Q84.0
BillableCongenital alopecia
Congenital alopecia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital atrichosis
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q84.1Congenital morphological disturbances of hair, NEC
Q84.2Other congenital malformations of hair
Q84.3Anonychia
Q84.4Congenital leukonychia
Q84.5Enlarged and hypertrophic nails
Q84.6Other congenital malformations of nails
Q84.8Other specified congenital malformations of integument
Q84.9Congenital malformation of integument, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(268)
SNOMED CT
- Congenital alopecia2965006
- Congenital atrichosis2965006
- Naevoid congenital alopecia2965006
- Nevoid congenital alopecia2965006
- KP - Keratosis pilaris5132005
- Keratosis pilaris5132005
- Acroosteolysis27201004
- Congenital hypotrichia56558005
- Congenital hypotrichosis56558005
- Hypotrichosis congenita56558005
- Cutis laxa, autosomal recessive59451000
- Alopecia universalis86166000
- Universal alopecia areata86166000
- Frontonasal dysplasia sequence86610004
- Median cleft face syndrome86610004
- False anodontia109440005
- Congenital retrognathism109515000
- Retrognathia109515000
- Retrognathism109515000
- Collodion baby205550003
- Lamellar ichthyosis205550003
- Congenital localised alopecia205592008
- Congenital localized alopecia205592008
- Tooth absent234948008
- Tooth missing234948008
- Sclerosing cholangitis235917005
- Odonto-onychial dysplasia with alopecia239019002
- Dwarfism, alopecia, pseudoanodontia, cutis laxa239025003
- ANOTHER (alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy, respiratory tract infection) syndrome239050000
- ANOTHER syndrome239050000
- Alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy and respiratory tract infections239050000
- Hypohidrotic ectodermal dysplasia, hypothyroidism, ciliary dyskinesia syndrome239050000
- Cutaneous syndrome with ichthyosis239057002
- Hereditary acroosteolysis254148004
- Congenital alopecia with keratin cysts254225000
- Hypotrichosis with keratosis pilaris and lentiginosis254227008
- Marie Unna congenital hypotrichosis254234005
- Marie Unna hereditary hypotrichosis254234005
- Marie Unna syndrome254234005
- Congenital generalised alopecia268288009
- Congenital generalized alopecia268288009
- Recession of bone298358008
- Vertical alopecia403533001
- Sutural alopecia403534007
- Triangular alopecia403535008
- IFAP - ichthyosis follicularis with alopecia and photophobia403782004
- Ichthyosis follicularis with alopecia and photophobia403782004
- Ichthyosis follicularis with alopecia and photophobia (IFAP)403782004
- Atrichia congenita403798006
- Periodontitis associated with genetic disorder710903001
- Periodontitis co-occurrent with genetic disorder710903001
- Atrichia with papular lesions715963002
- Autosomal recessive palmoplantar keratoderma and congenital alopecia Wallis type719104003
- Autosomal recessive palmoplantar keratoderma and congenital alopecia syndrome719104003
- Autosomal dominant palmoplantar keratoderma and congenital alopecia719518004
- Palmoplantar keratoderma and congenital alopecia Stevanovic type719518004
- Taurodontia with absent teeth and sparse hair syndrome719945007
- Alymphoid cystic thymic dysgenesis720345008
- Congenital alopecia and nail dystrophy with severe functional T-cell immunodeficiency720345008
- Pignata Guarino syndrome720345008
- Severe T-cell immunodeficiency, congenital alopecia, nail dystrophy syndrome720345008
- T-cell immunodeficiency, congenital alopecia, and nail dystrophy720345008
- Winged helix deficiency720345008
- Choroidal atrophy and alopecia syndrome720850008
- Moloney syndrome720850008
- Regional choroidal atrophy and alopecia720850008
- ACD (alopecia, contracture, dwarfism) mental retardation syndrome720979002
- ACD (alopecia, contracture, dwarfism) syndrome720979002
- Alopecia, contracture, dwarfism, intellectual disability syndrome720979002
- Alopecia, psychomotor epilepsy, periodontal pyorrhea, intellectual disability syndrome720980004
- Alopecia, psychomotor epilepsy, periodontal pyorrhoea, intellectual disability syndrome720980004
- Shokeir syndrome720980004
- Alopecia and intellectual disability with hypergonadotropic hypogonadism syndrome720981000
- Devriendt Vandenberghe Fryns syndrome720981000
- GAPO (growth retardation, alopecia, pseudoanodontia, optic atrophy) syndrome721843003
- GAPO syndrome721843003
- Growth retardation, alopecia, pseudoanodontia, optic atrophy syndrome721843003
- HLTRS (hypotrichosis, lymphedema, telangiectasia, renal defect) syndrome723363009
- HLTRS (hypotrichosis, lymphoedema, telangiectasia, renal defect) syndrome723363009
- Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome723363009
- Hypotrichosis, lymphoedema, telangiectasia, renal defect syndrome723363009
- HJMD (hypotrichosis, juvenile macular degeneration) syndrome723364003
- Hypotrichosis with juvenile macular degeneration syndrome723364003
- Hypotrichosis and intellectual disability syndrome Lopes type723365002
- Lopes Marques de Faria syndrome723365002
- MACS (macrocephaly, alopecia, cutis laxa, scoliosis) syndrome723367005
- MACS syndrome723367005
- Macrocephaly, alopecia, cutis laxa, scoliosis syndrome723367005
- RIN2 deficiency723367005
- Tall forehead, sparse hair, skin hyperextensibility, scoliosis syndrome723367005
- Congenital ichthyosis with hypotrichosis syndrome724277002
- Ichthyosis, follicular atrophoderma, hypotrichosis syndrome724277002
- Ichthyosis, hypotrichosis, sclerosing cholangitis syndrome724278007
- NISCH (neonatal ichthyosis, sclerosing cholangitis, hypotrichosis) syndrome724278007
- NISCH syndrome724278007
- Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome724278007
- ALX4 (human aristaless-like 4) related frontonasal dysplasia with alopecia and genital anomaly725029001
- Craniofrontonasal dysplasia with alopecia and hypogonadism725029001
- Frontonasal dysplasia with alopecia and genital abnomality725029001
- Frontonasal dysplasia with alopecia and genital anomaly syndrome725029001
- Developmental anomaly of periodontal tissue737265006
- Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome763404001
- Jagell, Holmgren, Hofer syndrome763404001
- HOPP syndrome763658004
- Hypotrichosis, osteolysis, periodontitis, palmoplantar keratoderma syndrome763658004
- Odonto onycho dysplasia with alopecia syndrome763828007
- Odonto-onycho dysplasia alopecia syndrome763828007
- ANE (alopecia, progressive neurological defect, endocrinopathy) syndrome770941005
- ANE syndrome770941005
- Alopecia, progressive neurological defect, endocrinopathy syndrome770941005
- Sparse hair, short stature, skin anomalies syndrome771182002
- Thumb deformity, alopecia, pigmentation anomaly syndrome771182002
- PARC (poikiloderma, alopecia, retrognathism, cleft palate) syndrome771186004
- PARC syndrome771186004
- Poikiloderma, alopecia, retrognathism, cleft palate syndrome771186004
- Spondyloepimetaphyseal dysplasia, hypotrichosis syndrome773300008
- Whyte syndrome773300008
- SOFT (short stature, onychodysplasia, facial dysmorphism, hypotrichosis) syndrome773625007
- SOFT syndrome773625007
- Short stature, onychodysplasia, facial dysmorphism, hypotrichosis syndrome773625007
- Alopecia, epilepsy, intellectual disability syndrome Moynahan type788417006
- Moynahan syndrome788417006
- Congenital dysplasia of nail unit1142193008
- Absence of teeth1162783002
- MFDA - mandibulofacial dysostosis with alopecia1216943004
- Mandibulofacial dysostosis with alopecia1216943004
UMLS
- ALOPECIA, CONGENITALC0265992
- ALPCC0265992
- Alopecia, congenitalC0265992
- Atrichia congenitaC0265992
- Atrichia congenita (disorder)C0265992
- Congenital AlopeciaC0265992
- Congenital alopeciaC0265992
- Congenital alopecia (disorder)C0265992
- Congenital atrichosisC0265992
- Naevoid congenital alopeciaC0265992
- Nevoid congenital alopeciaC0265992
- atrichia congenitaC0265992
- congenital alopeciaC0265992
Clinical Terms
- Cutaneous syndrome with ichthyosis
- atrichia congenita
- Hypohidrotic ectodermal dysplasia, hypothyroidism, ciliary dyskinesia syndrome
- GAPO syndrome
- Collodion baby
- Tooth absent
- HOPP syndrome
- Keratosis pilaris
- GAPO (growth retardation, alopecia, pseudoanodontia, optic atrophy) syndrome
- Retrognathia
- Frontonasal dysplasia with alopecia and genital abnomality
- Growth retardation, alopecia, pseudoanodontia, optic atrophy syndrome
- Hypotrichosis, osteolysis, periodontitis, palmoplantar keratoderma syndrome
- Odonto-onycho dysplasia alopecia syndrome
- Choroidal atrophy and alopecia syndrome
- Median cleft face syndrome
- SOFT (short stature, onychodysplasia, facial dysmorphism, hypotrichosis) syndrome
- Severe T-cell immunodeficiency, congenital alopecia, nail dystrophy syndrome
- Alopecia, progressive neurological defect, endocrinopathy syndrome
- Lopes Marques de Faria syndrome
- Acroosteolysis
- Cutis laxa, autosomal recessive
- HJMD (hypotrichosis, juvenile macular degeneration) syndrome
- MACS syndrome
- Congenital generalized alopecia
- Triangular alopecia
- ALPC
- Dwarfism, alopecia, pseudoanodontia, cutis laxa
- HLTRS (hypotrichosis, lymphoedema, telangiectasia, renal defect) syndrome
- Taurodontia with absent teeth and sparse hair syndrome
- Marie Unna congenital hypotrichosis
- Congenital dysplasia of nail unit
- Short stature, onychodysplasia, facial dysmorphism, hypotrichosis syndrome
- ANOTHER syndrome
- Congenital hypotrichosis
- PARC syndrome
- Congenital atrichosis
- Regional choroidal atrophy and alopecia
- Universal alopecia areata
- NISCH (neonatal ichthyosis, sclerosing cholangitis, hypotrichosis) syndrome
- Alopecia, epilepsy, intellectual disability syndrome Moynahan type
- Hypotrichosis congenita
- ALX4 (human aristaless-like 4) related frontonasal dysplasia with alopecia and genital anomaly
- RIN2 deficiency
- Congenital alopecia and nail dystrophy with severe functional T-cell immunodeficiency
- False anodontia
- Ichthyosis follicularis with alopecia and photophobia (IFAP)
- Developmental anomaly of periodontal tissue
- Frontonasal dysplasia with alopecia and genital anomaly syndrome
- MACS (macrocephaly, alopecia, cutis laxa, scoliosis) syndrome
- NISCH syndrome
- KP - Keratosis pilaris
- Alopecia, psychomotor epilepsy, periodontal pyorrhea, intellectual disability syndrome
- Atrichia with papular lesions
- Congenital generalised alopecia
- Congenital localized alopecia
- Tooth missing
- Atrichia congenita (disorder)
- Autosomal recessive palmoplantar keratoderma and congenital alopecia syndrome
- Alopecia and intellectual disability with hypergonadotropic hypogonadism syndrome
- ANE syndrome
- Devriendt Vandenberghe Fryns syndrome
- Nevoid congenital alopecia
- Ichthyosis, hypotrichosis, sclerosing cholangitis syndrome
- Odonto onycho dysplasia with alopecia syndrome
- IFAP - ichthyosis follicularis with alopecia and photophobia
- Recession of bone
- Hypotrichosis with keratosis pilaris and lentiginosis
- Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
- Congenital hypotrichia
- Marie Unna hereditary hypotrichosis
- Absence of teeth
- Sparse hair, short stature, skin anomalies syndrome
- Congenital alopecia (disorder)
- Shokeir syndrome
- Craniofrontonasal dysplasia with alopecia and hypogonadism
- Poikiloderma, alopecia, retrognathism, cleft palate syndrome
- Retrognathism
- Sclerosing cholangitis
- Autosomal dominant palmoplantar keratoderma and congenital alopecia
- Vertical alopecia
- Alymphoid cystic thymic dysgenesis
- MFDA - mandibulofacial dysostosis with alopecia
- Marie Unna syndrome
- Alopecia universalis
- Periodontitis associated with genetic disorder
- Thumb deformity, alopecia, pigmentation anomaly syndrome
- Winged helix deficiency
- Whyte syndrome
- ACD (alopecia, contracture, dwarfism) syndrome
- Hypotrichosis and intellectual disability syndrome Lopes type
- Tall forehead, sparse hair, skin hyperextensibility, scoliosis syndrome
- Spondyloepimetaphyseal dysplasia, hypotrichosis syndrome
- Pignata Guarino syndrome
- Lamellar ichthyosis
- Ichthyosis follicularis with alopecia and photophobia
- HLTRS (hypotrichosis, lymphedema, telangiectasia, renal defect) syndrome
- Naevoid congenital alopecia
- Alopecia, psychomotor epilepsy, periodontal pyorrhoea, intellectual disability syndrome
- Frontonasal dysplasia sequence
- Congenital retrognathism
- Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome
- Hereditary acroosteolysis
- T-cell immunodeficiency, congenital alopecia, and nail dystrophy
- ANOTHER (alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy, respiratory tract infection) syndrome
- PARC (poikiloderma, alopecia, retrognathism, cleft palate) syndrome
- Alopecia, congenital
- Macrocephaly, alopecia, cutis laxa, scoliosis syndrome
- Hypotrichosis, lymphoedema, telangiectasia, renal defect syndrome
- Periodontitis co-occurrent with genetic disorder
- Moynahan syndrome
- Moloney syndrome
- Ichthyosis, follicular atrophoderma, hypotrichosis syndrome
- Hypotrichosis with juvenile macular degeneration syndrome
- SOFT syndrome
- Mandibulofacial dysostosis with alopecia
- Congenital ichthyosis with hypotrichosis syndrome
- Jagell, Holmgren, Hofer syndrome
- Alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy and respiratory tract infections
- ANE (alopecia, progressive neurological defect, endocrinopathy) syndrome
- Congenital alopecia with keratin cysts
- ACD (alopecia, contracture, dwarfism) mental retardation syndrome
- Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome
- Odonto-onychial dysplasia with alopecia
- Palmoplantar keratoderma and congenital alopecia Stevanovic type
- Autosomal recessive palmoplantar keratoderma and congenital alopecia Wallis type
- Alopecia, contracture, dwarfism, intellectual disability syndrome
- Congenital localised alopecia
- Sutural alopecia
Frequently Asked Questions
What is the ICD-10 code for congenital alopecia?
The ICD-10-CM code for congenital alopecia is Q84.0. The full clinical description is "Congenital alopecia". Q84.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q84.0 mean?
ICD-10-CM code Q84.0 represents “Congenital alopecia”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q84.0 a billable code?
Yes, Q84.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q84.0 in?
Q84.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q84.0 map to?
Q84.0 maps to 59 SNOMED CT concepts: 720979002, 725029001, 770941005, 239050000, 1162783002, and 54 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q84.0?
Q84.0 is linked to 1 UMLS Concept Unique Identifier: C0265992. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q84.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital alopecia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q84.0?
Q84.0 maps to the ICD-11 code: LC30 (Developmental defects of hair or hair growth).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.