E88.40
BillableMitochondrial metabolism disorder, unspecified
Mitochondrial metabolism disorder, unspecified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- histiocytosis X (chronic) (C96.6)
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Use Additional Code
Additional codes that should follow this code
- codes for associated conditions
Also Known As / Clinical Terms
SNOMED CT
- Mitochondrial cytopathy240096000
- Mitochondrial disease240096000
- Hypertrophic mitochondrial cardiomyopathy472316006
- Demyelination of central nervous system co-occurrent and due to mitochondrial disease724784006
- Demyelination of central nervous system with mitochondrial disorder724784006
- Liver disease co-occurrent and due to mitochondrial disorder735732003
- Liver disease with mitochondrial disorder735732003
- Combined oxidative phosphorylation defect type 16771513008
- Infantile hypertrophic cardiomyopathy due to MRPL44 deficiency771513008
- Infantile hypertrophic cardiomyopathy due to mitochondrial ribosomal protein L44 deficiency771513008
- Dilated cardiomyopathy due to mitochondrial disease871639003
- Disorder of glomerulus due to mitochondrial cytopathy1148867008
- Glomerular disease due to mitochondrial cytopathy1148867008
- Non-syndromic mitochondrial sensorineural deafness1187512003
- Chorea due to mitochondrial cytopathy1259609008
- Chorea due to metabolic disorder1259619002
- Dystonia due to mitochondrial cytopathy1260365000
- Dystonia due to mitochondrial disease1260365000
- Myoclonic disorder due to mitochondrial cytopathy1263505003
- Myoclonic disorder due to mitochondrial disorder1263505003
- Mitochondrial metabolism defect133791000119107
Frequently Asked Questions
What is the ICD-10 code for mitochondrial metabolism disorder, unspecified?
The ICD-10-CM code for mitochondrial metabolism disorder, unspecified is E88.40. The full clinical description is "Mitochondrial metabolism disorder, unspecified". E88.40 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E88.40 mean?
ICD-10-CM code E88.40 represents "Mitochondrial metabolism disorder, unspecified". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E88.40 a billable code?
Yes, E88.40 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E88.40 in?
E88.40 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E88.40?
E88.40 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 10 more.
Are additional codes required with E88.40?
Yes, when using E88.40 you should also code: codes for associated conditions.
What SNOMED CT codes does E88.40 map to?
E88.40 maps to 13 SNOMED CT concepts: 1259619002, 1259609008, 771513008, 724784006, 871639003, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E88.40?
E88.40 is linked to 1 UMLS Concept Unique Identifier: C1456275. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.