D55.1
BillableAnemia due to other disorders of glutathione metabolism
Anemia due to other disorders of glutathione metabolism
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
- Anemia (due to) hemolytic nonspherocytic (hereditary), type I
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(55)
SNOMED CT
- HNSHA due to gamma glutamyl cysteine synthetase deficiency25251008
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to gamma glutamyl cysteine synthetase deficiency25251008
- Hereditary nonspherocytic haemolytic anaemia due to gamma glutamyl cysteine synthetase deficiency25251008
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to gamma glutamyl cysteine synthetase deficiency25251008
- Hereditary nonspherocytic hemolytic anemia due to gamma glutamyl cysteine synthetase deficiency25251008
- Erythrocytic glutathione deficiency anaemia52212006
- Erythrocytic glutathione deficiency anemia52212006
- HNSHA due to glutathione reductase deficiency52212006
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to glutathione reductase deficiency52212006
- Hereditary nonspherocytic haemolytic anaemia due to glutathione reductase deficiency52212006
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to glutathione reductase deficiency52212006
- Hereditary nonspherocytic hemolytic anemia due to glutathione reductase deficiency52212006
- HNSHA due to glutathione synthetase deficiency111579006
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to glutathione synthetase deficiency111579006
- Hereditary nonspherocytic haemolytic anaemia due to glutathione synthetase deficiency111579006
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to glutathione synthetase deficiency111579006
- Hereditary nonspherocytic hemolytic anemia due to glutathione synthetase deficiency111579006
- Haemolytic anaemia due to glutathione metabolism disorder191170009
- Hemolytic anemia due to glutathione metabolism disorder191170009
- Congenital nonspherocytic haemolytic anaemia301317008
- Congenital nonspherocytic hemolytic anemia301317008
- HNSHA - hereditary nonspherocytic haemolytic anaemia301317008
- HNSHA - hereditary nonspherocytic hemolytic anemia301317008
- Hereditary nonspherocytic haemolytic anaemia301317008
- Hereditary nonspherocytic hemolytic anemia301317008
UMLS
Clinical Terms
- Congenital nonspherocytic hemolytic anemia
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to glutathione synthetase deficiency
- HNSHA - hereditary nonspherocytic haemolytic anaemia
- Hereditary nonspherocytic hemolytic anemia due to glutathione reductase deficiency
- Hereditary nonspherocytic hemolytic anemia
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to glutathione reductase deficiency
- Congenital nonspherocytic haemolytic anaemia
- HNSHA - hereditary nonspherocytic hemolytic anemia
- Hereditary nonspherocytic hemolytic anemia (HNSHA) due to gamma glutamyl cysteine synthetase deficiency
- Hereditary nonspherocytic hemolytic anemia due to gamma glutamyl cysteine synthetase deficiency
- Haemolytic anaemia due to glutathione metabolism disorder
- HNSHA due to glutathione reductase deficiency
- HNSHA due to glutathione synthetase deficiency
- Erythrocytic glutathione deficiency anemia
- Erythrocytic glutathione deficiency anaemia
- Hereditary nonspherocytic haemolytic anaemia due to gamma glutamyl cysteine synthetase deficiency
- Hereditary nonspherocytic hemolytic anemia due to glutathione synthetase deficiency
- Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
- Hereditary nonspherocytic haemolytic anaemia
- Anemia (due to) hemolytic nonspherocytic (hereditary), type I
- Hereditary nonspherocytic haemolytic anaemia due to glutathione reductase deficiency
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to glutathione synthetase deficiency
- HNSHA due to gamma glutamyl cysteine synthetase deficiency
- Hemolytic anemia due to glutathione metabolism disorder
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to glutathione reductase deficiency
- Hereditary nonspherocytic haemolytic anaemia (HNSHA) due to gamma glutamyl cysteine synthetase deficiency
- Hereditary nonspherocytic haemolytic anaemia due to glutathione synthetase deficiency
Frequently Asked Questions
What is the ICD-10 code for anemia due to other disorders of glutathione metabolism?
The ICD-10-CM code for anemia due to other disorders of glutathione metabolism is D55.1. The full clinical description is "Anemia due to other disorders of glutathione metabolism". D55.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D55.1 mean?
ICD-10-CM code D55.1 represents “Anemia due to other disorders of glutathione metabolism”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D55.1 a billable code?
Yes, D55.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D55.1 in?
D55.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D55.1?
D55.1 has Excludes1 notes indicating codes that cannot be used together with it, including: drug-induced enzyme deficiency anemia (D59.2).
What SNOMED CT codes does D55.1 map to?
D55.1 maps to 5 SNOMED CT concepts: 301317008, 52212006, 25251008, 111579006, 191170009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D55.1?
D55.1 is linked to 3 UMLS Concept Unique Identifiers: C2873751, C2873752, C0494224. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D55.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like anemia due to other disorders of glutathione metabolism affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D55.1?
D55.1 maps to the ICD-11 code: 3A10.0Z (Haemolytic anaemias due to hexose monophosphate shunt or glutathione metabolism anomalies, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.