D66
BillableHereditary factor VIII deficiency
Hereditary factor VIII deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Classical hemophilia
- Deficiency factor VIII (with functional defect)
- Hemophilia NOS
- Hemophilia A
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(265)
SNOMED CT
- Factor V deficiency4320005
- Severe haemophilia A16872008
- Severe hemophilia A16872008
- Severe hereditary factor VIII deficiency disease16872008
- Mild haemophilia A26029002
- Mild hemophilia A26029002
- Mild hereditary factor VIII deficiency disease26029002
- AHG deficiency disease28293008
- Classical haemophilia28293008
- Classical hemophilia28293008
- Congenital factor VIII deficiency28293008
- Congenital factor VIII deficiency disease28293008
- Haemophilia A28293008
- Hemophilia A28293008
- Hereditary factor VIII deficiency disease28293008
- Sex-linked factor VIII deficiency28293008
- Moderate haemophilia A33344008
- Moderate hemophilia A33344008
- Moderate hereditary factor VIII deficiency disease33344008
- Haemophilia90935002
- Hemophilia90935002
- Collodion baby205550003
- Lamellar ichthyosis205550003
- Factor VIII deficiency234440005
- Haemophilia A with inhibitor234442002
- Hemophilia A with inhibitor234442002
- Hereditary factor VIII deficiency disease with inhibitor234442002
- Mild haemophilia A with inhibitor425949001
- Mild hemophilia A with inhibitor425949001
- Mild hereditary factor VIII deficiency disease with inhibitor425949001
- Haemophilia A without inhibitor438360006
- Hemophilia A without inhibitor438360006
- Hereditary factor VIII deficiency disease without inhibitor438360006
- Severe haemophilia A with inhibitor438373005
- Severe hemophilia A with inhibitor438373005
- Severe hereditary factor VIII deficiency disease with inhibitor438373005
- Moderate haemophilia A with inhibitor438599002
- Moderate hemophilia A with inhibitor438599002
- Moderate hereditary factor VIII deficiency disease with inhibitor438599002
- Hereditary combined coagulation factor deficiency439157002
- Mild haemophilia A without inhibitor440820004
- Mild hemophilia A without inhibitor440820004
- Mild hereditary factor VIII deficiency disease without inhibitor440820004
- Severe haemophilia A without inhibitor440993008
- Severe hemophilia A without inhibitor440993008
- Severe hereditary factor VIII deficiency disease without inhibitor440993008
- Moderate haemophilia A without inhibitor441006000
- Moderate hemophilia A without inhibitor441006000
- Moderate hereditary factor VIII deficiency disease without inhibitor441006000
- Combined deficiency of factor V and factor VIII715559004
- Factor V and factor VIII combined deficiency715559004
- Familial multiple coagulation factor deficiency715559004
- Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome733028000
- Mild hereditary factor VIII deficiency disease with high response inhibitor1285655009
- Mild hereditary factor VIII deficiency disease with low response inhibitor1285656005
- Severe hereditary factor VIII deficiency disease with high response inhibitor1285657001
- Severe hereditary factor VIII deficiency disease with low response inhibitor1285658006
- Moderate hereditary factor VIII deficiency disease with high response inhibitor1285659003
- Moderate hereditary factor VIII deficiency disease with low response inhibitor1285660008
- Disorder of bilateral ankle joints due to hemophilia911781000124102
- Hemophilic arthropathy of bilateral ankles911781000124102
- Hemophilic arthropathy of both ankles911781000124102
- Disorder of bilateral elbow joints due to hemophilia911771000124100
- Hemophilic arthropathy of bilateral elbows911771000124100
- Hemophilic arthropathy of both elbows911771000124100
- Disorder of bilateral hip joints due to hemophilia911811000124100
- Hemophilic arthropathy of bilateral hips911811000124100
- Hemophilic arthropathy of both hips911811000124100
- Disorder of bilateral knee joints due to hemophilia911801000124103
- Hemophilic arthropathy of bilateral knees911801000124103
- Hemophilic arthropathy of both knees911801000124103
- Disorder of bilateral shoulder joints due to hemophilia911821000124108
- Hemophilic arthropathy of bilateral shoulders911821000124108
- Hemophilic arthropathy of both shoulders911821000124108
- Disorder of bilateral wrist joints due to hemophilia911791000124104
- Hemophilic arthropathy of bilateral wrists911791000124104
- Hemophilic arthropathy of both wrists911791000124104
- Disorder of joint of left ankle due to hemophilia711451000124109
- Hemophilic arthropathy of left ankle711451000124109
- Disorder of joint of left elbow due to hemophilia711341000124104
- Hemophilic arthropathy of left elbow711341000124104
- Disorder of joint of left hip due to hemophilia711391000124108
- Hemophilic arthropathy of left hip711391000124108
- Disorder of joint of left knee due to hemophilia711411000124108
- Hemophilic arthropathy of left knee711411000124108
- Disorder of joint of left shoulder due to hemophilia711431000124102
- Hemophilic arthropathy of left shoulder711431000124102
- Disorder of joint of left wrist due to hemophilia711371000124107
- Hemophilic arthropathy of left wrist711371000124107
- Disorder of joint of right ankle due to hemophilia711441000124107
- Hemophilic arthropathy of right ankle711441000124107
- Disorder of joint of right elbow due to hemophilia711351000124102
- Hemophilic arthropathy of right elbow711351000124102
- Disorder of joint of right hip due to hemophilia711381000124105
- Hemophilic arthropathy of right hip711381000124105
- Disorder of joint of right knee due to hemophilia711401000124105
- Hemophilic arthropathy of right knee711401000124105
- Disorder of joint of right shoulder due to hemophilia711421000124100
- Hemophilic arthropathy of right shoulder711421000124100
- Disorder of joint of right wrist due to hemophilia711361000124100
- Hemophilic arthropathy of right wrist711361000124100
UMLS
- AHG deficiency diseaseC0019069
- Classic HemophiliaC0019069
- Classic HemophiliasC0019069
- Classical haemophiliaC0019069
- Classical hemophiliaC0019069
- Congenital Hemophilia AC0019069
- Congenital Hemophilia AsC0019069
- Congenital factor VIII deficiencyC0019069
- Congenital factor VIII deficiency diseaseC0019069
- Congenital factor VIII disorderC0019069
- HEMAC0019069
- HEMOPHILIA AC0019069
- HEMOPHILIA, CLASSICC0019069
- HaemophiliaC0019069
- Haemophilia AC0019069
- Haemophilia A (Factor VIII)C0019069
- HemophiliaC0019069
- Hemophilia AC0019069
- Hemophilia A (Factor VIII)C0019069
- Hemophilia A, CongenitalC0019069
- Hemophilia AsC0019069
- Hemophilia As, CongenitalC0019069
- Hemophilia, ClassicC0019069
- Hemophilias, ClassicC0019069
- Hereditary Factor VIII DeficiencyC0019069
- Hereditary factor VIII deficiencyC0019069
- Hereditary factor VIII deficiency diseaseC0019069
- Hereditary factor VIII deficiency disease (disorder)C0019069
- Sex-linked factor VIII deficiencyC0019069
- congenital factor viii disorderC0019069
- factor viii hemophiliaC0019069
- haemophilia aC0019069
- hemophilia AC0019069
- hemophilia aC0019069
- Deficiency factor VIII (with functional defect)C2873783
- Haemophilia NOSC0684275
- Hemophilia (disorder)C0684275
- Hemophilia NOSC0684275
- haemophiliaC0684275
- hemophiliaC0684275
- hemophilia disorderC0684275
- hemophiliasC0684275
Clinical Terms
- Hemophilic arthropathy of left hip
- Severe hereditary factor VIII deficiency disease with high response inhibitor
- Disorder of joint of right elbow due to hemophilia
- HEMOPHILIA, CLASSIC
- Collodion baby
- Severe hereditary factor VIII deficiency disease without inhibitor
- Hereditary combined coagulation factor deficiency
- Congenital factor VIII disorder
- hemophilia a
- Deficiency factor VIII (with functional defect)
- Mild haemophilia A
- Severe haemophilia A
- Moderate hemophilia A without inhibitor
- Moderate hemophilia A with inhibitor
- AHG deficiency disease
- Mild hereditary factor VIII deficiency disease with low response inhibitor
- Hemophilic arthropathy of bilateral shoulders
- Hereditary factor VIII deficiency disease without inhibitor
- Disorder of bilateral hip joints due to hemophilia
- Haemophilia A
- Moderate hereditary factor VIII deficiency disease with high response inhibitor
- Congenital factor VIII deficiency disease
- Factor V deficiency
- Hemophilic arthropathy of left knee
- HEMA
- Hemophilia (disorder)
- Haemophilia NOS
- Disorder of joint of left wrist due to hemophilia
- Hemophilic arthropathy of both elbows
- Hereditary factor VIII deficiency disease
- Mild hemophilia A
- Disorder of bilateral knee joints due to hemophilia
- Severe hemophilia A with inhibitor
- Hemophilic arthropathy of left wrist
- Haemophilia
- Hemophilic arthropathy of left ankle
- Classical hemophilia
- Hemophilia As
- Congenital factor VIII deficiency
- Disorder of joint of left hip due to hemophilia
- Factor VIII deficiency
- Mild haemophilia A with inhibitor
- Mild hemophilia A without inhibitor
- Severe hereditary factor VIII deficiency disease with low response inhibitor
- Factor V and factor VIII combined deficiency
- Hemophilic arthropathy of bilateral elbows
- Moderate hemophilia A
- Congenital Hemophilia As
- Combined deficiency of factor V and factor VIII
- Mild hereditary factor VIII deficiency disease with inhibitor
- factor viii hemophilia
- Congenital Hemophilia A
- Hemophilia A (Factor VIII)
- Haemophilia A (Factor VIII)
- Haemophilia A with inhibitor
- Hemophilic arthropathy of right shoulder
- Severe haemophilia A without inhibitor
- Hereditary factor VIII deficiency disease with inhibitor
- Disorder of bilateral elbow joints due to hemophilia
- Disorder of joint of right ankle due to hemophilia
- Mild hereditary factor VIII deficiency disease with high response inhibitor
- Moderate hereditary factor VIII deficiency disease with low response inhibitor
- Classical haemophilia
- Hemophilia
- Mild hereditary factor VIII deficiency disease
- Severe hemophilia A
- Disorder of joint of left knee due to hemophilia
- Moderate haemophilia A
- Hemophilic arthropathy of bilateral knees
- Classic Hemophilias
- Hemophilic arthropathy of both knees
- Familial multiple coagulation factor deficiency
- Hemophilic arthropathy of bilateral hips
- Disorder of joint of left ankle due to hemophilia
- Hemophilic arthropathy of both wrists
- Hemophilias, Classic
- Hemophilic arthropathy of right ankle
- Moderate haemophilia A without inhibitor
- Moderate haemophilia A with inhibitor
- hemophilias
- Hereditary factor VIII deficiency disease (disorder)
- Lamellar ichthyosis
- Severe hereditary factor VIII deficiency disease with inhibitor
- Disorder of bilateral shoulder joints due to hemophilia
- Mild haemophilia A without inhibitor
- Haemophilia A without inhibitor
- Hemophilic arthropathy of both shoulders
- Hemophilia A with inhibitor
- Hemophilic arthropathy of right elbow
- Hemophilic arthropathy of bilateral wrists
- Severe hereditary factor VIII deficiency disease
- Hemophilia A without inhibitor
- Disorder of joint of right hip due to hemophilia
- Moderate hereditary factor VIII deficiency disease without inhibitor
- Disorder of joint of left shoulder due to hemophilia
- Hemophilic arthropathy of both hips
- Disorder of bilateral ankle joints due to hemophilia
- Disorder of bilateral wrist joints due to hemophilia
- Sex-linked factor VIII deficiency
- Mild hereditary factor VIII deficiency disease without inhibitor
- Hemophilic arthropathy of bilateral ankles
- hemophilia disorder
- Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome
- Severe haemophilia A with inhibitor
- Hemophilic arthropathy of right knee
- Disorder of joint of right wrist due to hemophilia
- Hemophilic arthropathy of left shoulder
- Hemophilia A, Congenital
- Moderate hereditary factor VIII deficiency disease with inhibitor
- Disorder of joint of right shoulder due to hemophilia
- Hemophilic arthropathy of both ankles
- Disorder of joint of right knee due to hemophilia
- Mild hemophilia A with inhibitor
- Hemophilia As, Congenital
- Disorder of joint of left elbow due to hemophilia
- Hemophilic arthropathy of right hip
- Hemophilic arthropathy of left elbow
- Severe hemophilia A without inhibitor
- Hemophilic arthropathy of right wrist
- Classic Hemophilia
- Hemophilia NOS
- Moderate hereditary factor VIII deficiency disease
Frequently Asked Questions
What is the ICD-10 code for hereditary factor viii deficiency?
The ICD-10-CM code for hereditary factor viii deficiency is D66. The full clinical description is "Hereditary factor VIII deficiency". D66 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D66 mean?
ICD-10-CM code D66 represents “Hereditary factor VIII deficiency”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D66 a billable code?
Yes, D66 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D66 in?
D66 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D66?
D66 has Excludes1 notes indicating codes that cannot be used together with it, including: factor VIII deficiency with vascular defect (D68.0-).
What SNOMED CT codes does D66 map to?
D66 maps to 43 SNOMED CT concepts: 28293008, 205550003, 715559004, 911781000124102, 911771000124100, and 38 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D66?
D66 is linked to 3 UMLS Concept Unique Identifiers: C0019069, C2873783, C0684275. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D66 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary factor viii deficiency affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D66?
D66 maps to the ICD-11 code: 3B10.Z (Hereditary factor VIII deficiency, unspecified).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.