Q84.8
BillableOther specified congenital malformations of integument
Other specified congenital malformations of integument
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Aplasia cutis congenita
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q84.0Congenital alopecia
Q84.1Congenital morphological disturbances of hair, NEC
Q84.2Other congenital malformations of hair
Q84.3Anonychia
Q84.4Congenital leukonychia
Q84.5Enlarged and hypertrophic nails
Q84.6Other congenital malformations of nails
Q84.9Congenital malformation of integument, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(152)
SNOMED CT
- Adams-Oliver syndrome34748004
- Congenital absence of skin on scalp with limb-reduction anomaly34748004
- Type 2 aplasia cutis34748004
- ACC - Aplasia cutis congenita35484002
- Aplasia cutis congenita35484002
- Congenital absence of skin35484002
- Cutis aplasia35484002
- Epitheliogenesis imperfecta35484002
- Intestinal lymphangiectasia197260007
- Intestinal lymphangiectasis197260007
- Aplasia of skin254237003
- Congenital anomaly of lymphatic structure of trunk363031002
- Congenital sequelae of disorders363042006
- Hereditary disorder of lymphatic system363190001
- Sequelae of reproductive disorders363305005
- Aplasia cutis congenita due to underlying malformation (Type 4)403548007
- Aplasia cutis congenita associated with fetus papyraceus (Type 5)403549004
- Aplasia cutis congenita associated with foetus papyraceus (Type 5)403549004
- Aplasia cutis congenita in association with epidermolysis bullosa (Type 6)403550004
- Aplasia cutis congenita due to teratogenic drug (Type 7)403551000
- Aplasia cutis congenita following intra-uterine infection (Type 8)403552007
- Aplasia cutis congenita secondary to malformation syndrome (Type 9)403553002
- Delleman-Oorthuys syndrome403554008
- Oculocerebrocutaneous syndrome403554008
- Aplasia cutis in Trisomy 13 syndrome403756008
- Aplasia cutis in Chromosome 4 short-arm deletion syndrome (Wolf-Hirschhorn)403757004
- Aplasia cutis in Johanson-Blizzard syndrome403763008
- Naevus sebaceous707136009
- Naevus sebaceous of Jadassohn707136009
- Nevus sebaceous707136009
- Nevus sebaceous of Jadassohn707136009
- Organoid naevus707136009
- Organoid nevus707136009
- Sebaceous naevus707136009
- Sebaceous nevus707136009
- Aplasia cutis with myopia syndrome720499004
- Gershoni Baruch Leibo syndrome720499004
- Aplasia cutis congenita with intestinal lymphangiectasia syndrome720500008
- Bronspiegel Zelnick syndrome720500008
- Autosomal recessive aplasia cutis congenita of limb723500009
- Recessive aplasia cutis congenita of limbs723500009
- Aplasia cutis congenita with epibulbar dermoid syndrome723554006
- Oculoectodermal syndrome723554006
- Toriello Lacassie Droste syndrome723554006
- SCALP syndrome774208009
- Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome774208009
- Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome774208009
- Aplasia cutis congenita, naevus sebaceous syndrome774209001
- Aplasia cutis congenita, nevus sebaceous syndrome774209001
- Didymosis aplasticosebacea774209001
- Congenital lymphangiectases788292004
- Congenital lymphangiectasia788292004
- Congenital lymphangiectasis788292004
- Dermoid cyst of eye proper830036006
- Aplasia cutis congenita of limb838362006
- Microphthalmos due to Delleman syndrome1003369001
- Aplasia cutis congenita of trunk1144556009
- Aplasia of skin of trunk1144556009
- Aplasia of sudoriferous gland1144873002
- Aplasia of sweat gland1144873002
- Aplasia of eccrine gland1144874008
UMLS
- ACCC0282160
- ACC - Aplasia cutis congenitaC0282160
- APLASIA CUTIS CONGENITA, NONSYNDROMICC0282160
- Absence of part of skin at birthC0282160
- Aplasia Cutis CongenitaC0282160
- Aplasia Cutis Congenita, NonsyndromicC0282160
- Aplasia cutisC0282160
- Aplasia cutis congenitaC0282160
- Aplasia cutis congenita (disorder)C0282160
- Aplasia of skinC0282160
- Aplasia of skin (disorder)C0282160
- Congenital absence of skinC0282160
- Cutis aplasiaC0282160
- Epitheliogenesis imperfectaC0282160
- aplasia congenita cutisC0282160
- aplasia cutisC0282160
- aplasia cutis congenitaC0282160
- congenita aplasia cutiC0282160
- cuti aplasiaC0282160
- cutis aplasiaC0282160
- Other specified congenital malformations of integumentC0478090
Clinical Terms
- Aplasia of skin of trunk
- Sebaceous naevus
- Aplasia of sweat gland
- Absence of part of skin at birth
- Gershoni Baruch Leibo syndrome
- Sequelae of reproductive disorders
- Aplasia of skin
- Aplasia of skin (disorder)
- Naevus sebaceous of Jadassohn
- Congenital lymphangiectasis
- Aplasia cutis in Johanson-Blizzard syndrome
- ACC - Aplasia cutis congenita
- Aplasia cutis congenita secondary to malformation syndrome (Type 9)
- Aplasia cutis congenita
- aplasia congenita cutis
- Aplasia cutis congenita associated with fetus papyraceus (Type 5)
- Aplasia cutis congenita in association with epidermolysis bullosa (Type 6)
- Congenital anomaly of lymphatic structure of trunk
- cutis aplasia
- SCALP syndrome
- ACC
- Aplasia cutis in Trisomy 13 syndrome
- Oculoectodermal syndrome
- Aplasia cutis congenita (disorder)
- APLASIA CUTIS CONGENITA, NONSYNDROMIC
- Autosomal recessive aplasia cutis congenita of limb
- Intestinal lymphangiectasia
- aplasia cutis
- congenita aplasia cuti
- Aplasia cutis congenita due to underlying malformation (Type 4)
- Aplasia cutis congenita with intestinal lymphangiectasia syndrome
- Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome
- cuti aplasia
- Aplasia cutis congenita, naevus sebaceous syndrome
- Nevus sebaceous
- Hereditary disorder of lymphatic system
- Aplasia cutis congenita due to teratogenic drug (Type 7)
- Aplasia cutis congenita of trunk
- Congenital lymphangiectasia
- Aplasia of sudoriferous gland
- Type 2 aplasia cutis
- Congenital sequelae of disorders
- Congenital absence of skin
- Congenital absence of skin on scalp with limb-reduction anomaly
- Congenital lymphangiectases
- Didymosis aplasticosebacea
- Sebaceous nevus
- Microphthalmos due to Delleman syndrome
- Delleman-Oorthuys syndrome
- Aplasia cutis with myopia syndrome
- Aplasia cutis congenita of limb
- Aplasia cutis congenita with epibulbar dermoid syndrome
- Aplasia cutis congenita associated with foetus papyraceus (Type 5)
- Aplasia of eccrine gland
- Epitheliogenesis imperfecta
- Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome
- Intestinal lymphangiectasis
- Oculocerebrocutaneous syndrome
- Aplasia cutis in Chromosome 4 short-arm deletion syndrome (Wolf-Hirschhorn)
- Organoid naevus
- Adams-Oliver syndrome
- Bronspiegel Zelnick syndrome
- Nevus sebaceous of Jadassohn
- Aplasia cutis congenita, nevus sebaceous syndrome
- Recessive aplasia cutis congenita of limbs
- Dermoid cyst of eye proper
- Toriello Lacassie Droste syndrome
- Aplasia cutis congenita following intra-uterine infection (Type 8)
- Naevus sebaceous
- Organoid nevus
Frequently Asked Questions
What is the ICD-10 code for other specified congenital malformations of integument?
The ICD-10-CM code for other specified congenital malformations of integument is Q84.8. The full clinical description is "Other specified congenital malformations of integument". Q84.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q84.8 mean?
ICD-10-CM code Q84.8 represents “Other specified congenital malformations of integument”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q84.8 a billable code?
Yes, Q84.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q84.8 in?
Q84.8 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q84.8 map to?
Q84.8 maps to 32 SNOMED CT concepts: 35484002, 34748004, 403549004, 403551000, 403548007, and 27 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q84.8?
Q84.8 is linked to 2 UMLS Concept Unique Identifiers: C0282160, C0478090. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q84.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other specified congenital malformations of integument affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q84.8?
Q84.8 maps to the ICD-11 code: LC7Z (Structural developmental anomalies of the skin, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.