminase superactivity
- Hemolytic anemia due to adenylate kinase deficiency
- Nonspherocytic haemolytic anaemia due to deficiency of adenosinetriphosphatase
- Anemia due to pentose phosphate pathway defect
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to decreased adenosine deaminase activity
- Hereditary nonspherocytic haemolytic anaemia due to decreased adenosine deaminase activity
- Anaemia due to adenosine triphosphatase deficiency
- Nonspherocytic hemolytic anemia due to deficiency of adenosinetriphosphatase
- HNSHA due to diphosphoglycerate mutase deficiency
- HNSHA (hereditary nonspherocytic haemolytic anaemia) due to increased adenosine deaminase activity
- Anaemia due to pentose phosphate pathway defect
Frequently Asked Questions
What is the ICD-10 code for other anemias due to enzyme disorders?
The ICD-10-CM code for other anemias due to enzyme disorders is D55.8. The full clinical description is "Other anemias due to enzyme disorders". D55.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D55.8 mean?
ICD-10-CM code D55.8 represents “Other anemias due to enzyme disorders”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D55.8 a billable code?
Yes, D55.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D55.8 in?
D55.8 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D55.8?
D55.8 has Excludes1 notes indicating codes that cannot be used together with it, including: drug-induced enzyme deficiency anemia (D59.2).
What SNOMED CT codes does D55.8 map to?
D55.8 maps to 7 SNOMED CT concepts: 5315003, 725057008, 29177004, 15276008, 78908001, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D55.8?
D55.8 is linked to 1 UMLS Concept Unique Identifier: C0477305. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D55.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other anemias due to enzyme disorders affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D55.8?
D55.8 maps to the ICD-11 code: 3A10.Z (Hereditary haemolytic anaemia, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.