Q85.9

Billable

Phakomatosis, unspecified

Phakomatosis, unspecified

Status

Billable / Specific

Parent Code

Q85

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Hamartosis NOS

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(3)
Q85.0

Neurofibromatosis (nonmalignant)

Q85.1

Tuberous sclerosis

BillableQ85.8

Other phakomatoses, not elsewhere classified

ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LD2D.ZPhakomatoses or hamartoneoplastic syndromes, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(150)

SNOMED CT

UMLS

Clinical Terms

  • Neurocutaneous Syndrome
  • Hamartoma
  • Hamartosis NOS
  • Hamartomatous disease
  • Bilateral congenital hamartoma of irises
  • Linear basal cell nevus
  • Heart defect, tongue hamartoma, polysyndactyly syndrome
  • Portwine naevus
  • Congenital hamartoma of bilateral irises
  • Paving stone nevus
  • Congenital hamartoma of left iris
  • Port-wine stain of skin
  • Congenital hamartoma of right iris
  • Naevus flammeus
  • Hamartomatosis
  • Brunner gland hamartoma of duodenum
  • Port-wine stain in proteus syndrome
  • Hamartoma of Brunner gland of duodenum
  • Connective tissue hamartoma of skin
  • Ostravik Lindemann Solberg syndrome
  • Port-wine nevus
  • Proteus syndrome
  • hamartoses
  • Connective tissue nevus
  • Neuroectodermal Dysplasia Syndrome
  • Port-wine naevus
  • Port wine stain of skin
  • Neurocutaneous Syndromes
  • Phakomatoses
  • Linear basal cell naevus
  • Portwine nevus
  • Connective tissue naevus
  • Congenital hamartoma of iris of left eye
  • Syndromes, Neuroectodermal Dysplasia
  • NEUROCUTANEOUS DIS
  • Syndrome, Neuroectodermal Dysplasia
  • PWS - Port-wine stain
  • Dermal connective tissue hamartoma
  • Hamartoma of duodenal gland
  • Syndromes, Neurocutaneous
  • Neurocutaneous syndrome (disorder)
  • Glycosaminoglycans nevus
  • Neuroectodermal Dysplasia Syndromes
  • Connective tissue nevus of skin
  • Phacomatoses
  • Congenital hamartosis
  • Congenital hamartoma of iris
  • Congenital hamartoma
  • Hamartoma of intestine
  • hamartosis
  • Hamartoma of tongue
  • Congenital hamartoma of iris of right eye
  • Paving stone naevus
  • Neurocutaneous Disorder
  • Congenital hamartoma of both irises
  • Neuroectodermal dysplasia
  • Neurocutaneous Disorders
  • Port-wine stain
  • Glycosaminoglycans naevus
  • Congenital hamartoma of skin
  • Connective tissue naevus of skin
  • Phacomatosis
  • Neoplasm and/or hamartoma
  • Syndrome, Neurocutaneous
  • Hamartoma of small intestine
  • Nevus flammeus
  • Port-wine birthmark
  • Neuro-Oculo-Cutaneous Syndrome
Frequently Asked Questions
What is the ICD-10 code for phakomatosis, unspecified?

The ICD-10-CM code for phakomatosis, unspecified is Q85.9. The full clinical description is "Phakomatosis, unspecified". Q85.9 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q85.9 mean?

ICD-10-CM code Q85.9 represents “Phakomatosis, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q85.9 a billable code?

Yes, Q85.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q85.9 in?

Q85.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q85.9?

Q85.9 has Excludes1 notes indicating codes that cannot be used together with it, including: ataxia telangiectasia [Louis-Bar] (G11.3); familial dysautonomia [Riley-Day] (G90.1).

What SNOMED CT codes does Q85.9 map to?

Q85.9 maps to 20 SNOMED CT concepts: 16064571000119103, 1197705006, 399960008, 16064531000119101, 16064611000119107, and 15 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q85.9?

Q85.9 is linked to 2 UMLS Concept Unique Identifiers: C0265315, C0265316. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q85.9 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like phakomatosis, unspecified affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q85.9?

Q85.9 maps to the ICD-11 code: LD2D.Z (Phakomatoses or hamartoneoplastic syndromes, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.