E71
Non-billableDisord of branched-chain amino-acid metab & fatty-acid metab
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Child Codes (6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(2)
Frequently Asked Questions
What is the ICD-10 code for disord of branched-chain amino-acid metab & fatty-acid metab?
The ICD-10-CM code for disord of branched-chain amino-acid metab & fatty-acid metab is E71. The full clinical description is "Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism". E71 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code E71 mean?
ICD-10-CM code E71 represents “Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is E71 a billable code?
No, E71 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 6 child codes under E71.
What chapter is E71 in?
E71 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71?
E71 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What are the subcategories under E71?
E71 has 6 child codes, including: E71.0 (Maple-syrup-urine disease), E71.1 (Other disorders of branched-chain amino-acid metabolism), E71.2 (Disorder of branched-chain amino-acid metabolism, unsp), E71.3 (Disorders of fatty-acid metabolism), and 2 more.
What are the UMLS CUIs for E71?
E71 is linked to 1 UMLS Concept Unique Identifier: C0494332. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E71 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like disord of branched-chain amino-acid metab & fatty-acid metab affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E71?
E71 maps to the ICD-11 code: 5C50.Z (Inborn errors of amino acid or other organic acid metabolism, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.