N01
Non-billableRapidly progressive nephritic syndrome
Rapidly progressive nephritic syndrome
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Includes
Conditions included under this code
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Code Also
A second code may be required; sequencing depends on circumstances
Child Codes (11)
N01.0Rapidly progr nephritic syndrome w minor glomerular abnlt
N01.1Rapidly progr neph synd w focal and seg glomerular lesions
N01.2Rapidly progr neph syndrome w diffuse membranous glomrlneph
N01.3Rapidly progr neph synd w diffus mesangial prolif glomrlneph
N01.4Rapid progr neph synd w diffus endocaplry prolif glomrlneph
N01.5Rapidly progr neph syndrome w diffuse mesangiocap glomrlneph
N01.6Rapidly progr nephritic syndrome w dense deposit disease
N01.7Rapidly progr neph syndrome w diffuse crescentic glomrlneph
N01.8Rapidly progr nephritic syndrome w oth morphologic changes
N01.9Rapidly progr nephritic syndrome w unsp morphologic changes
N01.ARapidly progressive nephritic syndrome with C3 glomrlneph
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(11)
UMLS
- Glomerulonephritis rapidly progressiveC0221239
- Glomerulonephritis, rapidly progressiveC0221239
- RPGN - Rapidly progressive glomerulonephritisC0221239
- Rapidly Progressive GlomerulonephritisC0221239
- Rapidly progressive glomerulonephritisC0221239
- Rapidly progressive glomerulonephritis (disorder)C0221239
- rapidly progressive glomerulonephritisC0221239
- Rapidly progressive nephritic syndromeC0451728
- Rapidly progressive nephritic syndrome (disorder)C0451728
- rapidly progressive glomerular diseaseC0451728
- rapidly progressive nephritisC1404822
Frequently Asked Questions
What is the ICD-10 code for rapidly progressive nephritic syndrome?
The ICD-10-CM code for rapidly progressive nephritic syndrome is N01. The full clinical description is "Rapidly progressive nephritic syndrome". N01 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code N01 mean?
ICD-10-CM code N01 represents “Rapidly progressive nephritic syndrome”. It is classified under Chapter 14: Diseases of the Genitourinary System and is a non-billable header code. Use a more specific child code for billing purposes.
Is N01 a billable code?
No, N01 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 11 child codes under N01.
What chapter is N01 in?
N01 is in Chapter 14: Diseases of the Genitourinary System (codes N00-N99).
What codes cannot be used with N01?
N01 has Excludes1 notes indicating codes that cannot be used together with it, including: hypertensive chronic kidney disease (I12.-); nephritic syndrome NOS (N05.-).
What are the subcategories under N01?
N01 has 11 child codes, including: N01.0 (Rapidly progr nephritic syndrome w minor glomerular abnlt), N01.1 (Rapidly progr neph synd w focal and seg glomerular lesions), N01.2 (Rapidly progr neph syndrome w diffuse membranous glomrlneph), N01.3 (Rapidly progr neph synd w diffus mesangial prolif glomrlneph), and 7 more.
What are the UMLS CUIs for N01?
N01 is linked to 3 UMLS Concept Unique Identifiers: C0221239, C0451728, C1404822. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does N01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like rapidly progressive nephritic syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of N01?
N01 maps to the ICD-11 code: GB40 (Nephritic syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.