H49.81
Non-billableKearns-Sayre syndrome
Kearns-Sayre syndrome
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Progressive external ophthalmoplegia with pigmentary retinopathy
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
- nystagmus and other irregular eye movements (H55)
- internal ophthalmoplegia (H52.51-)
- internuclear ophthalmoplegia (H51.2-)
- progressive supranuclear ophthalmoplegia (G23.1)
Code Also
A second code may be required; sequencing depends on circumstances
- , if applicable, other manifestations, such as:
- heart block (I45.9)
Child Codes (4)
Also Known As / Clinical Terms
UMLS
- CHRONIC PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA WITH MYOPATHYC0022541
- CPEO WITH MYOPATHYC0022541
- CPEO WITH RAGGED-RED FIBERSC0022541
- CPEO with MyopathiesC0022541
- CPEO with MyopathyC0022541
- CPEO with Ragged Red FibersC0022541
- Chronic Progressive External Ophthalmoplegia with MyopathyC0022541
- Cpeo With Ragged-Red FibersC0022541
- Cytopathies, Kearns-Sayre MitochondrialC0022541
- Cytopathy, Kearn-Sayre MitochondrialC0022541
- Cytopathy, Kearns-Sayre MitochondrialC0022541
- KEARNS-SAYRE SYNDROMEC0022541
- KSSC0022541
- KSS - Kearns-Sayre syndromeC0022541
- Kearn Sayre Mitochondrial CytopathyC0022541
- Kearn SyndromeC0022541
- Kearn-Sayre Mitochondrial CytopathyC0022541
- Kearns Sayre Mitochondrial CytopathyC0022541
- Kearns Sayre Shy Daroff SyndromeC0022541
- Kearns Sayre SyndromeC0022541
- Kearns SyndromeC0022541
- Kearns' SyndromeC0022541
- Kearns-Sayre Mitochondrial CytopathiesC0022541
- Kearns-Sayre Mitochondrial CytopathyC0022541
- Kearns-Sayre SyndromeC0022541
- Kearns-Sayre mitochondrial cytopathyC0022541
- Kearns-Sayre syndromeC0022541
- Kearns-Sayre syndrome (disorder)C0022541
- Kearns-Sayre-Shy-Daroff SyndromeC0022541
- Mitochondrial Cytopathies, Kearns-SayreC0022541
- Mitochondrial Cytopathy, Kearn-SayreC0022541
- Mitochondrial Cytopathy, Kearns-SayreC0022541
- Mitochondrial ocular myopathyC0022541
- Myopathies, CPEO withC0022541
- Myopathy, CPEO withC0022541
- OCULOCRANIOSOMATIC SYNDROMEC0022541
- OPHTHALMOPLEGIA, PIGMENTARY DEGENERATION OF RETINA, AND CARDIOMYOPATHYC0022541
- OPHTHALMOPLEGIA, PROGRESSIVE EXTERNAL, WITH RAGGED-RED FIBERSC0022541
- OPHTHALMOPLEGIA-PLUS SYNDROMEC0022541
- Oculocraniosomatic SyndromeC0022541
- Oculocraniosomatic SyndromesC0022541
- Oculocraniosomatic syndromeC0022541
- Ophthalmoplegia Plus SyndromeC0022541
- Ophthalmoplegia Plus SyndromesC0022541
- Ophthalmoplegia plus syndromeC0022541
- Ophthalmoplegia plus syndrome (disorder)C0022541
- Ophthalmoplegia, Pigmentary Degeneration of Retina, and CardiomyopathyC0022541
- Ophthalmoplegia, Progressive External, With Ragged-Red FibersC0022541
- Ophthalmoplegia-Plus SyndromeC0022541
- Ophthalmoplegia-Plus SyndromesC0022541
- Sayre Syndrome, KearnsC0022541
- Syndrome, KearnsC0022541
- Syndrome, Kearns SayreC0022541
- Syndrome, Kearns'C0022541
- Syndrome, Kearns-SayreC0022541
- Syndrome, Kearns-Sayre-Shy-DaroffC0022541
- Syndrome, OculocraniosomaticC0022541
- Syndrome, Ophthalmoplegia PlusC0022541
- Syndrome, Ophthalmoplegia-PlusC0022541
- Syndromes, Ophthalmoplegia-PlusC0022541
- kearn sayer syndromeC0022541
- kearn sayers syndromeC0022541
- kearn sayre syndromeC0022541
- kearns sayer syndromeC0022541
- kearns sayers syndromeC0022541
- kearns sayre syndromeC0022541
- kearns syndromeC0022541
- kearns-sayer syndromeC0022541
- kearns-sayre syndromeC0022541
- Progressive external ophthalmoplegia with pigmentary retinopathyC2881300
Frequently Asked Questions
What is the ICD-10 code for kearns-sayre syndrome?
The ICD-10-CM code for kearns-sayre syndrome is H49.81. The full clinical description is "Kearns-Sayre syndrome". H49.81 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code H49.81 mean?
ICD-10-CM code H49.81 represents "Kearns-Sayre syndrome". It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a non-billable header code. Use a more specific child code for billing purposes.
Is H49.81 a billable code?
No, H49.81 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 4 child codes under H49.81.
What chapter is H49.81 in?
H49.81 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What are the subcategories under H49.81?
H49.81 has 4 child codes, including: H49.811 (Kearns-Sayre syndrome, right eye), H49.812 (Kearns-Sayre syndrome, left eye), H49.813 (Kearns-Sayre syndrome, bilateral), H49.819 (Kearns-Sayre syndrome, unspecified eye).
What are the UMLS CUIs for H49.81?
H49.81 is linked to 2 UMLS Concept Unique Identifiers: C0022541, C2881300. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.