G71.3
BillableMitochondrial myopathy, not elsewhere classified
Mitochondrial myopathy, not elsewhere classified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- arthrogryposis multiplex congenita (Q74.3)
- metabolic disorders (E70-E88)
- myositis (M60.-)
Also Known As / Clinical Terms
SNOMED CT
- Diabetes mellitus associated with genetic syndrome5969009
- Genetic syndromes of diabetes mellitus5969009
- Mitochondrial myopathy16851005
- Ragged red myopathy16851005
- COX - Cytochrome C oxidase deficiency67434000
- Complex IV deficiency67434000
- Cytochrome c oxidase deficiency67434000
- Cytochrome-c oxidase deficiency67434000
- Mitochondrial complex IV deficiency67434000
- Mitochondrial encephalomyopathy447292006
- Mitochondrial myoencephalopathy447292006
- Hypertrophic mitochondrial cardiomyopathy472316006
- Maternally inherited mitochondrial cardiomyopathy and myopathy472320005
- Childhood myocerebrohepatopathy spectrum702366001
- Mitochondrial DNA depletion syndrome 2 myopathic type703527003
- TK2-related mitochondrial DNA depletion myopathy703527003
- TK2-related mitochondrial DNA depletion syndrome myopathic form703527003
- TK2-related mitochondrial deoxyribonucleic acid depletion syndrome myopathic form703527003
- Congenital cataract, hypertrophic cardiomyopathy, mitochondrial myopathy syndrome717812000
- Sengers syndrome717812000
- Mitochondrial encephalocardiomyopathy due to transmembrane protein 70 mutation718212006
- TMEM70 related mitochondrial encephalo-cardio-myopathy718212006
- Mitochondrial neurogastrointestinal encephalomyopathy syndrome718214007
- Mitochondrial encephalomyopathy due to COXPD6 deficiency722212004
- Mitochondrial encephalomyopathy due to combined oxidative phosphorylation deficiency 6722212004
- Severe X-linked mitochondrial encephalomyopathy722212004
- Mitochondrial myopathy with sideroblastic anaemia syndrome724138007
- Mitochondrial myopathy with sideroblastic anemia syndrome724138007
- Myopathy, lactic acidosis and sideroblastic anaemia724138007
- Myopathy, lactic acidosis and sideroblastic anemia724138007
- Adult-onset CPEO (chronic progressive external ophthalmoplegia) with mitochondrial myopathy725464001
- Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy725464001
- Pure mitochondrial myopathy732245008
- Mitochondrial myopathy, lactic acidosis, deafness syndrome732951005
- Mitochondrial myopathy, lactic acidosis, hearing loss syndrome732951005
- Adult-onset multiple mitochondrial DNA (deoxyribonucleic acid) deletion syndrome due to DGUOK (deoxyguanosine kinase) deficiency733599009
- Adult-onset multiple mitochondrial DNA deletion syndrome due to DGUOK deficiency733599009
- Adult-onset multiple mitochondrial deoxyribonucleic acid deletion syndrome due to deoxyguanosine kinase deficiency733599009
- Mitochondrial DNA (deoxyribonucleic acid) maintenance syndrome due to MGME1 (mitochondrial genome maintenance exonuclease 1) deficiency764733009
- PEO (progressive external ophthalmoplegia) myopathy emaciation syndrome764733009
- Progressive external ophthalmoplegia, myopathy, emaciation syndrome764733009
- Mitochondrial DNA depletion syndrome 8A encephalomyopathic type with renal tubulopathy765100000
- Mitochondrial DNA depletion syndrome, encephalomyopathic form with renal tubulopathy765100000
- RRM2B-related mitochondrial DNA depletion syndrome, encephalomyopathic form with renal tubulopathy765100000
- Ribonucleotide reductase regulatory TP53 inducible subunit M2B-related mitochondrial deoxyribonucleic acid depletion syndrome encephalomyopathic form with renal tubulopathy765100000
- Mitochondrial DNA depletion syndrome encephalomyopathic form765401006
- Mitochondrial deoxyribonucleic acid depletion syndrome encephalomyopathic form765401006
- F-box and leucine rich repeat protein 4 related mitochondrial deoxyribonucleic acid depletion syndrome encephalomyopathic form765403009
- FBXL4 (F-box and leucine rich repeat protein 4) related early onset mitochondrial encephalopathy765403009
- FBXL4-related early onset mitochondrial encephalopathy765403009
- FBXL4-related encephalomyopathic mitochondrial DNA depletion syndrome765403009
- Mitochondrial DNA depletion syndrome 13 encephalomyopathic type765403009
- Lethal infantile mitochondrial disease766251006
- Lethal infantile mitochondrial myopathy766251006
- FAST kinase domains 2-related infantile mitochondrial encephalomyopathy778029000
- FASTKD2-related infantile mitochondrial encephalomyopathy778029000
- DNA replication helicase/nuclease 2-related mitochondrial deoxyribonucleic acid deletion syndrome783057002
- DNA2-related mitochondrial DNA deletion syndrome783057002
- Mitochondrial DNA deletion syndrome with limb-girdle weakness783057002
- Mitochondrial DNA deletion syndrome with progressive myopathy783057002
- Myopathy and diabetes mellitus783722008
- Benign COX (cytochrome C oxidase) deficiency784370005
- Infantile reversible cytochrome C oxidase deficiency myopathy784370005
- Mitochondrial myopathy with reversible COX (cytochrome C oxidase) deficiency784370005
- Mitochondrial myopathy with reversible complex IV deficiency784370005
- Mitochondrial myopathy with reversible cytochrome C oxidase deficiency784370005
- Reversible infantile cytochrome C oxidase deficiency784370005
- Reversible infantile respiratory chain deficiency784370005
- Maternally inherited mitochondrial myopathy1187517009
- Maternally inherited mitochondrial cardiomyopathy1187635008
- Booth Haworth Dilling syndrome1197052008
- Mitochondrial DNA depletion syndrome encephalomyopathic form with methylmalonic aciduria1197052008
- Mitochondrial deoxyribonucleic acid depletion syndrome encephalomyopathic form with methylmalonic aciduria1197052008
- Mitochondrial encephalomyopathy aminoacidopathy syndrome1197052008
- mtDNA (mitochondrial deoxyribonucleic acid) depletion syndrome encephalomyopathic form with methylmalonic aciduria1197052008
- Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies1208937004
- Mitochondrial deoxyribonucleic acid depletion syndrome, encephalomyopathic form with variable craniofacial anomalies1208937004
- mtDNA (mitochondrial deoxyribonucleic acid) depletion syndrome, encephalomyopathic form with variable craniofacial anomalies1208937004
- Autosomal dominant mitochondrial myopathy with exercise intolerance1222644009
- Mitochondrial deoxyribonucleic acid depletion syndrome myopathic form1231309005
- Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome1237514002
- Mitochondrial myopathy, cerebellar atrophy, pigmentary retinopathy syndrome1237514002
- COXPD39 - combined oxidative phosphorylation defect type 391279845005
- Combined oxidative phosphorylation defect type 391279845005
- GFM2-related combined oxidative phosphorylation defect1279845005
- GTP dependent ribosome recycling factor mitochondrial 2-related combined oxidative phosphorylation defect1279845005
- Hereditary cerebellar atrophy431641000124107
Frequently Asked Questions
What is ICD-10 code G71.3?
ICD-10-CM code G71.3 represents "Mitochondrial myopathy, not elsewhere classified". It is a billable/specific code that can be used on a claim.
Is G71.3 a billable code?
Yes, G71.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G71.3 in?
G71.3 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What codes cannot be used with G71.3?
G71.3 has Excludes1 notes indicating codes that cannot be used together with it, including: Kearns-Sayre syndrome (H49.81); Leber's disease (H47.21); Leigh's encephalopathy (G31.82); and 2 more.
What SNOMED CT codes does G71.3 map to?
G71.3 maps to 35 SNOMED CT concepts: 725464001, 733599009, 1222644009, 784370005, 1197052008, and 30 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G71.3?
G71.3 is linked to 1 UMLS Concept Unique Identifier: C0869052. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.