AutoICD API

E71

Non-billable

Disord of branched-chain amino-acid metab & fatty-acid metab

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

This is a header/category code. For billing purposes, use a more specific child code from the list below.

Status

Non-billable / Header

Block

E70-E88

Child Codes

6

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes 2

Conditions not included here, but the patient may have both

  • Ehlers-Danlos syndromes (Q79.6-)

Child Codes (6)

E71.0

Maple-syrup-urine disease

BillableE71.1

Other disorders of branched-chain amino-acid metabolism

E71.2

Disorder of branched-chain amino-acid metabolism, unsp

BillableE71.3

Disorders of fatty-acid metabolism

E71.4

Disorders of carnitine metabolism

E71.5

Peroxisomal disorders

Also Known As / Clinical Terms

UMLS

Frequently Asked Questions

What is ICD-10 code E71?

ICD-10-CM code E71 represents "Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism". It is a non-billable header code — use a more specific child code for billing purposes.

Is E71 a billable code?

No, E71 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 6 child codes under E71.

What chapter is E71 in?

E71 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E71?

E71 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What are the subcategories under E71?

E71 has 6 child codes, including: E71.0 (Maple-syrup-urine disease), E71.1 (Other disorders of branched-chain amino-acid metabolism), E71.2 (Disorder of branched-chain amino-acid metabolism, unsp), E71.3 (Disorders of fatty-acid metabolism), and 2 more.

What are the UMLS CUIs for E71?

E71 is linked to 1 UMLS Concept Unique Identifier: C0494332. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.