Q22.6
BillableHypoplastic right heart syndrome
Hypoplastic right heart syndrome
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q22.0Pulmonary valve atresia
Q22.1Congenital pulmonary valve stenosis
Q22.2Congenital pulmonary valve insufficiency
Q22.3Other congenital malformations of pulmonary valve
Q22.4Congenital tricuspid stenosis
Q22.5Ebstein's anomaly
Q22.8Other congenital malformations of tricuspid valve
Q22.9Congenital malformation of tricuspid valve, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(13)
SNOMED CT
UMLS
Clinical Terms
- Right hypoplastic heart syndrome (disorder)
- Right hypoplastic heart syndrome
- Pseudotruncus arteriosus
- Hypoplasia of right heart
Frequently Asked Questions
What is the ICD-10 code for hypoplastic right heart syndrome?
The ICD-10-CM code for hypoplastic right heart syndrome is Q22.6. The full clinical description is "Hypoplastic right heart syndrome". Q22.6 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q22.6 mean?
ICD-10-CM code Q22.6 represents “Hypoplastic right heart syndrome”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q22.6 a billable code?
Yes, Q22.6 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q22.6 in?
Q22.6 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q22.6 map to?
Q22.6 maps to 2 SNOMED CT concepts: 39589002, 268180007. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q22.6?
Q22.6 is linked to 1 UMLS Concept Unique Identifier: C0344963. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q22.6 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hypoplastic right heart syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q22.6?
Q22.6 maps to the ICD-11 code: LA8Z (Structural developmental anomaly of heart or great vessels, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.