Q80
Non-billableCongenital ichthyosis
Congenital ichthyosis
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Child Codes (7)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(18)
UMLS
- Congenital ichthyosisC0020758
- Congenital ichthyosis of skinC0020758
- Congenital ichthyosis of skin (disorder)C0020758
- Congenital ichthyosis, unspecifiedC0020758
- Fish scale diseaseC0020758
- Fish skinC0020758
- ICHTHYOSIS CONGENITAC0020758
- Ichthyosis CongenitaC0020758
- Ichthyosis congenitaC0020758
- Ichthyosis congenitalC0020758
- LAMELLAR EXFOLIATION OF NEWBORNC0020758
- Lamellar Exfoliation of NewbornC0020758
- Newborn Lamellar ExfoliationC0020758
- Newborn Lamellar ExfoliationsC0020758
- congenital ichthyosisC0020758
- fish skinC0020758
- ichthyosisC0020758
- ichthyosis congenitaC0020758
Frequently Asked Questions
What is the ICD-10 code for congenital ichthyosis?
The ICD-10-CM code for congenital ichthyosis is Q80. The full clinical description is "Congenital ichthyosis". Q80 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code Q80 mean?
ICD-10-CM code Q80 represents “Congenital ichthyosis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a non-billable header code. Use a more specific child code for billing purposes.
Is Q80 a billable code?
No, Q80 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 7 child codes under Q80.
What chapter is Q80 in?
Q80 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q80?
Q80 has Excludes1 notes indicating codes that cannot be used together with it, including: Refsum's disease (G60.1).
What are the subcategories under Q80?
Q80 has 7 child codes, including: Q80.0 (Ichthyosis vulgaris), Q80.1 (X-linked ichthyosis), Q80.2 (Lamellar ichthyosis), Q80.3 (Congenital bullous ichthyosiform erythroderma), and 3 more.
What are the UMLS CUIs for Q80?
Q80 is linked to 1 UMLS Concept Unique Identifier: C0020758. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q80 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital ichthyosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q80?
Q80 maps to the ICD-11 code: EC20.Y (Other specified genetic disorders of keratinisation).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.