Q80.9
BillableCongenital ichthyosis, unspecified
Congenital ichthyosis, unspecified
Status
Billable / Specific
Parent Code
Q80Coding Notes
Also Known As / Clinical Terms
SNOMED CT
- Congenital spherophakia4465002
- Spherophakia4465002
- Congenital keratoderma6874009
- XTE syndrome7037003
- Xeroderma, talipes AND enamel defect7037003
- Xeroderma, talipes and enamel defect (XTE) syndrome7037003
- Xeroderma, talipes and enamel defect syndrome7037003
- Congenital ichthyosis13059002
- Congenital ichthyosis of skin13059002
- Fish scale disease13059002
- Fish skin13059002
- Ichthyosis congenita13059002
- Keratoderma hereditarium mutilans24559001
- Mutilating keratoderma24559001
- Mutilating keratoderma of Vohwinkel24559001
- Vohwinkel syndrome24559001
- Vohwinkel's mutilating keratoderma24559001
- Congenital small lens35272001
- Microphakia35272001
- Congenital anomaly of lacrimal gland41620007
- Hypohidrosis45004005
- Hypohydrosis45004005
- Oligohidrosis45004005
- Congenital hypotrichia56558005
- Congenital hypotrichosis56558005
- Hypotrichosis congenita56558005
- Limb reduction-ichthyosis syndrome68551007
- Atresia of bile ducts77480004
- BA - Biliary atresia77480004
- Biliary atresia77480004
- Congenital biliary atresia77480004
- Absent salivary secretion87715008
- Aptyalia87715008
- Aptyalism87715008
- Asialia87715008
- Clinical xerostomia87715008
- Dry mouth87715008
- Xerostomia87715008
- Pseudo-Addison's disease91003006
- Salt-losing nephritis91003006
- Salt-losing nephropathy91003006
- Thorn's syndrome91003006
- Spastic quadriplegia192965001
- Spastic tetraplegia192965001
- Collodion baby205550003
- Lamellar ichthyosis205550003
- Ichthyosis congenita with biliary atresia235916001
- Sclerosing cholangitis235917005
- POF - Premature ovarian failure237788002
- Premature ovarian failure237788002
- Cutaneous syndrome with ichthyosis239057002
- Alacrima253215004
- Severe ichthyoses254159008
- Autosomal dominant ichthyosis402770002
- Ichthyosis, cerebellar degeneration and hepatosplenomegaly403779009
- PIBIDS syndrome, photosensitivity with IBIDS403781006
- Photosensitivity with ichthyosis, brittle hair, impaired intelligence, decreased fertility and short stature syndrome403781006
- Microspherophakia416671000
- Lentiglobus419281007
- Camisa disease717183001
- Keratoderma hereditarium mutilans with ichthyosis syndrome717183001
- Keratoderma ichthyosiform dermatosis elevated beta-glucuronidase syndrome717183001
- Vohwinkel ichthyosis syndrome717183001
- Erythrokeratodermia variabilis 3722035007
- Erythrokeratodermia variabilis Kamouraska type722035007
- Intellectual disability, enteropathy, deafness, peripheral neuropathy, ichthyosis, keratoderma syndrome722035007
- MEDNIK (mental retardation, enteropathy, deafness, peripheral neuropathy, ichtyosis, keratodermia) syndrome722035007
- MEDNIK syndrome722035007
- Osteosclerosis, ichthyosis, premature ovarian failure syndrome722114007
- Sclerosing dysplasia of bone, ichthyosis, premature ovarian failure syndrome722114007
- CEDNIK (cerebral dysgenesis, neuropathy, ichthyosis, keratoderma) syndrome722385008
- CEDNIK syndrome722385008
- Cerebral dysgenesis, neuropathy, ichthyosis, palmoplantar keratoderma syndrome722385008
- Trichothiodystrophy723551003
- Congenital ichthyosis with hypotrichosis syndrome724277002
- Ichthyosis, follicular atrophoderma, hypotrichosis syndrome724277002
- Ichthyosis, hypotrichosis, sclerosing cholangitis syndrome724278007
- NISCH (neonatal ichthyosis, sclerosing cholangitis, hypotrichosis) syndrome724278007
- NISCH syndrome724278007
- Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome724278007
- Bathing suit ichthyosis725588002
- Clayton-Smith Donnai syndrome732950006
- Ichthyosis, oral and digital anomalies syndrome732950006
- Congenital cataract ichthyosis syndrome732952003
- Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome733028000
- Ichthyosis, intellectual disability, dwarfism, renal impairment syndrome733097003
- Passwell Goodman Siprkowski syndrome733097003
- Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome763404001
- Jagell, Holmgren, Hofer syndrome763404001
- X-linked intellectual disability, hypogonadism, ichthyosis, obesity, short stature syndrome765471005
- Young Hughes syndrome765471005
- Ichthyosis782957005
- 15q26.3 microdeletion syndrome783551005
- Ichthyosis, short stature, brachydactyly, microspherophakia syndrome783551005
- Congenital ichthyosis, microcephalus, quadriplegia syndrome1197059004
- Congenital ichthyosis, microcephalus, tetraplegia syndrome1197059004
- Congenital ichthyosis, intellectual disability, spastic quadriplegia syndrome1208936008
- ELOVL4 (elongation of very long chain fatty acids-like 4) related neuro ichthyosis1208936008
- ELOVL4-related neuro ichthyosis1208936008
- HELIX (hypohidrosis, electrolyte imbalance, lacrimal gland dysfunction, ichthyosis, xerostomia) syndrome1217380005
- HELIX syndrome1217380005
- Hypohidrosis, electrolyte imbalance, lacrimal gland dysfunction, ichthyosis, xerostomia syndrome1217380005
UMLS
- Congenital ichthyosisC0020758
- Congenital ichthyosis of skinC0020758
- Congenital ichthyosis of skin (disorder)C0020758
- Congenital ichthyosis, unspecifiedC0020758
- Fish scale diseaseC0020758
- Fish skinC0020758
- ICHTHYOSIS CONGENITAC0020758
- Ichthyosis CongenitaC0020758
- Ichthyosis congenitaC0020758
- Ichthyosis congenitalC0020758
- LAMELLAR EXFOLIATION OF NEWBORNC0020758
- Lamellar Exfoliation of NewbornC0020758
- Newborn Lamellar ExfoliationC0020758
- Newborn Lamellar ExfoliationsC0020758
- congenital ichthyosisC0020758
- fish skinC0020758
- ichthyosisC0020758
- ichthyosis congenitaC0020758
Frequently Asked Questions
What is the ICD-10 code for congenital ichthyosis, unspecified?
The ICD-10-CM code for congenital ichthyosis, unspecified is Q80.9. The full clinical description is "Congenital ichthyosis, unspecified". Q80.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q80.9 mean?
ICD-10-CM code Q80.9 represents "Congenital ichthyosis, unspecified". It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q80.9 a billable code?
Yes, Q80.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q80.9 in?
Q80.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q80.9?
Q80.9 has Excludes1 notes indicating codes that cannot be used together with it, including: Refsum's disease (G60.1).
What SNOMED CT codes does Q80.9 map to?
Q80.9 maps to 45 SNOMED CT concepts: 783551005, 87715008, 253215004, 77480004, 402770002, and 40 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q80.9?
Q80.9 is linked to 1 UMLS Concept Unique Identifier: C0020758. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.